PMC2964807_01
Large bluish dilated vein on the scalp with venous sac in the midline
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F0001
This 2-year-old girl child born to nonconsanguineous parents presented with a history of large head and an abnormal compressible swelling on the right side of the scalp when she was 3 months old [Figure 1].
(A-C) T1-weighted images show the hypointense scalp vein with bony defect and venous sac. (D, E) The dilated ventricular system
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F0002
MRI showed a T1-hypointense swelling in the right parietal region with bony defect communicating with the superior sagittal sinus and ventricular dilatation [Figure 2]. MR venography showed a dilated large extracranial vein on the right parietal region communicating with the superior sagittal sinus through dilated diploic and emissary veins [Figure 3]. MR angiography was normal [Figure 4].
Magnetic resonance venography showing a large extracranial vein with venous sac in the midline communicating with the superior sagittal sinus
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F0003
MRI showed a T1-hypointense swelling in the right parietal region with bony defect communicating with the superior sagittal sinus and ventricular dilatation [Figure 2]. MR venography showed a dilated large extracranial vein on the right parietal region communicating with the superior sagittal sinus through dilated diploic and emissary veins [Figure 3]. MR angiography was normal [Figure 4].
Magnetic resonance angiography shows a normal arterial tree
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F0004
MRI showed a T1-hypointense swelling in the right parietal region with bony defect communicating with the superior sagittal sinus and ventricular dilatation [Figure 2]. MR venography showed a dilated large extracranial vein on the right parietal region communicating with the superior sagittal sinus through dilated diploic and emissary veins [Figure 3]. MR angiography was normal [Figure 4].
Digital subtraction angiography in the late venous phase showing the large extracranial vein communicating with the superior sagittal sinus through the emissary vein
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F0005
No dural arteriovenous fistula was found [Figure 5].