PMC7027183_01
The patient aged 15 with his mother and younger sister, showing the large FCP in the right temporal region.
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The patient, aged 80 years on most recent examination in 2018, had an onset of tonic- clonic seizures at eleven months old, following earlier appearance in infancy of a large cephalic plaque (Figure 1).
Frontal and right lateral views of the patient aged 41 showing severe angiofibromas (2a) and the FCP (2b).
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Examination at 41years noted the cephalic plaque on the right temple measuring 92x90mm (from scale photographs) on its longest axis, and multiple facial angiofibromas (Figure 2a,b).
Frontolateral and right lateral views of the patient aged 80 showing less vascularization of the angiofibromas (3a) and resolution of the FCP (3b).
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At 80 years he was having 1-2 partial seizures per week, controlled with Levetiracetam (Keppra), and clonazepam, and his angiofibromas had lessened in intensity, redness and size (Figure 3a) compared to age 41. His cephalic plaque had a residual diameter of 88x87mm with a small ridge remaining at the frontal border and the majority of the plaque area is now confluent with the scalp skin (Figure 3b).