▁certain ▁aspects ▁of ▁their ▁intelligence ▁are ▁above ▁the ▁average . ▁Despite ▁their ▁dis ability , ▁S MA - aff ected ▁people ▁report ▁high ▁degree ▁of ▁satisfaction ▁from ▁life . ▁ ▁Pal li ative ▁care ▁in ▁S MA ▁has ▁been ▁standard ised ▁in ▁the ▁Cons ensus ▁Stat ement ▁for ▁Standard ▁of ▁Care ▁in ▁Sp inal ▁Mus cular ▁At ro phy ▁which ▁has ▁been ▁recommended ▁for ▁standard ▁ad option ▁world wide . ▁ ▁Pro gn osis ▁In ▁lack ▁of ▁ph arm ac ological ▁treatment , ▁people ▁with ▁S MA ▁tend ▁to ▁d eter ior ate ▁over ▁time . ▁Rec ently , ▁surv ival ▁has ▁increased ▁in ▁severe ▁S MA ▁patients ▁with ▁ag gress ive ▁and ▁pro active ▁support ive ▁resp ir atory ▁and ▁nut r itional ▁support . ▁ ▁If ▁left ▁un tre ated , ▁the ▁majority ▁of ▁children ▁diagn osed ▁with ▁S MA ▁type ▁ 0 ▁and ▁I ▁do ▁not ▁reach ▁the ▁age ▁of ▁ 4 , ▁rec urrent ▁resp ir atory ▁problems ▁being ▁the ▁primary ▁cause ▁of ▁death . ▁With ▁proper ▁care , ▁mil der ▁S MA ▁type ▁I ▁cases ▁( which ▁account ▁for ▁appro x . ▁ 1 0 % ▁of ▁all ▁S MA 1 ▁cases ) ▁live ▁into ▁ad ul th ood . ▁Long - term ▁surv ival ▁in ▁S MA ▁type ▁I ▁is ▁not ▁sufficiently ▁ev iden ced ; ▁however , ▁recent ▁adv ances ▁in ▁resp ir atory ▁support ▁seem ▁to ▁have ▁brought ▁down ▁mort ality . ▁ ▁In ▁un tre ated ▁S MA ▁type ▁II , ▁the ▁course ▁of