PMC4358030_01
Generalized atrophy and elbow contracture was detected in our case
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F1
Quadriparesia and generalized atrophy with elbow contracture was detected [Figure 1].
PMC4358030_02
Perseveration in Luria alternating series test (drawing of the patient's 35-year-old brother)
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F2
In Luria alternating series, perseveration deficit was found [Figure 2].
T2-weighted MRI of the patient demonstrating prominent frontotemporal atrophy
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F3
After 2 years, MRI of the brain showed enlarged lateral ventricles and bilateral anterior frontotemporal atrophy [Figure 3].