PMC8736701_01
Extensive port-wine stain since birth.
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fig1
Multiple erythematous/hyperpigmented macules.
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Multiple erythematous and/or hyperpigmented punched-out lesions, some with scaly appearance and/or atrophic surface, were noted on the trunk and proximal parts of extremities (Figure 2).
Dermal infiltration of spindle cells in a collagenous stroma containing abundant mucin intermixed with some mast cells.
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Histopathologic assessment showed dermal infiltration of spindle cells in a collagenous stroma containing abundant mucin intermixed with some mast cells which was more compatible with "progressive mucinous histiocytosis" (Figures 3 and 4). "Cutaneous mucinosis of infancy" and "self-healing juvenile cutaneous mucinosis" were also suggested as differential diagnoses.
A magnified view of histopathological changes seen in the patient's tissue sample.
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Histopathologic assessment showed dermal infiltration of spindle cells in a collagenous stroma containing abundant mucin intermixed with some mast cells which was more compatible with "progressive mucinous histiocytosis" (Figures 3 and 4). "Cutaneous mucinosis of infancy" and "self-healing juvenile cutaneous mucinosis" were also suggested as differential diagnoses.
PMC8736701_02
Remarkable resolution of port-wine stain following PDL therapy.
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Her port-wine stain considerably improved following 4 sessions of PDL (pulsed-dye laser) therapy and other cutaneous lesions getting better spontaneously (Figures 5 and 6).
Spontaneous resolution of cutaneous lesions of NLE.
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fig6
Her port-wine stain considerably improved following 4 sessions of PDL (pulsed-dye laser) therapy and other cutaneous lesions getting better spontaneously (Figures 5 and 6).