PMC5005253_01
a Facial port-wine stain affecting the facial skin; b CT scan revealing cortical calcification in the cerebral hemisphere; c MR imaging demonstrating leptomeningeal venous angioma and enlargement of the choroid plexus; d An immediate postictal FDG-PET scan showing significant intense hypermetabolism in the left frontal lobe
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Fig1
This 3-month-old infant was noticed at birth have an unilateral congenital nevus flammeus (port-wine stain) (Fig. 1a). Computerised tomography (CT) scan revealed cortical calcification in the left cerebral hemisphere (Fig. 1b). Magnetic Resonance (MR) imaging demonstrated unilateral cerebral atrophy and leptomeningeal venous angioma (Fig. 1c). Immediate postictal evaluation of positron emission tomography (PET) demonstrated significant intense hypermetabolism in the left frontal lobe (Fig. 1d).
a Interictal scalp EEG showing markedly asymmetry with spikes observed on F3&F7; b Ictal scalp EEG revealing changing of the background activities and bilateral rhythmic slow waves with no localized value
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Fig2
The interictal scalp electroencephalography (EEG) (Fig. 2a) showed obvious asymmetry with spikes detected on left frontal and anterotemporal area, and the ictal scalp EEG revealed changing of the background activities and bilateral rhythmic slow waves with no localized value (Fig. 2b).
a Intraoperative image demonstrating leptomeningeal angioma; b Postoperative CT scan showing brain edema; c, d, e Postoperative MR images (axial, sagittal and cornonal view) confirming complete disconnection
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Fig3
Postoperative MR imaging demonstrated a complete disconnection of the affected hemisphere had been achieved (Fig. 3c-e).