PMC7769674_01
Pedigree of the studied family.
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fig1
The transmission mode was recessive (Figure 1).
Clinical evaluation. (a) Occlusal view of maxillary arch. (b) Occlusal view of mandibular arch. (c) Intraoral photograph showing an anterior and posterior cross bite. (d) Bite registration in the correct occlusal vertical dimension.
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The left maxillary molar was decayed (Figures 2(a) and 2(b)). An anterior and lateral crossbite was diagnosed (Figure 2(c)). Aluwax ). An interocclusal rest space of 6 mm was evaluated (Figure 2(d)).
Radiographic evaluation. (a) Panoramic view of the jaws showing multiple unerupted supernumerary teeth. (b) Frontal radiograph showing a delayed closure of sagittal suture and the presence of Wormian bones. (c) Cone-beam radiograph of maxillary and mandibular arches showing a dilacerated root and inverted erupting pathway. (d) Sagittal cone-beam computed tomography section showing an incomplete formation of the left unerupted permanent incisor root. (e) Thorax radiograph showing hypoplasia of the left clavicle.
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fig3
They present a right eruption pathway (Figure 3(a)). The lower permanent incisors had submucosal situation (Figure 3(c) and 3(d)). The frontal radiograph showed the presence of multiple wormian bones, a widened sagittal suture, and an underdevelopment of the maxilla and paranasal sinuses (Figure 3(b)). The left clavicle was hypoplastic with a deformation of the vertebral column in the thorax X-ray (Figure 3(e)). The patient was very pleased and satisfied with her new appearance (Figure 3(b) and 3(c)).
Ultrastructural evaluation. (a) A scanning electron microscopy (zoom x2000) view showing the prismatic aspect of the enamel of the patient's temporary tooth. (b) A scanning electron microscopy (zoom x2000) view showing some dentinal tubules in longitudinal section.
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Dental treatment. (a) Extraction of the mandibular incisors and canines. (b) Interim maxillary and mandibular prostheses. (c) Prostheses adjusted in the mouth. (d) Final clinical view.
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fig5
After obtaining the patient's consent, the lower incisors and canines were extracted (Figure 5(a)).