Miller Fischer syndrome is a rare entity characterized by the triad of external ophthalmoplegia, ataxia, and areflexia. It is thought to be a form of Guillain-Barre syndrome. Presently described is the case of a 68-year-old woman who presented with bilateral, external ophthalmoplegia, areflexia, and ataxia. After excluding other conditions, a diagnosis of Miller Fisher syndrome was made. She was treated with intravenous immunoglobulin and completely recovered in 8 weeks.