PMC6479100_01
Patient admitted with deformated right hemiface with exopthalmos.
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The physical exam found a right exophtalmia, a swelling deformatted right hemiface (Fig. 1) and a bulky whitish tumor filling the right nasal cavity at the nasal endsocopy.
Imaging findings in CE-CT and MRI. (A) CT showed heteregenous tumor mesuring 8.7 x 6.5 cm, heterogenously enhancing with important lysing of the inner wall of the right orbit. (B) MRI showed confirmed high vascularized and extensive mass filling the right nasal cavity.
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Important lysis of the inner wall of the right orbit with important extension (intra-orbital, intra sellar, nasopharynx and right pterygoide fossa) (Fig. 2).
Ulcerated tumor proliferation richly vascularized with thickened-wall vessels and turgid endothelium. This proliferation is made of globular cells with abundant eosinophilic cytoplasm. This aspect is compatible with epitheloid hemangioendothelioma.
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The histological aspect is compatible with a epitheloid hemangioendothelioma (Fig. 3).
Important regression of the deformation of the right hemiface and the exopthalmous 18 months after admission.
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