ɪɾ ɪz ɐn ʌŋkˈɑːmən kˈɔːz ʌv ˌʌnɛksplˈeɪnd hˈɑːɹt fˈeɪlɪɹ ɪn ˈɪnfənts ænd tʃˈɪldɹən, ænd ɪz wˈʌn kəmpˈoʊnənt ʌv ˌeɪtʃˌiːsˈiː sˈɪndɹoʊm.
It is an uncommon cause of unexplained heart failure in infants and children, and is one component of HEC syndrome.