PMC5828096_01
Patient with Ellis-van Creveld syndrome.
CRID2018-8631602.001.jpg
PMC5828096_01_CRID2018-8631602.001.jpg
fig1
A 15-year-old female was referred to the Department of Prosthetic Dentistry for evaluation and prosthetic dental treatment of congenitally absent maxillary lateral incisors and mandibular incisors (Figure 1).
Hands showing polydactyly and hypoplastic nails.
CRID2018-8631602.002.jpg
PMC5828096_01_CRID2018-8631602.002.jpg
fig2
Polydactyly of hands was observed with dysplastic and atrophic finger and toe nails (Figure 2).
Absent maxillary lateral incisors and mandibular incisors, large maxillary labial frenum, multiple accessory labial frenula, midline diastema, mandibular anterior ridge defect, and crossbite.
CRID2018-8631602.003.jpg
PMC5828096_01_CRID2018-8631602.003.jpg
fig3
Laterally, there were multiple small accessory labial frenula (Figure 3).
Panoramic radiograph showing agenesis of maxillary lateral incisors, mandibular incisors, and all 4 third molars.
CRID2018-8631602.004.jpg
PMC5828096_01_CRID2018-8631602.004.jpg
fig4
Lateral cephalogram.
CRID2018-8631602.005.jpg
PMC5828096_01_CRID2018-8631602.005.jpg
fig5
Cervical Vertebrae Maturation Index (CVMI), using lateral cephalogram (Figure 5), depicted the patient to be in CVMI Stage V.
Quad helix cemented to maxillary molars.
CRID2018-8631602.006.jpg
PMC5828096_01_CRID2018-8631602.006.jpg
fig6
Initial activation of 8 mm was done extraorally, and the bands were cemented with glass ionomer cement (Ketac Cem Glass Ionomer Cement, 3M) on maxillary molars (Figure 6).
Andrew's removable component with Ceka Preciline attachments.
CRID2018-8631602.007.jpg
PMC5828096_01_CRID2018-8631602.007.jpg
fig7
Bar and Clip attachments (Preci-Horix, Ceka) were used to secure removable and fixed component (Figure 7).