PMC5573462_01
The patient with MOPD II at left and her older sister at
right. Patient is five years old and the older sister is fourteen years
old. Relatively proportionate short stature is noted.
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fig1
The older sister was fourteen years old and was not affected by MOPD II syndrome.On clinical examination, she was proportionally short (Figure 1).
Patient's chest radiograph at age 2 shows narrow
chest, hypoplastic scapula, hypoplastic pelvis and slender bones.
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fig2
Her chest was narrow, the scapula and pelvis were hypoplastic and all bones were slender (Figure 2).
Hand photo of the patient at age 5 (A) and hand
radiograph of the patient at age 2 (B).
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Her elbows were bent, and the fingers and thumbs were short (Figure 3).
(A) Her height is only 62 cm. (B) Large and prominent nose and small pinnae. Hair is thin and dry. (C) Oral examination
of the patient revealed small incisors and posterior teeth with severe caries.
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fig4
The large nose with a prominent nasal bridge was observed (Figure 4). Oral hygiene was poor and there were many decayed teeth (Figure 4). All teeth were hypoplastic and there were increased spaces between the teeth in maxilla but the spaces between the teeth in mandibula were normal (Figure 4).
Periapical (A,B,C,D) and lateral cephalometric (E) radiographs show short-rooted incisors, rootless primary
molars, micrognathia and hypoplastic alveolar bone. (D) shows the extraction area after two weeks. In (E), large sella
turcica and premature closure of cranial sutures are observed.
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Radiographic examination revealed rootless primary molars, and most deciduous incisors appeared to have premature exfoliation (Figure 5).
(A)Extracted teeth.(B) Extraction area after two weeks.
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After two weeks, the extraction area was healthy (Figure 6).