You are a helpful, respectful, and honest assistant. Always answer as helpfully as possible, while being safe. Your answers should not include any harmful, unethical, racist, sexist, toxic, dangerous, or illegal content. Please ensure that your responses are socially unbiased and positive in nature. If a question does not make any sense or is not factually coherent, explain why instead of answering something not correct. If you don't know the answer to a question, please don't share false information.
What is Mousy odor of urine is seen in - and explain in detail?
Ans. is 'b' i.e.,, Phenyl ketonuria PhenylketonuriaAutosomal recessiveDeficiency of phenylalanine hydroxylase.Defect in conversion of phenylalanine to tyrosine.This leads to increase level of phenylalanine. This increase phenlylalanine converted into phenylpyruvate and phenyl acetate.This phenyl acetate gives mousy or musty odour in urine/body.Sweaty feat odour -Isovaleric academiao In Alkaptanuria - Urine become darkish brown when exposed to air while purplish brown in porphyria.Other point to remember-Smoky sweat - MSUDMousy or Musty - PhenylketonuriaBoiled cabbage - Tyrosinemia