PMC6263244_01
Bony swelling present over the posterior part of maxilla involving the maxillary tuberosity and part of palate.
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Occlusal radiograph showing fibrous dysplasia with ground glass appearance over the right side extending from first premolar to the area beyond maxillary tuberosity.
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PMC6263244_02
Preoperative images showing facial asymmetry due to bony hard expansion of craniofacial bones.
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No associated skin pigmentations were detected (Figure 3).
Lateral and PA views of radiographs showing ground glass appearance involving multiple cranial bones.. Abbreviation: PA, posteroanterior.
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Three years ago, the patient underwent a radiographic imaging (Figure 4) and computed tomography scans on which a diffuse thickening of cranial bones (frontal, occipital, sphenoid, zygomatic, petrous, and mastoid bones of both sides and temporal and parietal bones of the left side) involving mainly outer table is noted (Figure 5).
(A) CT and (B) 3D CT scans showing expansile growth of the multiple skull and facial bones.. Abbreviation: CT, computed tomography.
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Three years ago, the patient underwent a radiographic imaging (Figure 4) and computed tomography scans on which a diffuse thickening of cranial bones (frontal, occipital, sphenoid, zygomatic, petrous, and mastoid bones of both sides and temporal and parietal bones of the left side) involving mainly outer table is noted (Figure 5).
Postoperative images.
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In both the cases, incisional biopsies followed by surgical corrections were performed (Figure 6).
Histopathological sections of both cases revealing curvilinear-shaped bony trabeculae with the absence of osteoblastic rimming, seen dispersed within cellular loosely organized fibrous stroma.
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The trabeculae showed the presence of osteocytes and the absence of peripheral rimming of osteoblasts suggestive of fibrous dysplasia (Figures 7 and 8).
Histopathological sections of both cases at x40 magnification showing bony trabeculae with absence of osteoblastic rimming.
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The trabeculae showed the presence of osteocytes and the absence of peripheral rimming of osteoblasts suggestive of fibrous dysplasia (Figures 7 and 8).