PMC9550431_01
TEE horizontal view: right atrial mass (black arrow) in the area adjacent to the tricuspid valve. No visual obstruction of flow was identified on Doppler.
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fig1
A transesophageal echocardiogram (TEE) identified two tumors within the right atrium (Figures 1 and 2).
TEE horizontal view: right atrial masses in the area of the tricuspid valve and atrioventricular groove (blue arrow) and in the area of the atrioventricular groove (black arrow).
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fig2
A transesophageal echocardiogram (TEE) identified two tumors within the right atrium (Figures 1 and 2).
(a) Cardiac paraganglioma histology. Multiple large groups of characteristic Zellballen morphology (in black circles) with nests of uniform, polygonal chromaffin/chief cells surrounded by sustentacular support cells and well-formed vascular cuffing. (b) Cardiac paraganglioma histology. Characteristic Zellballen morphology (white circles) with nests of uniform, polygonal chromaffin/chief cells surrounded by sustentacular support cells and well-formed vascular cuffing.
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fig3
Immunohistochemistry confirmed neoplastic cells which stained positive for chromogranin and GATA binding protein 3 (GATA-3) and a solid nest-like arrangement partially demarcated by S100-positive sustentacular cells in a "Zellballen" pattern (Figures 3(a), 3(b) and 4).