PMC3659888_01
(a) Family pedigree of Case 1, (b) Family pedigree of Case 2   Bilateral pheochromocytoma,   Left sided pheochromocytoma with pancreatic neuroendocrine carcinoma The numbers in squares and circles represent the age of diagnosis of pheochromocytoma in each affected member
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F1
Family screening revealed bilateral pheochromocytomas in one sibling and her father [Figure 1b].
Magnetic resonance angiogram of Case 1 (a) showing dilatation of brachiocephalic trunk (b), dilatation of aortic root (c), stenosis of the celiac artery at its origin (d) and stenosis of right renal artery (e)
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F2
Magnetic resonance angiogram [Figure 2] showed dilatation of aortic root and the proximal ascending aorta (largest diameter = 41 mm).
PMC3659888_02
(a) Family pedigree of Case 1, (b) Family pedigree of Case 2   Bilateral pheochromocytoma,   Left sided pheochromocytoma with pancreatic neuroendocrine carcinoma The numbers in squares and circles represent the age of diagnosis of pheochromocytoma in each affected member
IJEM-17-163-g001.jpg
PMC3659888_02_IJEM-17-163-g001.jpg
F1
Family screening revealed bilateral pheochromocytomas in one sibling and her father [Figure 1b].
Computerized tomography of Case 2 showing calcification of aorta (a), calcification of coronary artery (b), beaded appearance of aorta on CT angiogram with calcification of both common iliac arteries (c) and right adrenal pheochromocytoma and paraganglioma at left renal hilum (d)
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F3
CT angiogram showed thickening of the aortic wall with characteristic beading of aorta suggestive of aortoarteritis [Figure 3].