PMC4008904_01
Facial nevus flammeus involving V1 and V2 dermatomes of trigeminal nerve with upper lip hypertrophy
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F1
On examination, patient had bilateral capillary hemangioma involving upper two-thirds of the face as well as both eyelids [Figure 1].
Oral involvement showing gingival hypertrophy
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F2
The upper lip was protruding and hypertrophied along with upper gingival hypertrophy [Figure 2].
Dilated and telangiectatic episcleral vessels in right eye
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F3
There was episcleral telangiectasia in the inferonasal quadrant of OD [Figure 3].
(a) Dilated and tortuous retinal blood vessels in right eye (b) Normal retinal vessels in left eye. Optic disks showing bilateral advance glaucomatous cupping
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F4
OU. Ophthalmoscopically and angiographically dilated tortuous central retinal vessels with arteriovenous malformation were seen in superior retina of OD [Figure 4] while the retinal vessels were of normal caliber in OS.
Contrast-enhanced MRI T1-weighted images showing (a) Dilated medullary vein (white arrow) and dilated choroid plexus (black arrow) on right side (b) Bilaterally dilated lateral ventricles
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F5
The lateral ventricles were also enlarged [Figure 5].