Renal hydatidosis represents only 2-3% of hydatid disease. It is endemic in parts of eastern Europe, middle East, south America, Australia, New Zealand, Alaska, and Canada. Cystic rupture into the collecting system causes hydaturia; isolated renal involvement is even rarer. Here we report a case of left renal hydatid cyst in a 40 year old man presenting as hematuria and macroscopic hydaturia since last ten years. The patient underwent exploratory laparotomy and recovered.