PMC4921162_01
Coronal (A) and axial (B) CT shows bilateral symmetric, hippocampal, and amygdalae calcifications.
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Calcifications were also seen in the left basal ganglia (Figs. 1A and B).
A) T2-weighted MRI shows hypointense lesions in the mesial temporal lobes bilaterally. B) and C) Gradient echo MRIs show hypointense lesions symmetrically involving the amygdalae, heads of hippocampi, parahippocampal gyri, and left basal ganglia.
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T2-weighted images showed hypointense lesions in the mesial temporal lobes bilaterally (Fig. 2A). The gradient echo images showed hypointense lesions symmetrically in the amygdalae, the heads of the hippocampi, the parahippocampal gyri, and in the left basal ganglia (Figs. 2B, 2C).
Patient photograph shows poxlike scarred lesions in the face.
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A dermatologic opinion revealed poxlike scarred lesions in her face with dry and wrinkled skin (Fig. 3).
Patient photograph shows the maculopapular and beaded lesions of moniliform blepharosis (arrow).
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Maculopapular, beaded lesions were also noted in her lower eyelids:typical of moniliform blepharosis (Fig. 4).
Photomicrograph shows amorphous PAS-positive hyaline material (low power, Periodic Acid Schiff stain).
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Hematoxylin-eosin and Periodic Acid Schiff (PAS) stains revealed amorphous, PAS-positive hyaline material in the walls of the dermal vessels, around the eccrine sweat glands, and along the dermo-epidermal junction; this confirmed the diagnosis of lipoid proteinosis (Fig. 5).