PMC3304179_01
Frontal view of the patient showing mandibular swelling
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F1
The approximately 5 x 4 cm facial swelling extended superiorly from right corner of mouth to 1 cm inferiorly beyond the lower border of the mandible, medially from left para-symphysis region to distally half of the body of the mandible [Figure 1].
Intraoral view showing missing lower canines
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F2
Intraoral swelling was present in relation to mandibular anterior teeth [Figure 2].
Orthopantomograph showing multiple cysts in maxilla and mandible
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F3
Orthopantomograph revealed multiple unilocular well-defined radiolucencies with sclerotic border in maxilla and mandible [Figure 3].
Lower occlusal view showing radiolucency and impacted teeth
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F4
Mandibular occlusal radiograph [Figure 4] revealed a well-defined radiolucent lesion with a sclerotic border extending from periapical region of lower anteriors extending to the lower border of the mandible in relation to 33 and 43.
Lateral skull view showing bridging of the sella turcica
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F5
Lateral skull view revealed bridging of the sella turcica [Figure 5].
CT, axial view showing multiple cystic lesions in maxilla
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F6
Computed tomographic (CT) images showed multiple cystic lesions in maxilla [Figure 6] and mandible [Figure 7].
CT, axial view showing extensive cystic lesion in mandible
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F7
Computed tomographic (CT) images showed multiple cystic lesions in maxilla [Figure 6] and mandible [Figure 7].
Bifid third rib on the right side with dextrocardia
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F8
Postero-anterior [Figure 8] chest radiograph revealed a bifid third rib in the right side and an unusual finding of dextrocardia.
CT, axial view showing calcification of falx cerebri
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F9
CT images of the brain showed areas of hyperdensities, suggestive of falx cerebri [Figure 9] and tentorial cerebelli [Figure 10] calcification.
CT, axial view showing calcification of tentorial cerebelli
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F10
CT images of the brain showed areas of hyperdensities, suggestive of falx cerebri [Figure 9] and tentorial cerebelli [Figure 10] calcification.
CT, axial view showing bifid spine, cervical and thoracic vertebrae
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F11
CT images of spine revealed bifid spine in relation to C6 C7 T1 [Figure 11].
Ultrasonographic image showing spleen in right hypochondrium
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F12
Ultrasonographic images showed the presence of spleen in the right hypochondrium [Figure 12] and liver in the left hypochondrium [Figure 13] with transposition on great vessels [Figure 14].
Ultrasonographic image showing left hypochondrium
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F13
Ultrasonographic images showed the presence of spleen in the right hypochondrium [Figure 12] and liver in the left hypochondrium [Figure 13] with transposition on great vessels [Figure 14].
Ultrasonographic image showing transposition of great vessels
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F14
Ultrasonographic images showed the presence of spleen in the right hypochondrium [Figure 12] and liver in the left hypochondrium [Figure 13] with transposition on great vessels [Figure 14].
Multiple palmer pits
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F15
There were multiple palmer pits [Figure 15] measuring 0.2-0.3 mm in diameter, which were brownish black in color, and were present on the palms of both his hands.