PMC8383822_01
ABR results from subject A, a 9-year-old male with mild symptoms of the disease. Waves I and II were present in both ears and the absolute latencies of Wave I were within normal limits. Questionable wave Vs were present in both ears. Red is right ear; blue is left ear.
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F1
The waveform morphology was poor (Fig. 1).
PMC8383822_02
PMC8383822_03
ABR results from subject C, a 5-year-old male, who had severe developmental delay. Only Wave I was present in both ears with normal absolute latencies. No other repeatable waveforms were present.
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F2
No other repeatable waveforms were present (Fig. 2).
PMC8383822_04
PMC8383822_05
PMC8383822_06
ABR results are from subject F, a 42-year-old male with moderate symptom severity. Waves I, III, and V were present, but all absolute and interpeak latencies were delayed.
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F3
Waves I, III, and V were present, but all absolute and interpeak latencies were delayed (Fig. 3).
PMC8383822_07
PMC8383822_08