PMC8524673_01
(A) Fatty change and ballooned hepatocytes with mild portal chronic inflammation (H&E, X200). (B) Portal fibrosis with slender septa extending from portal tracts and surrounding steatosis (Trichrome stain, X200).
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F1
The liver biopsy showed moderate (50-60%) macrovesicular steatosis, mild portal inflammation with lymphocytes and eosinophils, and grade II to III periportal fibrosis with slender portal septa (Figures 1A,B).
Timeline of our patient's presentation throughout diagnosis and treatment of Wilson disease and GLUT-1 deficiency.
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