Fusion is a developmental anomaly which occurs due to a union of one or more adjacent teeth during morpho-differentiation of the dental germs. Early diagnosis of this condition is important because it may cause clinical problems, such as esthetic concerns and arch asymmetry. These anomalies may be unilateral or bilateral and may affect either dentition, although the deciduous teeth are more commonly affected. This report describes a rare case of unilateral fusion between the mandibular permanent lateral incisors and the canine. Only few cases have been previously reported in the English literature. Hence this article aimed at reporting a case of this rare condition and evaluating the presence of any associated pathology.