Multicystic dysplastic kidney (MCDK) is a congenital anomaly as the result of abnormal interaction between the ureteric bud and metanephric mesenchyme. Unilateral MCDK can be associated with other anomalies of the genitourinary tract. Relatively rare associated anomaly is the presence of ipsilateral refluxing blind megaureter. The patient reported herein is a 23-years-old woman with involuted MCDK and ipsilateral blind megaureter causing chronic urinary infection and chronic abdominal pain. Preoperative and intraoperative examination failed to detect the communication between megaureter and the urinary bladder.