PMC5394385_01
(a) PA (posteroanterior) view of the spine showing progressive cervicothoracic scoliosis. (b) Lateral view image of the spine showing severe kyphosis with rotatory subluxation at the level of T4-T5. The degree of subluxation almost gives the appearance of a congenital vertebral dislocation at the T4 on T5 junction.
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Shriner's hospital at 3 years of age with Spina Bifida, congenital vertebral dislocation, and severe congenital scoliosis (Figures 1 and 2). Skeletal survey at the time also demonstrated dysplasia of both his ischium and certain segments of his spinal column (Figures 1 and 3).
(a) Sagittal cut of a CT-scan (myelogram) of the spine showing kyphosis demonstrated in the plain radiographs of Figure 1. (b) Three-dimensional reconstruction of the thoracic spine showing the severity of kyphoscoliosis.
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Shriner's hospital at 3 years of age with Spina Bifida, congenital vertebral dislocation, and severe congenital scoliosis (Figures 1 and 2). Skeletal survey at the time also demonstrated dysplasia of both his ischium and certain segments of his spinal column (Figures 1 and 3).
(a) AP radiograph of the pelvis and (b) abduction internal rotation views, both demonstrating bilateral dysplasia of the ischium.
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Shriner's hospital at 3 years of age with Spina Bifida, congenital vertebral dislocation, and severe congenital scoliosis (Figures 1 and 2). Skeletal survey at the time also demonstrated dysplasia of both his ischium and certain segments of his spinal column (Figures 1 and 3).
AP and lateral radiographs of the spine showing spinal instrumentation from the level of T1 down to the pelvis; the crank-shaft of his spine is also apparent here.
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From an orthopedic point of view, he developed a crank-shaft phenomenon of his spinal fusion and pseudarthrosis across his lumbosacral junction over the course of 8 years after surgery (Figure 4).
Postoperative AP radiograph of the pelvis after bilateral dega osteotomy and bilateral proximal femur varus derotational osteotomy.
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On his last assessment by the orthopedics team, imaging showed no further signs of subluxation (Figure 5).