PMC4896234_01
27-year-old man with Ehlers-Danlos syndrome, type IV. Axial CT with contrast of the head, highlighting dilated right internal carotid artery with a surrounding crescent of soft tissue density.
gr1.jpg
PMC4896234_01_gr1.jpg
fig1
The patient underwent a head CT with contrast, which showed a vascular abnormality involving the right carotid artery (Fig. 1).
27-year-old man with Ehlers-Danlos syndrome, type IV. Axial magnetic resonance T2 image of the head, highlighting dilated right internal carotid artery with a surrounding crescent of intermediate signal.
gr2.jpg
PMC4896234_01_gr2.jpg
fig2
Brain MRI showed unremarkable brain parenchyma and identified an abnormality of the high cervical right internal carotid artery (Fig. 2).
27-year-old man with Ehlers-Danlos syndrome, type IV. Coronal CT with contrast, demonstrating multiple sites of stenosis in left and right vertebral arteries.
gr3.jpg
PMC4896234_01_gr3.jpg
fig3
An additional neck CT with contrast demonstrated several areas of narrowing and dilatation of the left vertebral artery (Fig. 3). Additionally, there was an isolated area of stenosis of the right vertebral artery with post-stenotic dilatation (Figure 3, Figure 4).
27-year-old man with Ehlers-Danlos syndrome, type IV. Three-dimensional reconstruction from neck CT, demonstrating saccular dilatation of the right vertebral artery.
gr4.jpg
PMC4896234_01_gr4.jpg
fig4
Additionally, there was an isolated area of stenosis of the right vertebral artery with post-stenotic dilatation (Figure 3, Figure 4).
27-year-old man with Ehlers-Danlos syndrome, type IV. Coronal CT with contrast, demonstrating narrowing of the left subclavian artery (without color in 5A, filled in red in 5B) with a surrounding crescent of soft tissue density (without color in 5A, outlined in yellow in 5B).
gr5.jpg
PMC4896234_01_gr5.jpg
fig5
The patient also underwent a chest CT, which demonstrated an abnormality of the left subclavian artery, with a crescentic rim of soft tissue tracking with the vessel, beginning at its origin (Figure 5, Figure 6).
27-year-old man with Ehlers-Danlos syndrome, type IV. Axial CT with contrast, demonstrating narrowing of the left subclavian artery (without color in 6A, filled in red in 6B) with a surrounding crescent of soft tissue density (without color in 6A, outlined in yellow in 6B).
gr6.jpg
PMC4896234_01_gr6.jpg
fig6
The patient also underwent a chest CT, which demonstrated an abnormality of the left subclavian artery, with a crescentic rim of soft tissue tracking with the vessel, beginning at its origin (Figure 5, Figure 6).