PMC6069986_01
(a, b) The fundus evaluation revealed widespread outer retinal atrophy with visible large choroidal vessels. Marked temporal sub-retinal fibrosis was noted with foveal atrophy which was more marked in the left eye. (c, d) OCT revealed evidence of outer retinal atrophy with associated sub-foveal scarring. RPE discontinuity can be visualised in the left eye. (e, f) Fundus fluorescein angiogram noted a choroidal hyperfluorescence due to extensive windrow defects, suggestive of RPE loss
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Fig1
Fundus examination (Fig. 1a, b) showed presence of widespread outer retinal atrophy with visible choroidal vessels and peripheral sub-retinal scarring. We carried out an OCT evaluation (Fig. 1c, d) of the patient which showed evidence of outer retinal atrophy with associated sub-foveal scarring which was more pronounced in the left eye. An examination of the medical records revealed an old fundus fluorescein angiogram, from 10 years ago, which showed prominent areas of choroidal hyperfluoresence due to extensive window defects, indicative of RPE damage (Fig. 1e, f).