PMC4322408_01
Trichrome stain represents the absence of the myocardial muscle and replacement of the myocardium by dense fibrous tissue
APC-8-71-g001.jpg
PMC4322408_01_APC-8-71-g001.jpg
F1
The specimen showed complete absence of myocardial striated muscle and instead consisted of dense and loose fibro-connective tissue with prominent blood vessels and small amount of epicardial fat, all consistent with Uhl's anomaly (Figure 1).
Chest and abdominal X-ray on presentation
APC-8-71-g002.jpg
PMC4322408_01_APC-8-71-g002.jpg
F2
Her chest X-ray was unremarkable [Figure 2].