PMC4809448_01
A, Back. B, Lips.
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A previously healthy 7-year-old girl from the city of Valledupar, Colombia, presented to a different Institution in March 2009, with a 2-month history of severe depression, oral ulcers, denuded lips, and progressive bullae involving the face, extremities, and lower back and affecting 40% of her body surface (Figs 1 and 2).
A, Finger. B, Soles.
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A previously healthy 7-year-old girl from the city of Valledupar, Colombia, presented to a different Institution in March 2009, with a 2-month history of severe depression, oral ulcers, denuded lips, and progressive bullae involving the face, extremities, and lower back and affecting 40% of her body surface (Figs 1 and 2).
Skin biopsy taken before treatment initiation shows acantholytic intraepidermal vesicular dermatitis suggestive of vulgaris pemphigus.
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She had pemphigus vulgaris diagnosed by skin biopsy (Fig 3) and direct immunofluorescence and received treatment with oral prednisone, thalidomide, and azathioprine, with minimal improvement.
Abdominal ultrasound scan shows a 55-mm, hypoechoic, solid mass with low resistance.
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Salmonellosis was documented, and an abdominal ultrasound scan found a 55-mm vascularized mass in the right flank (Fig 4); biopsy of the mass showed an inflammatory myofibroblastic tumor (Fig 5).
Biopsy of the abdominal mass found a fusocellular lesion associated with a mononuclear inflammatory infiltrate. A histologic diagnosis of an inflammatory myofibroblastic tumor was made.
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Salmonellosis was documented, and an abdominal ultrasound scan found a 55-mm vascularized mass in the right flank (Fig 4); biopsy of the mass showed an inflammatory myofibroblastic tumor (Fig 5).