Background:
Anti-GAD-related cerebellar ataxia has rarely been described as an acute cause of autoimmune ataxia.
Phenomenology shown:
A young female who acutely developed anti-GAD-associated ataxia with magnetic resonance imaging (MRI) showing cerebellar edema and follow-up MRI 6 months later showing cerebellar atrophy.
Educational value:
Recognizing that anti-GAD-associated cerebellar ataxia can present in a young adult as an acute and severe cause of ataxia, with cerebellar changes evident on MRI.