Purpose:
To describe the clinical, pathological, and immunohistochemical characteristics and therapies of a rare case of primary synovial sarcoma in the orbit.
Design:
Retrospective interventional case report.
Participant:
A 6-year-old girl with pathologically proven synovial sarcoma in the orbit. The diagnosis was confirmed by immunohistochemistry.
Methods:
The patient was treated with right lateral orbital and right temporal tumor resection, followed by chemotherapy. She was followed up every 3 months for 1 year.
Results:
The tumor was excised, and the patient received 5 courses of chemotherapy. She did well during the initial first-year follow-up with no recurrent signs.
Conclusions:
We reported the sixth case of primary synovial sarcoma in the orbit and the first case of a 6-year-old girl.