PMC7125497_01
Patient with fine, lightly pigmented, sparse hair and dry and rough skin with scanty eyebrows.
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On physical examination, he was found to have fine, lightly pigmented, sparse hair and dry and rough skin with scanty eyebrows (Figure 1).
Upper limbs and lower limbs showing ectrodactyly with absent 2nd and 3rd digit/toes.
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Both upper limbs and lower limbs had ectrodactyly with absent 2nd and 3rd digit/toes (Figure 2).
Intraoral and radiographic examination revealing oligodontia with 11, 12, 16, 21, 22, 26, 36, 42, and 46 as the teeth present. Unerupted tooth 47 present in the lower jaw.
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The intraoral examination revealed oligodontia with 11, 12, 16, 21, 22, 26, 36, 42, and 46 as the only teeth present (Figure 3). Panoramic view revealed an unerupted tooth 47 in the lower jaw (Figure 3).
(a) Radiograph of a hand showing syndadactyly of 1st and 2nd metacarpals with aplasia of 2nd and hypoplasia of 3rd phalange. (b) Radiograph of a foot showing syndactyly of 1st and 2nd metatarsals with aplasia of 2nd and hypoplasia of 3rd phalanges.
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Syndadactyly of the 1st and 2nd metacarpals with aplasia of the 2nd and hypoplasia of the 3rd phalange was seen in the hand (Figure 4(a)). Similarly, syndactyly of the 1st and 2nd metatarsals with aplasia of the 2nd and hypoplasia of the 3rd phalanges were seen in the foot radiograph (Figure 4(b)).
Postoperative radiograph showing root canal treated teeth with respect to teeth 11,21,22 and 46.
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Root canal treatment with respect to teeth 11, 12, 16, 21, 22, 26, 36, and 46 was done, followed by restoration with composite resin (Figure 5).
Special trays fabricated on the cast model with self-cure acrylic resin. Aluminium foil has been used for making the spacer.
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Special trays were fabricated on the cast model with self-cure acrylic resin (Figure 6).
The complete overdentures delivered to the patient. Frontal and lateral views of the denture inside the patient's mouth.
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The complete overdentures were delivered (Figure 7).
Photograph of the patient after 2 years follow-up.
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