PMC4393836_01
Chest X-ray (posteroanterior view), revealing oligemic lung fields and right ventricular type cardiomegaly. RA, Right atrium; RV, Right ventricle
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F1
Chest roentgenogram (Figure 1) revealed an RV type of apex, inconspicuous pulmonary bay, left-sided aortic arch, and oligemic lung fields.
Echocardiographic parasternal long-axis view, revealing aortic override with a large ventricular septal defect (VSD)
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F2
Echocardiography (Figures 2 and Figure 3) demonstrated large sub-aortic perimembranous ventricular septal defect (VSD) with 50% aortic override, large ostium-secundum atrial septal defect (ASD), thickened septal leaflet of the tricuspid valve with severe tricuspid regurgitation, dilated and hypertrophied RV, dilated right atrium (RA), and thick-dysplastic pulmonary valve.
Echocardiographic apical four-chamber view, revealing atrial septal defect (ASD) and ventricular septal defect (VSD)
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F3
Echocardiography (Figures 2 and Figure 3) demonstrated large sub-aortic perimembranous ventricular septal defect (VSD) with 50% aortic override, large ostium-secundum atrial septal defect (ASD), thickened septal leaflet of the tricuspid valve with severe tricuspid regurgitation, dilated and hypertrophied RV, dilated right atrium (RA), and thick-dysplastic pulmonary valve.
Coronary angiogram, revealing a single coronary artery (SCA) giving rise to the right coronary artery (RCA), left circumflex coronary artery (LCX), and left anterior descending coronary artery (LAD)
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F4
Coronary angiograms (Figure 4) in standard and oblique views with caudal and cranial tilts confirmed the presence of a single coronary artery arising from the left coronary sinus giving rise to the right coronary artery (RCA) from its proximal segment and subsequently dividing into the left anterior descending (LAD) and left circumflex coronary arteries.