PMC5256577_01
Fundus photographs. Retinal hyperpigmentation in bone spicules at mid-periphery. Pigment clumping in macular area. Extensive atrophy of retinal pigment epithelium. Slight retinal arteriolar attenuation
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Fig1
Arteries and veins were slightly narrow or attenuated (Fig. 1). 
Electrorretinogram. Scotopic and photopic responses with marked reduction in the amplitude of a and b waves. Flicker and oscillatory potentials with implicit time delay and flattening of recordings
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Fig2
Electroretinogram (ERG) showed diminished b-wave amplitudes in both photopic and scotopic phases with a marked reduction in the amplitude of all waves, implicit time delay of the flicker response and flattening of oscillatory potentials (Fig. 2).
Fluorescein angiography. Macular fluorescence blockage from pigment clumping, patchy areas of hyperfluorescence corresponding to areas of RPE atrophy causing window defect
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Fig3
Fluorescein angiography evidenced central hypofluorescence due to contrast blockage in the areas with pigment accumulation and patchy hyperfluorescence due to window defects in RPE atrophy areas (Fig. 3).  
Clinical photograph right eye. Fine diffuse keratic precipitates more evident in the lower cornea. The patient also had mild anterior chamber cellular reaction (0.5+) and a subtle stromal velvety appearance
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Fig4
On a follow-up visit, 3 years after initial consultation, examination of the OD revealed a white asymptomatic eye with fine translucent 'stellate' keratic precipitates scattered over the entire endothelium and mild cellular reaction in the anterior chamber with no synechiae, iris nodules or heterochromia but subtle stromal atrophy of the iris crypts in comparison with the OS (Fig. 4).
Automated visual fields. Severe affection of both visual fields involving fixation
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Fig5
The OS showed no signs of inflammation thus matching the criteria for unilateral Fuchs' heterochromic iridocyclitis (FHI) Visual Fields were severely affected (Fig. 5) .