PMC6982424_01
Myoclonus Recorded on Surface EMG in the Right Upper Limb and Accelerometer (Acc) Attached to the Right Index Finger. Some arrhythmic myoclonic jerks are shown with an arrow. Note the tremor-like postural irregular rhythmic myoclonus (*) in (B). (A) Rest; (B) extension of wrist; (C) drawing a spiral. Trap, trapezius; Bic, biceps; ECR, extensor carpi radialis; FCR, flexor carpi radials; FDI, first dorsal interosseous.
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Electrophysiological examination of the right upper limb revealed myoclonic bursts occurring at rest, posture and action, ranging between 38 and 108ms (mean of 73ms, calculated on 32 myoclonic bursts) (Figure 1).
Jerk-Locked EEG-EMG Back Averaging (JLBA) in Patient 1 with Two Series Comprising a Total of 200 Myoclonic Bursts Registered in the Right First Dorsal Interosseous (FDI). There is no evidence of a pre-myoclonic potential on EEG recordings.
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There was no premyoclonic potential on jerk-locked EEG-EMG back averaging (JLBA) (Figure 2) and C-reflex was absent.
PMC6982424_02