PMC7499312_01
Chest X-ray showing the presence of a right-sided spontaneous pneumothorax with a midline shift to the left.
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The chest X-ray showed a right pneumothorax (Figure 1) that was drained.
CT scan showing overdistension of the right chest with parenchymal air cystic lesions involving the external segment of the middle lobe.
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A thoracic CT scan searching an underlying pathology revealed overdistension of the right hemithorax with parenchymal air cystic lesions involving the external segment of the middle lobe conducting to a malformation cystic adenomatoid, a fairly abundant right hydropneumothorax responsible for a compressive effect on the adjacent pulmonary parenchyma, and inflammation of the pleura (Figure 2).
Multiple resected fragments with a gelatinous component with necrotic fragments.
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Through an open thoracotomy, we found a gelatinous component in the right chest originated from the middle right lobe extending to the pleura and diaphragm; a middle lobectomy was performed with resection of the gelatinous component (Figure 3).The specimen weighed 194 g and measured 16 cm.
Photograph of pneumoblastoma type II showing malignant mesenchymal cell proliferation.
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Cytological finding confirmed macroscopically multiple fragments with polypoid cerebroid and necrotic component and rare cystic wall.Microscopically, the tumor proliferation had the double epithelial (Figure 4) and sarcomatous component (Figure 5).
Photograph of pneumoblastoma type II showing a multicystic structure with the epithelial component.
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Cytological finding confirmed macroscopically multiple fragments with polypoid cerebroid and necrotic component and rare cystic wall.Microscopically, the tumor proliferation had the double epithelial (Figure 4) and sarcomatous component (Figure 5).