PMC10424440_01
Chest radiograph image: decreased volume of the left lung, shifting of the mediastinum to the left, enlargement of the right lung hilum.
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F1
Chest radiographs showed a decreased volume of the left lung, shifting of the mediastinum to the left, and enlargement of the right lung hilum (Figure 1). Atypical vascular branches dividing from the aorta and forming the vasculature of the left lung were also visible (Figure 3C, Supplementary File S1).
A transthoracic echocardiogram: (A) color Doppler flow not registered in the left pulmonary artery; (B) suspected right arch of aorta and anomaly of subclavian arteries.
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F2
A transthoracic echocardiogram revealed absence of the left pulmonary artery, and right arch of aorta and anomaly of subclavian arteries was suspected (Figure 2).
(A) Chest CT angiography scan, coronary reconstruction: elongation of the aorta and an aberrant right subclavian artery with KD; (B) chest CT angiography scan: absence of the left pulmonary artery; (C) chest CT angiography reconstruction: atypical vascular branches dividing from the aorta and forming the vasculature of the left lung; Abb.: Ao, aorta; AsA, ascending aorta; DA, descending aorta; PA, pulmonary artery; RPA, right pulmonary artery; star, abberant right subclavian; triangle, left subclavian artery; grey arrow, KD; black arrow, atypical branch; white arrow, anomalous left lung vascular bundle.
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F3
The diagnosis was confirmed by computed tomography (CT) scans of the chest that demonstrated elongation of the aorta and an aberrant right subclavian artery with Kommerell's diverticulum (KD) (Figure 3A), as well as absence of the left pulmonary artery (Figure 3B), with a hypoplastic upper lobe of the left lung. Atypical vascular branches dividing from the aorta and forming the vasculature of the left lung were also visible (Figure 3C, Supplementary File S1).