PMC9772262_01
Disease progression map. CSF, cerebrospinal fluid; ADEM, acute disseminated encephalomyelitis; MP, methylprednisolone; IVIG, intravenous immunoglobulin; PACNS, primary angiitis of the central nervous system; RTX, rituximab; FFA, Fundus fluorescein angiography.
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F1
Brain magnetic resonance imaging (MRI) showed hyperintensities on T2-weighted imaging and sagittal fluid-attenuated inversion recovery imaging (subcortical, periventricular, corpus callosum, and brainstem), with a quasi-circular region of restricted diffusion (Figure 1). Fundus fluorescein angiography displayed branch retinal artery occlusion and leakage of the micro-arterial wall (Figure 1). Ultimately, the diagnosis of SuS was confirmed based on the above findings (Figure 1), and subsequently, methylprednisolone and infliximab were administered.
The patient's audiogram.
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F2
Subsequently, a hearing test showed binaural sensorineural deafness (low-medium -frequency) (Figure 2).