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Craniospinal MRI (a-d) and temporal bone CT (e) images. Spine MRI reveals a solid tumour mass hyper intense on sagittal T2-weighted images (a, white arrows) with mild and inhomogeneous contrast enhancement on Gd-enhanced sagittal T1-weighted images (b, black arrowheads). Brain MRI axial STIR show bilateral frontal periventricular nodules of gray matter heterotopias (c, black arrowheads) and an area of abnormal cerebella foliation (d, white arrowhead). Temporal bone CT scan depicts bilateral digenesis of the lateral semicircular canals and vestibules forming a single cavity with normal appearing cochleae (e, black arrows).
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Leptomeningeal invasion and dissemation were absent (Figure 2a, b). Brain MRI showed small nodules of subependymal gray matter heterotopia, bilateral hippocampal malrotation, and abnormal cerebellar foliation (Figure 2c, d). Temporal bone computerized tomography revealed bilateral digenesis of the lateral semicircular canals and vestibules forming a single cavity with normal appearing cochleae (Figure 2e).
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