PMC4732263_01
Axial noncontrast (a) computed tomography images shows a well-defined intraconal mass in the posterior right orbit. Postcontrast image (b) heterogenous enhancement of the lesion causing proptosis and medial displacement of optic nerve
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F1
Computed tomography (CT scan) revealed a well-defined intraconal mass in the posterior right orbit with postcontrast heterogenous enhancement causing proptosis and medial displacement of optic nerve [Figure 1].
Magnetic resonance sagittal images shows a retro-orbital lesion of hypointense signal on T1-weighted (a) with postcontrast T1-weighted image (b) revealing heterogenous enhancement of the lesion
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F2
Postcontrast T1-weighted image revealed a heterogenous enhancement of the lesion [Figure 2].
(a) Tumor revealing patternless fibroblastic proliferation and vascular channels with pericytomatous arrangement (H and E, x100) (b) spindle cells growing in a haphazard manner in a variable cellular stroma described as "patternless pattern" (H and E, x400)
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F3
There was no significant cellular atypia and mitosis was 1-2/10 high-power fields [Figure 3].
Tumor cells with strong and diffuse positivity to CD34 (a) but negativity for S-100 (b)
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F4
On immunohistochemistry, the tumor cells had strong and diffuse positivity to CD34, vimentin and bcl-2 but negativity for S-100, progesterone receptor, smooth-muscle actin (SMA), and cytokeratin [Figure 4].