Spinal sarcoidosis represents a rare subgroup of neurosarcoidosis. Most spinal sarcoid lesions are intramedullary, and only a few cases of Intradural Extramedullary (IDEM) sarcoidosis have been reported till date.A thirty years-old female patient with intradural extramedullary sarcoid lesion in the cervico-dorsal spinal canal (C7-D1) without any systemic involvement of sarcoidosis is described. The patient presented with rapidly progressive compressive myelopathy with bladder involvement. She was treated with surgical removal of the lesion coupled with the administration of steroid and showed marked improvement.