PMC4214905_01
Chest radiograph showing right upper lobe cystic parenchymal lesions, pneumothorax with left lung passive atelectasis, with normal cardiovascular silhouette.
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F1
A chest radiograph revealed right upper lobe cystic parenchymal lesions and a pneumothorax greater than 50% on the left side, requiring thoracostomy tube placement (Fig. 1).
High-resolution computed tomography scan of the chest showing multiple well-defined, thin-walled cystic parenchymal lesions distributed diffusely throughout the lungs, and closed left thoracostomy tube with a small residual left pneumothorax, with normal cardiovascular structures.
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F2
High-resolution computed tomography of the chest revealed multiple, well-circumscribed, round, and thin-walled cysts that were scattered in a bilateral, roughly symmetric pattern (Fig. 2).
Surgical lung biopsy showing spindle cells in the wall of a cystic space stain for HMB-45; 400x.
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F3
The smooth muscle component was positive for antibodies to vimentin, actin and desmin, but it also reacted with antibodies to human melanin black 45 (HMB 45) (Fig. 3).