ðə bɹˈæntʃttʃˈeɪn ˈælfəkˈiːɾoʊ ˈæsɪd dˌiːhaɪdɹˈoʊdʒneɪs kˈɑːmplɛks, ðæt nˈoːɹməli kənvˈɜːts lˈuːsiːn, ˈaɪsoʊljˌuːsiːn, ɔːɹ vˈeɪlaɪn ˌɪntʊ ɐkˈɪlkˈoʊ ɐ dᵻɹˈɪvətˌɪvz, kənvˈɜːts hˌaɪpoʊɡlˈaɪsɪn ɐ ˌɪntʊ hˈaɪli tˈɑːksɪk məkpˈɑːkˈoʊ ˈeɪ.
The branched-chain alpha-keto acid dehydrogenase complex, that normally converts leucine, isoleucine, or valine into acyl-CoA derivatives, converts Hypoglycin A into highly toxic MCPA-CoA.