PMC9745053_01
Duplication situating in the midline, at 6 o'clock direction in the lithotomy position.
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F1
An 11-month-old girl was found to have a posterior anal orifice since birth (Figure 1B).
Case 1: dilated rectum and sigmoid colon (A); rectal stenosis presented in MRI (B); complete removal of the ACD (C); histology showing squamous epithelium, fibers, blood vessels, and smooth muscle tissue (D).
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F2
The proximal rectum and sigmoid colon were significantly dilated, with the widest part being about 44 mm (Figure 2A). The duplication appeared as a line of high-signal lesions communicating with the skin (Figure 2B). Histology confirmed the diagnosis of ACD and showed the specimen covered with squamous epithelium, fibers, blood vessels, and smooth muscle tissue (Figure 2D).
Case 1: barium edema 4 months after surgery.
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F3
Re-examination of the barium enema 4 months after surgery showed that the distal rectum was 6 mm and the mega-rectosigmoid progressed, with the widest part being about 60 mm (Figure 3).
PMC9745053_02
Duplication situating in the midline, at 6 o'clock direction in the lithotomy position.
fped-10-955845-g001.jpg
PMC9745053_02_fped-10-955845-g001.jpg
F1
An 11-month-old girl was found to have a posterior anal orifice since birth (Figure 1B).
Case 2: Barium fistulography of ACD (A); barium enema (B); simple mucosectomy (C); histology showing squamous epithelium (D).
fped-10-955845-g004.jpg
PMC9745053_02_fped-10-955845-g004.jpg
F4
Barium fistulography and contrast enema showed a 5-mm-long and 4-mm-diameter tubular area with no communication with the rectum (Figure 4A). No obvious abnormality was observed in the size and shape of the colon and rectum (Figure 4B). The duplication was completely resected and sent for pathological examination, with the posterior rectal wall left completely intact (Figure 4C). Histology confirmed the diagnosis of ACD and showed that the specimen was covered with squamous epithelium (Figure 4D); no complication was reported during the 11-month follow-up.