PMC3262527_01
Xanthoma on elbow skin in, (a) an atheroma protruding into the aortic lumen in (b) (red star).
CARDIOLOGY2011-804767.001.jpg
PMC3262527_01_CARDIOLOGY2011-804767.001.jpg
fig1
On inspection, the xanthomas on her elbow and knee were rather evident (Figure 1(a)). TEE also showed a diffuse narrowing of the aorta from annular level to the descending thoracic aorta (Figure 1(b)). The diameters of the aorta were measured as 1.1, 1.4, and 1.5 cm at the levels of the aortic annulus, sinotubular junction, and ascending aorta, respectively, (body surface area was 1.56 m2).
MR angiogram showing diffuse narrowing of the entire aorta.
CARDIOLOGY2011-804767.002.jpg
PMC3262527_01_CARDIOLOGY2011-804767.002.jpg
fig2
Magnetic resonance angiography confirmed the diffuse narrowing of the entire aorta (Figure 2).
Critical ostial and mid portion stenosis of the right coronary artery and a moderate ostial stenosis of the LMCA on coronary angiography.
CARDIOLOGY2011-804767.003.jpg
PMC3262527_01_CARDIOLOGY2011-804767.003.jpg
fig3
Coronary angiograms showed a critical ostial stenosis of the right coronary artery and a moderate ostial narrowing of the left main coronary artery (LMCA) (Figure 3).