PMC3225455_01
Photograph of the posterior pole (A) and peripheral region (B) of the right eye of a patient with idiopathic uveal effusion syndrome (IUES) in July 2001. A choroidal detachment can be seen (B). The ultrasonographic image of the right eye shows a retinal detachment in the inferior hemisphere (C). Photograph of the posterior pole (D) and peripheral region (E) of the left eye in September 2006. A ciliochoroidal detachment can be seen (E). Optical coherence tomography shows a macular detachment in the left eye (F).
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The posterior pole of the ocular fundus showed atrophy of the retinal pigment epithelium (RPE; Figure 1A). An annular ciliochoroidal detachment and a shifting bullous retinal detachment were noted in the right eye (Figure 1B and C). Atrophy of the RPE in the posterior pole and annular ciliochoroidal detachments were noted in the left eye (Figure 1D and E). OCT demonstrated subretinal fluid in the macula (Figure 1F).
Fluorescein angiograms (A and B) and indocyanine green angiograms (C and D) in May 2008. The arrow points to the direction and length of the enhanced depth imaging optical coherence tomographic scan (EDI-OCT) (C). The EDI-OCT image shows large low-reflective areas (indicated by asterisks) in the outer choroid in the patient (E) which was not noted in a control subject (F).
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In May 2010, fluorescein angiography (FAG) showed marked hyperfluorescence in the macular region of the left eye due to window defect with late subretinal leakage (Figure 2A and B). ICGA findings. In the late phase of ICGA, hypofluorescence was noted throughout the posterior pole (Figure 2D). EDI-OCT scan. EDI-OCT demonstrated low-reflective areas (indicated by asterisks in Figure 2E) in the outer choroid (Figure 2C and E) in April 2011. The choroidal thickness was 787 mum (indicated by the arrow in Figure 2E) which was significantly thicker than the normal value (272 +- 90 mum, n = 131) obtained from age-matched normal controls (indicated by the arrow in Figure 2F).