PMC4878224_01
First presentation, note the midline tongue fusion with bifid frenulum and endotracheal tube as nasopharyngeal stent
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F1
Mucosa of the floor of the mouth was in continuity with the palate [Figure 1].
Magnetic resonance imaging; sagittal view showing tongue into the nasopharynx and hypoplasia of inferior cerebellar vermis
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F2
MRI was suggestive of cleft palate with tongue protruding into the nasal cavity and hypoplasia of inferior cerebellar vermis [Figure 2].
(a) Pre-operative image, tracheostomy in situ present. (b) Immediate post-operative image, complete release of tongue
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F3
A definitive release of the tongue from palate [Figure 3] was done in the second stage at 3 months of life (tongue adhered to palate in the lateral half; the central half was pushed up into the nasal cavity and nasopharynx through the cleft palate).