PMC6837811_01
Lateral radiograph of the skull shows normal bone density with wormian bones in the lambdoid suture (hollow arrow), prognathism and supernumerary teeth (white arrow). Patient is wearing dental prosthesis.
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A lateral radiograph of the skull (Figure 1) showed normal bone density, wormian bones (white arrow), mandibular prognathism and supernumerary teeth.
Water's view for paranasal sinuses shows an open metopic suture (hollow arrow), aplastic frontal sinuses, hypoplastic maxillary sinuses (white arrows) and underpneumatised mastoids.
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Radiographs of the PNS sinuses (Figure 2) revealed an open metopic suture, aplasia of the frontal sinuses, hypoplasia of the maxillary sinuses and underpneumatised mastoids.
Postero-anterior radiograph of the upper chest shows aplasia of lateral two-thirds of both clavicles (white arrows) and a bell-shaped thorax.
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Radiographs of the shoulders (Figure 3) demonstrated aplasia of the lateral two-thirds of both clavicles and a bell-shaped thorax.
Coronal section of computed tomography-paranasal region shows supernumerary unerupted teeth, a deviated nasal septum, hypoplastic maxillary sinuses and a high-arched palate.
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Non-contrast CT of the PNS revealed normal bone density, multiple supernumerary teeth, a deviated nasal septum and a high-arched palate (Figure 4), a dysplastic clivus which was flexed with convexity towards the endocranium (Figure 5), an open metopic suture and sclerotic mastoids (Figure 6).
Sagittal-section computed tomography scan shows a dysplastic clivus with its flexion deformity and convexity towards the endocranium (arrow).
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Non-contrast CT of the PNS revealed normal bone density, multiple supernumerary teeth, a deviated nasal septum and a high-arched palate (Figure 4), a dysplastic clivus which was flexed with convexity towards the endocranium (Figure 5), an open metopic suture and sclerotic mastoids (Figure 6).
Axial-computed tomography section at the level of skull base (a) shows under-pneumatised mastoids, non-pneumatised sphenoid sinuses and superiorly (b) shows an open metopic suture (curved arrow).
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Non-contrast CT of the PNS revealed normal bone density, multiple supernumerary teeth, a deviated nasal septum and a high-arched palate (Figure 4), a dysplastic clivus which was flexed with convexity towards the endocranium (Figure 5), an open metopic suture and sclerotic mastoids (Figure 6).