PMC7381327_01
Summative timeline showcasing key findings of the patient's evolution and detailed treatment (case 1).
fped-08-00370-g0001.jpg
PMC7381327_03_fped-08-00370-g0001.jpg
F1
At 11 years old, when a donor was available, preoperative echocardiography and cardiac catheterization were performed (Figure 1) and the patient underwent HT with no intraoperative complications and favorable postoperative outcome. Postoperative echocardiography parameters are shown in Figure 1.
Case 1: Transthoracic echocardiography at the moment of diagnosis: (A) Apical and lateral LV trabeculations and intertrabecular recesses (arrows); (B) Non-compaction (red line) to compaction (green line) ratio in end-systole of >2.7 (12.5/4.5 mm); (C) LV trabeculations (white arrows) and intertrabecular recesses (red arrows) more visible in diastole; (D) Color Doppler echocardiography showing direct blood flow from LV cavity into the recesses (arrows) in diastole.
fped-08-00370-g0002.jpg
PMC7381327_01_fped-08-00370-g0002.jpg
F2
A thickened, non-compacted, endocardial layer was observed, with prominent trabeculations and intertrabecular recesses located at the apex and mid-lateral wall of the LV (Figure 2A). The non-compaction to compaction (NC/C) ratio assessed in end-systole was >2.7 (Figure 2B). The trabeculations and intertrabecular recesses were more visible in diastole (Figure 2C). Doppler echocardiography revealed direct blood flow from LV cavity into the recesses (Figure 2D).
PMC7381327_02
Summative timeline showcasing key findings of the patient's evolution and detailed treatment (case 1).
fped-08-00370-g0001.jpg
PMC7381327_03_fped-08-00370-g0001.jpg
F1
At 11 years old, when a donor was available, preoperative echocardiography and cardiac catheterization were performed (Figure 1) and the patient underwent HT with no intraoperative complications and favorable postoperative outcome. Postoperative echocardiography parameters are shown in Figure 1.
PMC7381327_03
Summative timeline showcasing key findings of the patient's evolution and detailed treatment (case 1).
fped-08-00370-g0001.jpg
PMC7381327_03_fped-08-00370-g0001.jpg
F1
At 11 years old, when a donor was available, preoperative echocardiography and cardiac catheterization were performed (Figure 1) and the patient underwent HT with no intraoperative complications and favorable postoperative outcome. Postoperative echocardiography parameters are shown in Figure 1.
PMC7381327_04
Summative timeline showcasing key findings of the patient's evolution and detailed treatment (case 2).
fped-08-00370-g0003.jpg
PMC7381327_07_fped-08-00370-g0003.jpg
F3
Echocardiography parameters are shown in Figure 3.
PMC7381327_05
PMC7381327_06
Summative timeline showcasing key findings of the patient's evolution and detailed treatment (case 2).
fped-08-00370-g0003.jpg
PMC7381327_07_fped-08-00370-g0003.jpg
F3
Echocardiography parameters are shown in Figure 3.
Case 2: Multi-detector Computed Tomography (MDCT) angiography at the moment of diagosis: (A) Axial reconstruction and (B) Coronal reconstruction: Black arrows show prominent trabeculations and deep intertrabecular recesses located at the apex and lateral wall of the LV; (C) Sagital reconstruction, short axis plane showing non-compaction (red line) to compaction (green line) ratio of > 3.3 (17,9/5,39 mm).
fped-08-00370-g0004.jpg
PMC7381327_06_fped-08-00370-g0004.jpg
F4
Mid-lateral and apical LV prominent trabeculations and intertrabecular recesses were observed (Figures 4A,B). The NC/C ratio was >3.3 (Figure 4C).
PMC7381327_07
Summative timeline showcasing key findings of the patient's evolution and detailed treatment (case 2).
fped-08-00370-g0003.jpg
PMC7381327_07_fped-08-00370-g0003.jpg
F3
Echocardiography parameters are shown in Figure 3.