PMC5389223_01
Erythema of vulva, vagina, and partial fusion of labia minora and majora and burying of clitoris with histopathology revealing basal vacuolization, necrotic keratinocytes, Max Joseph spaces, and pigmentary incontinence, along with dermal lymphocytic proliferation
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F1
On mucocutaneous examination, intense erythema of vulva, vagina, and partial fusion of labia minora and majora with burying of clitoris were present [Figure 1]. The one from erythematous patch on labia minora revealed orthohyperkeratosis, basal vacuolization, squamatization, necrotic keratinocytes, Max Joseph spaces, and pigmentary incontinence, along with dermal lymphocytic proliferation [Figure 1].
Hyperpigmentation, fissuring, and scaling with marked stenosis of anal mucosa and histopathology showing fibrosis, pigmentary incontinence, basal vacuolization, and necrotic keratinocytes, along with dense dermal lymphocytic infiltration
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F2
Anal mucosa exhibited hyperpigmentation, fissuring, and scaling, along with marked stenosis [Figure 2]. The third biopsy from perianal region exhibited fibrosis, pigmentary incontinence, basal vacuolization, and necrotic keratinocytes, along with dense dermal lymphocytic infiltration [Figure 2].
Hyperpigmentation and erosions along gingival margins
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F3
On examination of the oral cavity, violaceous plaques were present over labial and lingual aspects of the maxillary and mandibular gingival surfaces [Figure 3].