Pulmonary torsion is a severe, life-threatening event, rarely occurring in children. We present a case of atypical postoperative complication of esophageal atresia repair in the form of pulmonary torsion comprising the middle lobe of the right lung. Clinical deterioration in the face of normal arterial blood gases should rise a high index of suspicion for pulmonary torsion. Early diagnosis is crucial, treatment is surgical, detorsion if possible, or if the lobe is not viable-resection.