We report a rare case of inferior vena cava (IVC) aneurysm in a 22-year old Afghan-Iranian male patient. CT scan illustrated a saccular aneurysm of IVC originating from right side of the IVC below the renal veins (a saccular type 3 IVC aneurysm). We planned open resection and repair of the aneurysm. The patient had well recovery after the operation and his follow-up did not reveal any morbidity. IVC aneurysm is a rare clinical entity. Its diagnosis necessitates precise clinic suspicion and the management is based on anatomical location and associated anomalies.