Enrico Drago Francesca Garbarino Sara Signa Alice Grossi Francesca Schena Federica Penco Elettra Santori Fabio Candotti Kaan Boztug Stefano Volpi Marco Gattorno Roberta Caorsi
10.3389/fimmu.2022.937108
Front Immunol
2022 Sep 9;13:937108.
dada2 hemophagocitic lymphohistiocytosis immunoglobulin therapy viral infection
CC BY
https://pubmed.ncbi.nlm.nih.gov/36159847/
Immunologic Deficiency Syndromes Lymphohistiocytosis, Hemophagocytic / diagnosis Lymphohistiocytosis, Hemophagocytic / drug therapy Lymphohistiocytosis, Hemophagocytic / etiology Polyarteritis Nodosa Virus Diseases
Immunologic Deficiency Syndromes Lymphohistiocytosis, Hemophagocytic / diagnosis Lymphohistiocytosis, Hemophagocytic / drug therapy Lymphohistiocytosis, Hemophagocytic / etiology Polyarteritis Nodosa Virus Diseases Case Reports Adenosine Deaminase / genetics Agammaglobulinemia Female Humans Immunoglobulins, Intravenous / therapeutic use Inflammation Intercellular Signaling Peptides and Proteins Measles Vaccine Severe Combined Immunodeficiency Tumor Necrosis Factor Inhibitors Immunoglobulins, Intravenous Intercellular Signaling Peptides and Proteins Measles Vaccine Tumor Necrosis Factor Inhibitors Adenosine Deaminase Severe combined immunodeficiency due to adenosine deaminase deficiency
PMC9503826
36159847
Case Report: Susceptibility to viral infections and secondary hemophagocytic lymphohistiocytosis responsive to intravenous immunoglobulin as primary manifestations of adenosine deaminase 2 deficiency
2022