PMC3861857_01
a Lens partially subluxated into the anterior chamber. The crystalline lens is incarcerated in the pupil. b The whole corneal endothelium is touched by the iris and crystalline lens.
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F1
The left pupil was irregular and anteriorly displaced, touching the endothelium of the cornea (fig. 1).
A subluxated lens (white arrows) and displaced iris (white arrowheads), touching the whole corneal endothelium, are detected by optical coherence tomography.
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F2
Anterior segment optical coherence tomography revealed the partially subluxated lens, which was incarcerated in the pupil, and touching the endothelium of the cornea (fig. 2).
a Chest radiograph revealed normal cardiac and aortic shape. No abnormal lesion was visible in the parenchyma of either lung. Scoliosis of spine was not found. b, c There was no gross skeletal abnormality such as arachnodactyly or brachydactyly on hands or feet.
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F3
There was no gross craniofacial abnormality or any skeletal abnormality on his spine and extremities (fig. 3).
a Dry vitrectomy was performed to get enough retrolental space and prevent sudden decreasing intraocular pressure after lens extraction. b Intracapsular lens extraction was performed with a lens spoon.
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F4
Partial pars plana dry vitrectomy was performed (fig. 4a). The whole lens was extracted with a lens spoon, without difficulty (fig. 4b).