PMC5278205_01
(a), (b) Spade-shaped incisors, pointed cusps, and spacing between teeth in case 1. (c) Orthopantomograph showing thin enamel with normal radio density. (d) Spinal radiographs revealing kyphoscoliosis and tongue-like projections from anterior surface of vertebral bodies in case 1.
CRID2017-6176372.001.jpg
PMC5278205_01_CRID2017-6176372.001.jpg
fig1
Two siblings, a 13-year-old girl (case 1, Figures 1(a)-1(d)) and a 10-year-old boy (case 2, Figures 2(a)-2(d)) of normal intelligence had come to Chettinad Dental College and Research Institute, Chennai, with a complaint of decayed teeth. On oral examination, exposed teeth with sharp cusps and rough enamel texture were found (Figures 1(a), 1(b), 2(a), and 2(b)). The orthopantomograph showed thin hypoplastic enamel of normal radiodensity (Figures 1(c) and 2(c)). The lateral spinal view revealed anterior beaking of the vertebral body (Figure 1(d)).
(a), (b) Spade-shaped incisors, pointed cusps, and spacing between teeth in both maxillary and mandibular teeth in case 2. (c) Orthopantomograph showing thin enamel with normal radio density. (d) Pelvic radiograph showing shallow acetabula and square-shaped femoral head in case 2.
CRID2017-6176372.002.jpg
PMC5278205_01_CRID2017-6176372.002.jpg
fig2
Two siblings, a 13-year-old girl (case 1, Figures 1(a)-1(d)) and a 10-year-old boy (case 2, Figures 2(a)-2(d)) of normal intelligence had come to Chettinad Dental College and Research Institute, Chennai, with a complaint of decayed teeth. On oral examination, exposed teeth with sharp cusps and rough enamel texture were found (Figures 1(a), 1(b), 2(a), and 2(b)). The pelvic view radiograph revealed an irregularly outlined square-shaped head of the femur and coxa valga defect (Figure 2(d)).