PMC9063803_01
(A and B) Distribution of typical lesions on almost all parts of the body, except the scalp, face, palm and soles in a two- month-old girl with incontinentia pigmenti. (C) Erythematosus papules and (D) vesicles on the trunk ((D) is the enlargement of a red square region in (C)). (E) Hyperpigmented macules distributed linearly and swirled along Blaschko's lines. (F) Retinal neovascularization on peripheral part of the right eye at 3 months of age. (G) Normal retinal vasculature on the right eye at 6 months of age.
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A two-month-old baby girl presented with a painless and non-itchy erythematous papules and vesicles on abdomen, groins, and both upper limbs (Figure 1A-D), as well as hyperpigmented macules arranged spindle-like in almost all parts of the body except the face, both palms and soles (Figure 1E). No abnormalities were found in the EEG, whereas ophthalmological evaluation by the ophthalmologist showed RN on the peripheral side of the right eye (Figure 1F). On day 116 of evaluation, the skin lesions resolved, leaving hyperpigmented macular lesions, and the RN achieved spontaneous resolution (Figure 1G).
PMC9063803_02
(A and B) Distribution of the lesions on almost all parts of the body, except the scalp, face, palm and soles, in a two-month-old girl with incontinentia pigmenti. (C) Verrucous papules left knee and (D-E) finger toes. (F-G) Hyperpigmented macules distributed linearly and swirled along Blaschko's lines in trunks and both legs.
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A two-month-old baby girl presented with painless and non-itchy erythematous papules as well as hyperpigmented macules and papules in almost all parts of the body except the face, both palms and feet (Figure 2A and B). Some of the erythematous papules and vesicles resolved and formed verrucous papules (Figure 2C-E) and also hyperpigmented macules (Figure 2F and G), whereas new lesions kept appearing.