PMC4532087_01
Ultrasonographic findings. (A) Right subcostal scanning shows that the left portal vein and it's branches are well visualized but the right portal vein is absent. (B) Right intercostal scan reveals that the gallbladder is shifted anterolaterally to chest wall. Left medial segment contains stones.
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Abdominal ultrasonography (Fig. 1A, 1B) and CT (Fig. 2A, 2B) visualized an enlarged caudate lobe as well as left lobe of the liver.
ERCP shows absence of hepatic duct leading to right lobe. Gallbladder moved upward to form blunt angle between gallbladder long axis and common bile duct. Intrahepatic duct stones are seen also.
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ERCP (Fig. 3) revealed an absence of the right hepatic duct, supralateral displacement of gallbladder forming a blunt angle between the long axis of gallbladder and common bile duct.
99mTc-DISIDA hepatobiliary scintigraphy at 1 hour visualizes superiorly displaced gallbladder, and no excretory abnormality.
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Liver scan using 99mTc-DISIDA (Fig. 4) showed an upward displacement of gallbladder with normal excretory function.
(A) Celiac angiography shows that hepatic artery divided into middle and left hepatic artery, cystic artery arises from left hepatic artery, but artery going to the right lobe is absent. (B) Portovenography shows absence of right portal vein.
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Hepatic artery was divided into the middle and left hepatic artery from which the cystic artery is originating, but the right hepatic artery was not found on celiac angiography (Fig. 5A). Portovenography showed an absence of the right portal vein (Fig. 5B).