PMC3217590_01
(a) Coronal CT revealing a well-circumscribed heterogenic mass lateral to the right kidney with appearance of a giant angiomyolipoma measuring 129.2 x 51.5 mm. (b) Axial CT appearance of the right renal angiomyolipoma measuring 57.3 x 40.3 mm. Small intraparenchymatous cystic lesions were present.
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Several small intraparenchymatous cystic lesions less than 14 mm were present (Figure 1).
(a) Coronal CT revealing pulmonary lymphangioleiomyomatosis with a moderate degree of pulmonary cystic affectation. Three lesions in each lung are identified by arrows. (b) Coronal CT revealing a marked resolution of pulmonary cysts after a 6-month treatment with low-dose rapamycin. One lesion in the right lung and three in the left had become imperceptible (arrows and asterisks).
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CT showed innumerable thin-walled cystic air spaces of different sizes throughout the lung parenchyma, characteristic of pulmonary LAM (Figure 2(a)). A thoracic-abdominal CT showed radiological improvement in the LAM lesions 6 months after the initiation of rapamycin therapy (Figure 2(b)).
MRI showing the right kidney 2 months after kidney-sparing conservative surgery. (a) Coronal appearance of the right kidney. (b) Axial appearance of the right kidney. Good kidney preservation was apparent.
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An MRI performed two months later revealed a right kidney well preserved with only small intraparenchymatous AMLs (Figure 3). At that time, the serum creatinine was 0.7 mg/dL (61.88 mumol/L). 
(a) Axial CT appearance of the right kidney after a 12-month treatment with low-dose rapamycin. (b) Axial MRI appearance of the right kidney after a 12-month treatment with low-dose rapamycin. No angiomyolipomas regrowth was apparent. Only small intraparenchymatous cystic lesions less than 14 mm were present.
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After 12 months, the right kidney remained well preserved with only small intraparenchymatous AMLs (Figure 4).