PMC9500375_01
PMC9500375_02
The girl has mild cyanosed lips (A), digital clubbing in toes (B) and fingers (C) of high-density shadows in both lungs. Electrocardiogram (ECG) and echocardiogram were both normal.
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F1
On physical examination, we found the girl had cyanosed lips and acropachy (see Figure 1).
(A,B) Computer tomography angiography (CTA) showed the splenic vein (SV) joined the superior mesenteric vein (SMV) and then flowed upward into the inferior vena cava (IVC) directly.
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F2
We came to a conclusion that the girl was a patient of abernethy malformation (see Figure 2).
(A) Delayed splenic arteriography showed that the splenic vein (SV) joined the superior mesenteric vein (SMV), which merged into the inferior vena cava (IVC) directly. (B) The inferior vena cava balloon occlusion test showed a tiny branch of the intrahepatic portal vein (the black arrow).
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F3
We also performed the inferior vena cava balloon occlusion test, which can not only clearly show the confluence of the splenic vein and superior mesenteric vein with the inferior vena cava, but also helped us find a tiny branch of the intrahepatic portal vein (see Figure 3).