PMC9200443_01
(A) Subcostal sagittal 2D echocardiographic view showing anomalous superior vena cava (SVC) connection to the left atrium (LA) and inferior vena cava (IVC) connection to the right atrium (RA). (B) Subcostal sagittal color doppler echocardiographic view showing anomalous superior vena cava (SVC) connection to the left atrium (LA). (C) Suprasternal 2D echocardiographic view showing anomalous superior vena cava (SVC) connection to the left atrium (LA). AO: aorta, RUPV: right upper pulmonary vein, LPVS: lower pulmonary vein.
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There was evidence of abnormal connection of right sided superior vena cava (SVC) draining to the left atrium (LA) with anomaly of right upper pulmonary vein (RUPV) return and intact atrial septum (Fig. 1).
(A) Oblique coronal cut (MRI still image) through the superior vena cava (SVC)-left atrium (LA)-left ventricle (LV) with dark blood technique, (note the anomalous right upper pulmonary vein (RUPV) open to right superior vena cava (RSVC). (B) Contrast enhanced 3D MRA image of the right SVC draining the right lower pulmonary vein before entering LA.(C) 3D volume rendered surface shaded-MRA showing RSVC to LA and RUPV connected to Lower part of SVC, (posterior view) Note: (right lower pulmonary vein (RLPV) connect normally to LA along with the left veins).
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The diagnosis was confirmed by cardiac magnetic resonance imaging (CMRI) (Fig. 2), which also revealed the unique extra abnormality of partial anomalous pulmonary venous return (PAPVR) whereas the right upper pulmonary vein joins the SVC before it enters to the LA.