PMC4084616_01
Mature cataract, port-wine stains, and asymmetric face in the right side.
CRIOPM2014-312030.001.jpg
PMC4084616_01_CRIOPM2014-312030.001.jpg
fig1
Anterior segment examination revealed mature cataract in the right eye (Figure 1) and normal findings in the left eye.
Port-wine stains over the right side of his face, ankle (a), and toes (b).
CRIOPM2014-312030.002.jpg
PMC4084616_01_CRIOPM2014-312030.002.jpg
fig2
During the physical examination, port-wine stains were noted over the right side of his face (Figure 2(a)), ankle, and toes (Figure 2(b)).
Cranial magnetic resonance imaging studies showed cortical atrophy discordant to his age (a), asymmetric vascular dilatations in the right hemisphere (b), hypertrophy in the right periorbital soft tissue (c), and choroidal plexus (d).
CRIOPM2014-312030.003.jpg
PMC4084616_01_CRIOPM2014-312030.003.jpg
fig3
After cataract surgery, funduscopic examination revealed severe vitreoretinopathy (a) and choroidal hemangioma (b) in the right eye. Fundus fluorescein angiography demonstrated leaking from dilated retinal vessels (c), ischemia, and neovascularization (d).
CRIOPM2014-312030.004.jpg
PMC4084616_01_CRIOPM2014-312030.004.jpg
fig4
After removing cataractous lens, we were able to examine the fundus that revealed severe vitreoretinopathy (Figure 4(a)) and choroidal hemangioma (Figure 4(b)). Fundus fluorescein angiography findings revealed dilated retinal vessels (Figure 4(d)), neovascularization, leaking (Figure 4(c)), and ischemia in the right eye.
Funduscopic examination (a) and fundus fluorescein angiography (b) findings were within normal limits in the left eye.
CRIOPM2014-312030.005.jpg
PMC4084616_01_CRIOPM2014-312030.005.jpg
fig5
The funduscopic examination (Figure 5(a)) and fundus fluorescein angiography (Figure 5(b)) findings were within normal limits in the left eye.