PMC3461780_01
Sacrococcygeal mass extending to the vulva
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F1
The girl had cafe-au-lait pigmentations over her trunk with a slightly mobile, suprapubic mass and a sacral mass which extended to the perineum, involving the vulva [Figure 1].
Magnetic resonance imaging. The sagittal view shows a tumor involving the bladder (B) and the uterus (U)
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F2
Magnetic resonance imaging (MRI) of the pelvic region showed numerous soft tissue masses involving the bladder, uterus, and rectum [Figure 2].
Intraoperative findings showing the tumor involving the bladder
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F3
An incision biopsy showed a schwannoma and exploratory laparotomy revealed an infiltrating tumor involving the entire wall of the bladder [Figure 3], uterus, both fallopian tubes, the distal rectum, and anus.