PMC5334604_01
Brain MRI (T1-weighted images) showing a severe atrophy of the cerebellum in the sagittal plane (A). The arrows point to the atrophic vermis, whereas the morphology of the brainstem appears normal (arrowhead). A severe atrophy of the cerebellar cortex is observed in the frontal plane [arrows in panel (B)]. Note that the dentate nuclei are clearly identified on both sides (arrowheads). Striatum, thalamus, subcortical white matter, and cerebral cortex appear morphologically normal on both sides [axial image in panel (C)].
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F1
Brain MRI demonstrated a diffuse cerebellar cortical atrophy sparing cerebellar nuclei (Figure 1).