Objective:
To report a hypertensive and systematically pigmented female with primitive neuroectodermal tumors.
Clinical presentation and intervention:
A female patient presented with a complaint of right flank pain. She had a right renal space-occupying lesion, underwent right radical nephrectomy, and returned to normotensive postoperatively. The pathological examination identified typical primitive neuroectodermal tumor histology. During a 60-month follow-up period, she remained normotensive and demonstrated normal renal and adrenal functions.
Conclusion:
Early diagnosis and definitive surgery led to the patient's long-term survival.