PMC6218749_01
(a) and (b) Color fundus photo demonstrating macular atrophy and surrounding pseudodrusen OU. (c) and (d) FAF reveals hypoautofluorescence in areas of atrophy OU with a central island in the right macula.
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Peripapillary atrophy was also present along with scattered areas of peripheral pavingstone degeneration OU (Figures 1(a) and 1(b)). Fundus autofluorescence (FAF) showed well-defined areas of atrophy OU and sparing of the central fovea in the right eye (Figures 1(c) and 1(d)).
(a) and (b) SDOCT shows outer retinal and choriocapillaris atrophy with outer retinal tubulations OU.
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OCT (SDOCT) (Heidelberg Spectralis OCT, Heidelberg, Germany) revealed outer retinal and choriocapillaris atrophy and reticular pseudodrusen (Figures 2(a) and 2(b)). OCTA (Angioplex, Carl Zeiss Meditec, Dublin, CA) demonstrated marked absence of choriocapillaris flow (Figures 3(a) and 3(b)).
(a) and (b) OCTA reveals a marked decrease in choriocapillaris flow with large choroidal vessel flow present in the right (a) and left (b) eyes.
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fig3
OCT (SDOCT) (Heidelberg Spectralis OCT, Heidelberg, Germany) revealed outer retinal and choriocapillaris atrophy and reticular pseudodrusen (Figures 2(a) and 2(b)). OCTA (Angioplex, Carl Zeiss Meditec, Dublin, CA) demonstrated marked absence of choriocapillaris flow (Figures 3(a) and 3(b)).