PMC7744754_01
(A) Spontaneous bursts of repetitive spikes with an occipital predominance associated with myoclonic jerks. (B) EEG showing normal posterior background and a non-sustained photoparoxysmal response associated with multifocal myoclonic jerks following stimulation at 14 Hz.
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F1
Her EEG revealed a normal posterior background as well as frequent bursts and fragments of generalized spike and polyspike and wave discharges (GPSWD) with an occipital amplitude predominance, commonly associated with myoclonic jerks (Figure 1A). Intermittent photic stimulation at a frequency of 14 Hz triggered bursts of posteriorly predominant repetitive spikes that were associated with multifocal myoclonus, following which the photic stimulation was aborted (Figure 1B).
(A) Fixation off sensitivity. (B) REM sleep. A peculiar pattern consisting of repetitive spikes over the parasagittal derivations associated with fragmentary minimyoclonus of the right hand.
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F2
The epileptiform discharges and associated myoclonic jerks persisted as long as her eyes remained closed and were immediately aborted upon eye opening (Figure 2A). During REM sleep, a peculiar pattern consisting of bursts of repetitive parasagittal spikes associated with fragmentary minimyoclonus of the hands was seen (Figure 2B).