PMC3299063_01
EMG showing high-frequency repetitive discharges of single motor unit action potential MUAP, characteristically waning in amplitude and frequency, suggestive of neuromyotonia
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F1
It is characterized by rippling painful muscle spasms (which, contrary to those seen in the Stiff Person syndrome, persist after nerve block, anesthesia and sleep and have typical electromyographic findings) [Figure 1].
A lady having Satoyoshi's syndrome showing absence of eyebrows and eyelashes with partial alopecia
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F2
Disease presents with muscle spasms in the legs and alopecia [Figure 2].
EMG showing continuous (low frequency) motor unit activity simultaneously occurring in agonist and antagonist muscles even in relaxation, suggestive of Stiff Person syndrome
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F3
Her EMG studies showed presence of continuous motor activity, suggestive of Stiff Person syndrome [Figure 3].