A 69-year-old male patient presented with painless protrusion of his left eye for 6 months. A large, anterior orbital vascular mass was seen in the superior conjunctival fornix. Neuroimaging and Doppler studies revealed a highly vascular circumscribed, enhancing mass lesion in the superior orbit. Carotid angiogram showed a feeder vessel which was embolized followed by complete excision of the lesion. Further investigations confirmed primary extra-marginal zone B-cell non-Hodgkin's lymphoma of the orbit. To our knowledge, this is the first case report of a primary orbital lymphoma treated by Transcatheter arterial embolization and excision.