PMC3690703_01
Neurofibromatosis Type 2. A 34-year-old man with mild hearing loss in the left ear. Axial computed tomography (parenchymal window) of the temporal bone shows subependymal calcification (arrow) at the foramen of Monro
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F1
Temporal bone CT [Figure 1a-d], showed subependymal calcification at the foramen of Monro [Figure 1a], choroid plexus calcifications within the lateral ventricles [Figure 1b], a small calcified lesion adjacent to the right cavernous sinus [Figure 1c], and a partially calcified midline mass adjacent to the fourth ventricle [Figure 1d].
Neurofibromatosis Type 2. A 34-year-old man with mild hearing loss in the left ear. Axial computed tomography (parenchymal window) of the temporal bone shows extensive choroid plexus calcifications within both atria (arrows) extending into the left temporal horn (arrowhead)
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F2
Cerebral MRI with intravenous contrast administration showed no major findings except an enhancing mass at the posterior aspect of the fourth ventricle Figure 2.
Neurofibromatosis Type 2. A 34-year-old man with mild hearing loss in the left ear. Axial computed tomography (parenchymal window) of the temporal bone reveals a small calcified lesion (arrow) adjacent to the right cavernous sinus
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F3
Inner ear MRI with the aid of fast imaging employing steady state acquisition (FIESTA) [Figure 3a] and contrast enhanced T1-weighted sequences with thin slices [Figure 3b] revealed bilateral small intracanalicular lesions consistent with schwannomas.
Neurofibromatosis Type 2. A 34-year-old man with mild hearing loss in the left ear. Axial computed tomography (parenchymal window) of the temporal bone shows a midline mass (arrow) with coarse calcifications at the posterior aspect of the fourth ventricle. Note the normal appearance of bilateral pontocerebellar cisterns
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F4
Spinal MRI [Figure 4a and b], which was performed to evaluate possible additional tumors, showed a mass causing focal cord expansion at C5-C6 level [Figure 4a] and multiple enhancing small intramedullary lesions [Figure 4b] consistent with ependymomas in the cervical cord.
Neurofibromatosis Type 2. A 34-year-old man with mild hearing loss in the left ear. Cerebral magnetic resonance. Sagittal postcontrast T1-weighted image shows an enhancing midline mass (arrow) within the posterior fossa.
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F5
Posterior fossa mass was operated and diagnosed as WHO Grade 2 ependymoma histopathologically [Figure 5].