PMC5101502_01
Chest X-ray showing cardiac dextroposition and radiopaque right hemithorax.
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F1
Moreover, cardiac dextroposition and a radiopaque right hemithorax were confirmed on a chest X-ray examination (Fig. 1).
CTA showing right pulmonary vein drainage to the inferior vena cava.
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F2
The computerised tomography angiography (CTA) revealed partially anomalous pulmonary venous drainage to the IVC, APC originating from the abdominal aorta, and hypoplasia of the right lung (Fig. 2), which confirmed the diagnosis of scimitar syndrome.
(A) Catheterisation showing systemic arterial collaterals arising from the abdominal aorta and supplying the right lung. (B) and (C) Catheterisation showing coil embolisation of the systemic arterial collaterals supplying the right lung.
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F3
A 4-F Cobra cathether (Cook, Bloomington, IN) was delivered to the APC via the femoral artery and then two 8 x 50-mm MReye embolisation coils (Cook, Bloomington, IN), five 5 x 30-mm MReye embolisation coils and two 5 x 30-mm Cook coils (Cook, Bloomington, IN) were deployed for occlusion (Fig. 3A,B).
Catheterisation showing complete occlusion of the atrial septal defect by the Amplatzer septal occluder.
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F4
ASD (pathway: MPA->RV->RA->ASD->LA). A 10-mm Amplatzer septal occluder (AGA Medical, MN) was implanted after balloon sizing the defect (diameter: 8 mm) (Fig. 4).