PMC6964329_01
Fibrofolliculomas, dome-shaped, yellowish papules on the cheeks and nose
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Numerous, soft, whitish-yellow lesions were found on patient's face during physical examination (Figure 1).
Baseline chest computed tomography, lung window: A) axial plane, B) coronal reconstruction. It shows multiple well-circumscribed, thin-walled, and variable sized lung cysts with round, oval, and irregular shapes with predominantly basal distribution. The largest cyst is located in the left lower lobe
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Subsequent CT examination revealed multiple, thin walled, differently shaped cysts in both lungs, located predominantly in the lower lung zones (Figure 2). The largest cyst had dimensions of 11 x 10 x 3.1 cm (Figures 2B, 3).
Reconstruction in 3D Pulmo software depicts areas of less than -950 HU in colour blue
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The largest cyst had dimensions of 11 x 10 x 3.1 cm (Figures 2B, 3).
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Baseline chest computed tomography, lung window: A) axial and B) coronal plane. Computed tomography scan shows characteristic distribution of lung cysts predominantly in medial aspect of middle and lower lung zones
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Chest CT revealed numerous thin-walled lung cysts located mostly in lower lung zones (Figure 4A). The largest lung cyst had dimensions of 4.2 x 2.4 x 2.1 cm (Figures 4B, 5).
Reconstruction in 3D Pulmo software depicts areas of less than -950 HU in colour blue
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The largest lung cyst had dimensions of 4.2 x 2.4 x 2.1 cm (Figures 4B, 5).
Chest computed tomography, lung window: A) axial plane, B) coronal plane. Recurrent pneumothoraces. There is a right-sided pneumothorax and small cysts in both lungs
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After reappearance of the pneumothorax three years later, wedge resection of the right lung containing emphysematous bulle was performed (Figure 6).
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