PMC7154070_01
PMC7154070_02
PMC7154070_03
Erythema in palms accompanied by intense Raynaud's phenomenon.
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F1
On physical examination malar rash and intense Raynaud's phenomenon were noted (Figure 1).
Magnetic resonance coronary angiography in a Whole-Heart iPAT sequence in a short axis view. Red Arrow: normal proximal right coronary artery 3 mm (z-score + 054), with dilated mid right coronary artery 6 mm (z-score + 7.35) and dilated distal right coronary artery 6 mm (z-score + 8.07). Ao, aorta; RA, Right atrium; LA, Left atrium (Courtesy of Dr. Roberto Cano).
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F2
Echocardiogram and heart MRI revealed large ectasia of the main left coronary artery (z-score + 6.12), large ectasia of the circumflex artery (z-score + 5.19), with normal proximal right coronary artery and large ectasia of the mid right coronary artery (z-score + 7.35) with mild mitral regurgitation (Figure 2).