PMC5423708_01
Timeline of events.. EF: ejection fraction; SPAP: systolic pulmonary artery pressure; RHC: right heart catheterization; mPAP: mean pulmonary artery pressure; PCWP: pulmonary capillary wedge pressure; PVR: pulmonary vascular resistance; NYHA: New York Heart Association.
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During the visit, she endorsed New York Heart Association (NYHA) class III symptoms and the decision was made to admit her for expedited workup of her PAH and initiation of targeted PAH therapy (Figure 1).
Echocardiogram with four-chamber view before PAH therapy.
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Her hemolytic anemia quickly resolved and 1 month after starting pulse dose steroids and maintenance immunomodulation, she had dramatic improvement in her clinical symptoms as well as TTE findings (Figures 2-5).
Echocardiogram with four-chamber view after pulse dose steroids.
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Her hemolytic anemia quickly resolved and 1 month after starting pulse dose steroids and maintenance immunomodulation, she had dramatic improvement in her clinical symptoms as well as TTE findings (Figures 2-5).
Echocardiogram showing systolic interventricular flattening of the ventricular septum before PAH therapy.
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Her hemolytic anemia quickly resolved and 1 month after starting pulse dose steroids and maintenance immunomodulation, she had dramatic improvement in her clinical symptoms as well as TTE findings (Figures 2-5).
Echocardiogram showing improvement in systolic interventricular flattening of the ventricular septum after pulse dose steroids.
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Her hemolytic anemia quickly resolved and 1 month after starting pulse dose steroids and maintenance immunomodulation, she had dramatic improvement in her clinical symptoms as well as TTE findings (Figures 2-5).