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The preoperative orthopantomogram.
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Outpatient Unit of the Department of Maxillofacial Paediatric Surgery, Children's Hospital, ASST degli Spedali Civili, Brescia, Italy. Physical examination revealed only mandibular hypoplasia with multiple deciduous teeth and caries; the patient was noted to be 'fragile' (syndromic child). Orthopantomography revealed mixed dentition with nothing of note in the mandible or maxilla (Fig. 1).
The axial CT view of the mandibular lesion.
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The maxilla also appeared to have expanded, containing similar, solid vascularised tissue, and even the sphenoid appeared to have partially expanded; the ethmoid was partially occupied by hypodense material (Fig. 2, Fig. 3, Fig. 4).
The angio-CT coronal view of the mandibular and maxillary lesions.
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The maxilla also appeared to have expanded, containing similar, solid vascularised tissue, and even the sphenoid appeared to have partially expanded; the ethmoid was partially occupied by hypodense material (Fig. 2, Fig. 3, Fig. 4).
The axial CT view of the small areas of osteolysis in the middle thirds of both iliac wings on the lateral and medial sides.
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A similar 15-cm alteration was found along the rear edge of the intermediate and distal diaphyses of the right femur; on the right side, an isolated phenomenon of identical appearance affected the posterior region of the distal tibia (Fig. 5, Fig. 6, Fig. 7)
The axial CT view of an isolated phenomenon of identical appearance affected the posterior region of the distal tibia.
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Endothelial-vascular spaces without atypia interspersed with fibrous connective tissue stroma.
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No malignant cell or cellular atypia was noted (Fig. 8).