PMC8586170_01
Interictal EEG of proband demonstrating frequent right centrotemporal spikes and sharps. Ictal episodes not captured during EEG monitoring.
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At four years of age, Epilepsy Monitoring Unit (EMU) evaluation revealed poorly sustained background rhythm, frequent interictal right central temporal sharp waves and vertex sharp waves and rare left central and temporal sharp waves, consistent with focal seizure tendency (Figure 1).
PMC8586170_02
Ictal EEG of proband's sibling demonstrating seizure onset right fronto-temporal region (A) and subsequent seizure spread to entire right hemisphere and left frontotemporal region (B).
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EEG revealed frequent right hemisphere interictal epileptiform discharges with diffuse and focal right hemisphere frontal and temporal region slowing consistent with focal seizure tendency (Figure 2A and B).