PMC3644792_01
Non contrast computed tomography scan of brain showing bilateral basal ganglia calcification
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F1
Non-contrast computed tomography (CT) of the brain showed extensive intracranial calcification involving the basal ganglia, cerebellum, and cerebral cortex on both the right and left sides [Figure 1].
(a) Pure tone audiogram showing bilateral severe sensorineural deafness, predominantly in higher frequencies. (b) Legend for the audiogram
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F2
Pure tone audiometry (PTA) showed bilateral moderate-to-severe hearing loss that was more severe at the higher end of the frequency spectrum [Figure 2a and b].
Ultrasonography of abdomen showing an empty left renal fossa (indicated by the arrow)
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F3
Ultrasonography showed the absence of renal shadow on the left kidney and an increased cortical echogenicity of 8.4 cm in the right kidney [Figure 3].