PMC9203825_01
(A) Hypsarrhythmia: discontinuous, asynchronous background with high-voltage irregular slow waves and multifocal spikes. (B) An electrodecremental event. The clinical spasm () was associated with sudden attenuation in the voltage.
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The neurology team reviewed him, and an electroencephalogram (EEG) was done, which showed hypsarrhythmia ( Figure 3A ), in keeping with the diagnosis of IS. EEG recording of electrodecremental response during an episode of spasms was noted ( Figure 3B ).
Timeline of events from day 3 of life to 6 years of age. CBG, capillary blood glucose; DZX, diazoxide; GIR, glucose infusion rate; HH, hyperinsulinemic hypoglycemia; RFS, resolution fast study; SFS, safety fast study; D, day of life; M, months; Y, years.
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He will have a repeat Synacthen test when he turns 7-year-old ( Figure 4 ).