Osteoid osteoma is one of the osteoblastic benign bone tumors, which occurs frequently at the cortex of long bones, usually in the diaphysis or metadiaphysis. Although the tumor location in the bone varies, epiphyseal intramedullary osteoid osteoma has been rarely reported. Herein, we report a 14-year-old male patient with epiphyseal intramedullary osteoid osteoma, occurring at the distal radius, with magnetic resonance imaging findings.