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What is An infant presents to OPD with signs of heart failure. On examination, there is hypotonia; hepatomegaly, cardiomegaly. ECG shows tall QRS complex and short PR interval. Which enzyme is deficient in this condition? and explain in detail?
Hypotonia, hepatomegaly, cardiomegalyare seen in Pompe disease.
Acid maltase or Alpha 1,4. Glucosidase is deficient in Pompe disease.