PMC4274712_01
The abdomen was severely distended with signs of ascites (a). Also noted was ambiguous genitalia with a phallus like structure (b).
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fig1
Initial examination revealed a markedly distended abdomen with signs of severe ascites (Figure 1). Perineal examination revealed a phallus like structure with no urethral, vaginal, or anal openings (Figure 1).
Pre-op MRI demonstrating an elongated bladder up to the level of urachus; a blind ending rectal pouch having no communication with the urogenital system; hydrometrocolpos; and absence of abdominal wall muscles.
CRIS2014-746323.002.jpg
PMC4274712_01_CRIS2014-746323.002.jpg
fig2
Further radiological investigations (Figure 2) revealed hydrometrocolpos, absent anterior abdominal wall muscles, moderate hydronephrosis and hydroureter, and linear streaked calcifications in the left kidney which was smaller compared to the right (2.3 cm and 3.2 cm, resp.).