PMC3617621_01
PMC3617621_02
The patient had had a white forelock of hair
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F0001
On examination, he had a white forelock of hair and massively distended abdomen, pale irises, and absence of reaction to any sound (Figure 1).
Radiographic X-Ray revealed dilated bowel loops but no air-fluid levels or pelvic gas
PAMJ-14-60-g002.jpg
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F0002
Radiographic investigations revealed dilated bowel loops but no air-fluid levels or pelvic gas (Figure 2).
Intra-operatively, the colon and distal ileum were found contracted; the ileum proximal to the transition zone was distended
PAMJ-14-60-g003.jpg
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F0003
An exploratory laparotomy was undertaken revealed distended proximal jejunal and ileal loops, the 30 cm of terminal ileum and the colon were contracted (Figure 3).