Nodular lymphoid hyperplasia (NLH) is a pathology of the gastrointestinal tract that is commonly found in children. Most of its etiology is benign and associated with some underlying causes such as food hypersensitivity, viral or bacterial infection, giardiasis, Helicobacter pylori (H. pylori) infection, immunodeficiency, celiac disease, and inflammatory bowel disease. It is characterized by the growth of submucosal lymphoid tissue and a mucosal response to different types of noxious stimuli. In this report, we present the case of a child with recurrent hematemesis.