PMC4034297_01
Front and back views. Dorsal dextroconvex , "S"-shaped scoliosis and deformed thorax. Fixed retraction of elbow flexion muscles (biceps, brachial, brachioradial) with bilateral elbow ankylosis in 90 degrees flexum
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F1
We also noticed dorsal dextroconvex, "S" shaped scoliosis and deformed thorax (Fig. 1 a,band 2), I cirt=3,5cm, Schober index=1cm; retraction of pectoral muscles (with a 4,2cm hard, bone tissue accumulation at the medial third, across the anterior axillary line), also the deltoid, coracobrachial muscles with the fixation of scapulohumeral joints in an anatomical position and with the presence of hard bone consistency accumulations of 4/3cm at postero-lateral inferior third of the right forearm and at inferior third of right arm. Regarding both upper limbs we observed a fixed retraction of the elbow flexion muscles (biceps, brachial, brachioradial) with bilateral elbow ankylosis in 90 degrees flexum (Fig. 1-3).
Lateral view. Lordosis, dextroconvex , "S"-shaped scoliosis and deformed thorax. Fixed retraction of elbow flexion muscles (biceps, brachial, brachioradial) with bilateral elbow ankylosis in 90 degrees flexum
JMedLife-06-454-g002.jpg
PMC4034297_01_JMedLife-06-454-g002.jpg
F2
We also noticed dorsal dextroconvex, "S" shaped scoliosis and deformed thorax (Fig. 1 a,band 2), I cirt=3,5cm, Schober index=1cm; retraction of pectoral muscles (with a 4,2cm hard, bone tissue accumulation at the medial third, across the anterior axillary line), also the deltoid, coracobrachial muscles with the fixation of scapulohumeral joints in an anatomical position and with the presence of hard bone consistency accumulations of 4/3cm at postero-lateral inferior third of the right forearm and at inferior third of right arm. Regarding both upper limbs we observed a fixed retraction of the elbow flexion muscles (biceps, brachial, brachioradial) with bilateral elbow ankylosis in 90 degrees flexum (Fig. 1-3).
Soft tissue calcifications
JMedLife-06-454-g003.jpg
PMC4034297_01_JMedLife-06-454-g003.jpg
F3
Regarding both upper limbs we observed a fixed retraction of the elbow flexion muscles (biceps, brachial, brachioradial) with bilateral elbow ankylosis in 90 degrees flexum (Fig. 1-3).
CT aspect. Dextro-converse scoliosis; bone thorax deformation. Pulmonary fibrosis.
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F4
C2-C3. Chest radiography and CT were performed which revealed soft tissue lesions of pulmonary fibrosis (Fig. 4 and 5) and calcification of the periarticular soft tissue extended to the lower limbs, glenohumeral joints and muscles round the backbone (Fig. 4 - 9), spine with marked kyphoscoliosis deformities which contributed to increased restrictive ventilatory dysfunction.
CT aspect. Marked kyphoscoliosis deformities. Lateral view.
JMedLife-06-454-g005.jpg
PMC4034297_01_JMedLife-06-454-g005.jpg
F5
C2-C3. Chest radiography and CT were performed which revealed soft tissue lesions of pulmonary fibrosis (Fig. 4 and 5) and calcification of the periarticular soft tissue extended to the lower limbs, glenohumeral joints and muscles round the backbone (Fig. 4 - 9), spine with marked kyphoscoliosis deformities which contributed to increased restrictive ventilatory dysfunction.