PMC6585220_01
Preoperative image showing nasomaxillary mass causing cheilo-nasal dysmorphism
AMS-9-208-g001.jpg
PMC6585220_01_AMS-9-208-g001.jpg
F1
There was considerable elevation of the alar base and obliteration of the right nasal cavity [Figure 1].
(a) Preoperative magnetic resonance imaging showing soft-tissue mass in the nasomaxillary region. (b) Delivery of the excised mass. (c) Closure of the defect
AMS-9-208-g002.jpg
PMC6585220_01_AMS-9-208-g002.jpg
F2
T-high-field magnetic resonance imaging (MRI) revealed a soft-tissue mass in the central aspect of the right maxilla extending into nasal cavity with cranial displacement of the deciduous central incisor [Figure 2a]. The child was subsequently taken up for excision of the nasomaxillary mass under general anesthesia [Figure 2b and c].
Photomicrograph showing cellular spindle cell lesion arranged in fascicles with "herringbone pattern"
AMS-9-208-g003.jpg
PMC6585220_01_AMS-9-208-g003.jpg
F3
Microscopy revealed densely packed spindle cells arranged in fascicles and demonstrating herringbone pattern [Figure 3].
Photomicrograph showing vimentin positivity in neoplastic cells
AMS-9-208-g004.jpg
PMC6585220_01_AMS-9-208-g004.jpg
F4
Immunohistochemical staining reported positivity for vimentin [Figure 4], smooth muscle actin, and CD 34 while being negative for S100, CD99, BCL-2 myogenin, and desmine.
Eighteen months' postoperative follow-up showing complete regain of facial architecture
AMS-9-208-g005.jpg
PMC6585220_01_AMS-9-208-g005.jpg
F5
The patient is being followed up for the last 2 years and has remained disease free so far [Figure 5].