PMC10076629_01
Severe ruptured blisters with skin lesions on both lower limbs.
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F1
Physical examination at birth indicated skin defects of both lower limbs with basal flushing and exudation, but no obvious signs of infection were found in the wounds (Figure 1).
(A) x-ray demonstrates a single bubble sign; (B) upper gastrointestinal angiography shows no contrast uptake beyond the stomach.
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F2
The results of coagulation function showed prothrombin time (PT) 16.0 s (ref. 9.8-12.1 s), active partial thromboplastin time (APTT) 110.2 s (ref. 25.0-31.3 s), international normalized ratio (INR) 1.38 (ref. 0.88-1.08). x-ray showed gas in the stomach but no inflation in the small intestine, which is considered pyloric obstruction (Figure 2A). Contrast medium accumulation in the stomach lumen was observed on upper gastrointestinal angiography, with no development in the duodenum or distal part (Figure 2B).
PMC10076629_02