Parachordoma is an extremely rare entity and there are only about 50 to 60 cases reported, in which there is only one definite pelvic parachordoma. We present a huge well-defined presacral tumor in a 48-year-old woman who has the symptoms of lower abdominal pain and difficulty in defecating. Radiological findings of the tumor on computed tomography and magnetic resonance imaging are described in detail. The reasons why we report the case are because the patient has rare clinical symptoms and because this is the second pelvic parachordoma. Then, we summarize the radiological features of parachordoma based on our study and the review of literature.