PMC9555291_01
Evolution of cardiac hypertrophy and dilation. (A) Chest radiograph showing marked cardiomegaly in the neonatal period. (B) Echocardiogram showing hypertrophic left ventricle in the neonatal period. (C) Echocardiogram showing mixed left ventricular hypertrophy and dilation at 2 months of age. (D) Echocardiogram showing resolution of left ventricular hypertrophy with worsening of dilation at 7 months of age. IVS, interventricular septum; LA, left atrium; LV, left ventricle.
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F1
A repeat echocardiogram showed resolution of left ventricular hypertrophy with continuing dilation (Figure 1D).
PMC9555291_02
Evolution of cardiac hypertrophy and dilation. (A) Chest radiograph showing marked cardiomegaly in the neonatal period. (B) Echocardiogram showing hypertrophic left ventricle in the neonatal period. (C) Echocardiogram showing mixed left ventricular hypertrophy and dilation at 2 months of age. (D) Echocardiogram showing resolution of left ventricular hypertrophy with worsening of dilation at 7 months of age. IVS, interventricular septum; LA, left atrium; LV, left ventricle.
fped-10-944178-g0001.jpg
PMC9555291_02_fped-10-944178-g0001.jpg
F1
A repeat echocardiogram showed resolution of left ventricular hypertrophy with continuing dilation (Figure 1D).
Evolution of cardiac indices in response to treatment. The dashed green line represents initiation of ERT. LV%fs, left ventricular percentual fractional shortening; LVPWd, left ventricular posterior wall dimension; LV mass, left ventricular mass; LV mass/BSA, left ventricular mass/body surface area.
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PMC9555291_02_fped-10-944178-g0002.jpg
F2
Evolution of systolic function and cardiac indices are presented in Figure 2.