PMC3523445_01
Electrocardiogram of a patient with Fahr's disease showing incomplete right bundle branch block with left anterior fascicular block, and normal PR interval during sinus rhythm
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F1
Her echocardiogram was normal and her baseline ECG showed incomplete right bundle branch block with left anterior fascicular block, normal PR/QT interval (Figure 1) with intermittent narrow QRS CHB and a ventricular rate of 40 beats per minute (bpm) (Figure 2).
Electrocardiogram of a patient with Fahr's disease showing intermittent narrow QRS complete heart block with a ventricular rate of 40 beats per minute
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F2
Her echocardiogram was normal and her baseline ECG showed incomplete right bundle branch block with left anterior fascicular block, normal PR/QT interval (Figure 1) with intermittent narrow QRS CHB and a ventricular rate of 40 beats per minute (bpm) (Figure 2).
Electrocardiogram of a patient with Fahr's disease showing intermittent advanced varying atrioventricular blocks
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F3
During the hospitalization period, she developed recurrent Stokes-Adams attacks with seizures and the monitor demonstrated intermittent advanced varying atrioventricular (AV) blocks with wide QRS escape rhythm suggesting infrahisian block (Figure 3).
Monitor rhythm strip of a patient with Fahr's disease showing prolonged ventricular (P-wave) asystole with occasional ventricular escape beats (The atrial rate during these advanced AV blocks was 250-300 bpm indicating either atrial tachycardia or atrial flutter)
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F4
This was followed by asystolic cardiac arrest with monitor indicating prolonged P-wave asystole (Figure 4).
Brain CT scan demonstrating bilateral symmetric basal ganglia calcification in a patient with Fahr's disease and isolated cardiac conduction system disease
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F5
Brain CT scan in our hospital confirmed bilateral "cloudy" looking symmetric basal ganglia calcification (Figure 5).