PMC3271301_01
Gross findings. (A) Micrognathia, (B) Clubbing fingers, (C) Slim extremities compared with trunk.
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F1
Physical examination revealed micrognathia (Fig. 1A), clubbing fingers (Fig. 1B), and slim extremities compared with trunk (Fig. 1C).
Hyperpigmented, telangiectatic, and atrophic changes on the skin. (A) Trunk. (B) both axillae.
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F2
Dermatologic examination showed generalized hyperpigmented, telangiectatic, and atrophic changes with accentuation on both axillae (Fig. 2), antecubital, and popliteal fossae.
Linear brownish hyperkeratotic and sclerosing band on the skin. (A) Popliteal fossa. (B) Antecubital fossa.
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F3
Linear hyperkeratotic and sclerotic bands were found on the both antecubital and popliteal fossae (Fig. 3).
Histopathological findings of the skin. (A) Increased melanin pigments in the basal layer and sclerotic changes and telangiectasia in the upper dermis (H&E, x 40). (B) Fragmentations of elastic fibers in the dermis (Elastic stain, x 200).
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F4
Histopathologic finding revealed increased melanin pigments in the basal layer and sclerotic changes and telangiectasia in the upper dermis (Fig. 4A). The fragmentations of elastic fibers in the dermis were noted in elastic stain (Fig. 4B) consistent with a diagnosis of HSP.