PMC9651021_01
General physical examination findings in a man with Mounier Kuhn Syndrome: (A) shows wasting and mild abdominal distension due to ascites, (B) shows grade 3 digital clubbing, (C) shows pitting oedema after removing stockings.
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On physical examination, he was sick-looking, severely wasted (37kgs body weight, height -160.5cm, BMI-14.4 kilogram per meters2; Figure 1A). He had proptosis grade 3 digital clubbing (Figure 1B), central and peripheral cyanosis and pretibial oedema (Figure 1C).
Chest x-ray images AP (A) and lateral (B), showing the dilated trachea (block arrow) and right principal bronchus (notched arrow) with diffuse reticulolinear opacities and cystic bronchiectasis of the lower lung zones.
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Figure 2 shows the chest X-ray.
Axial CT images (A) is soft tissue window demonstrating a dilated trachea (measurement calipers) and (B) is a lung window demonstrating a tracheal diverticulum (arrow).
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Figures 3-5show the High-resolution chest computed tomography (HRCT).    
Coronal CT scans, lung window: (A) demonstrates the grossly dilated and tortuous principal bronchi (measurement calipers), Right bronchus measures 4.25cm and left bronchus measures 3.81cm; (B) demonstrates cystic and varicose bronchiectasis.
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Figures 3-5show the High-resolution chest computed tomography (HRCT).    
CT images lung window: (A) demonstrating ground glass opacities and bronchiectasis in the right middle lobe (blue arrow) and (B) demonstrating mucus filled bronchi with air fluid levels (orange arrows).
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Figures 3-5show the High-resolution chest computed tomography (HRCT).    