Background:
High-frequency pallidal stimulation has been shown to improve various types of dystonia, including myoclonus-dystonia.
Case report:
We report a case of epsilon sarcoglycan mutation-negative myoclonus-dystonia with response to low-frequency bilateral pallidal stimulation.
Discussion:
Low-frequency pallidal stimulation provides an effective means of treating various dystonias, regardless of genetic status, as in our case, as it provides increased programming options with fewer adverse effects.