PMC3177382_01
(A) Cutaneous pigmentation of periorbital and malar region on the left side of the face, (B) Pigmentation of lower and lateral part of left eye sclera, (C) Cutaneous pigmentation over the pinna of the left ear, (D) Left buccal mucosa showing diffuse areas of pigmentation.
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Superiorly, it extended to the hairline on the same side, inferiorly to an imaginary line joining corner of the mouth to left ear tragus (Figure 1A). Bluish-blackish discoloration of the sclera and pinna were noticed on the same side (Figures 1B and 1C). Brownish-black diffuse pigmentation was noticed on the buccal mucosa of the same side extending anteriorly from the angle of the mouth to the retro-molar area, and superio-inferiorly to the depth of the buccal sulcus (Figure 1D).