PMC4793795_01
The clinical examinations showed a complete cleft lip and palate (left side) and deletion of the central finger on the right hand, fusion of second and third finger of the left hand and fusion of the second and third toe on both feet.
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F1
Paper-thin, dry and reddened skin and sparse scalp hair were also visible (Figure 1).
After lip adhesion, 4 months of age.
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F2
For improved soft-tissue conditioning, lip adhesion was planned (Figure 2).
Swelling of the back of the tongue and exfoliation after the "all in one" closure and before re-intubation.
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F3
Nevertheless, after surgery, the child had to be re-intubated at the intensive care unit due to an exfoliative stomatitis and dramatic swelling of the back of the tongue with impairment of the upper respiratory tract (Figure 3).
Follow-up 6 months after surgery with harmonious upper lip and no abnormalities in the epidermis.
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F4
The further post-operative course of treatment was without complications (Figure 4).
PMC4793795_02
The clinical examination of the patient 3 h after birth shows the typical characteristics for the EEC-syndrome.
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F5
This case presents the sister of the above described boy, born 3 years and eight months later: Born at 38 week of gestation with a birth weight of 2'985 g she showed a bilateral cleft lip, syndactyly on all extremities and a conspicuous dryness of the skin (Figure 5).
Follow-up 4.5 months after surgery. No complications have occurred in wound healing due to the EEC-syndrome
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F6
The postoperative course of treatment was uneventful (Figure 6).