PMC7493039_01
Child admitted with left peripheral facial palsy grade V (House Brackmann score).
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Clinical examination showed a grade V left peripheral facial paralysis (House Brackmann score), a hard swelling extending from the mastoid region, the pinna to the parotid region and a bleeding whitish mass in the left ear canal (Fig. 1).
A: Axial CT scan showing bone lysis by a lesional process responsible for mastoid ostelysis with lysis of the petrous apex.. B: Axial CT showing temporal endocranial development with extension to the cerebellopontine angle.
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It had an endocranial temporal development with extension to the left cerebellopontine angle (Fig. 2).
Hematein and eosin stain of the tumor with a high-power view (x40) showing dense cellularity of a monomorphic, ovoid or slightly angular nuclei diffuse tumor proliferation with finely granular chromatin. The cytoplasm is scanty, ill defined. The stroma is thin including slightly tickened wall vessels.
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Pathology and immunohistochemical study were compatible with an embryonal rhabdomyosarcoma (Fig. 3, Fig. 4).