elephantiasis is one of the oldest , bizarre and most crippling disorder that has a long history and worldwide distribution . genital elephantiasis is caused by a variety of infective and non infective causes leading to blockage of lymphatics . esthioneme is a greek terminology used to describe elephantiasis which means to eat and carries an idea something gnawed , eroded or ulcerated ( 1 ) . wuchereria bancroftii , which accounts for 90% of filarial infections and is estimated to infect 120 million people in the tropics ( 2 ) . out of infected people1:3 live in india ( 3 ) and 1 billion of people are at the risk of infection ( 4 ) . the order of involvement of lymphatic filariasis is lower limb , trunk , breast , upper limb and genitelia . in india bihar has highest endemicity ( around 17% ) , kerala ( around 15.7% ) and utter predesh ( around 14.6% ) ( 2 ) . we are presenting a rare case of unilateral vulval elephantiasis which has recurred after initial reconstructive surgery . a 38 year old female patient presented with swelling in vulval region since 2 years . patient complains of increase in the size of the swelling from past 2 years and swelling has reached to present size . the swelling was small in size of around 6 * 7 cm in 2002 and the swelling was excised and diagnosis of vulval elephantiasis was made and pelvic reconstructive surgery was done . reports of which are not available but according to patients history her external genital were of normal size fallowing surgery . on examination patient was afebrile and no lymphadenopathy and her gait was unusually wide and large , hypertrophied , pendulous , multilobed mass of hypertrophied tissue hanging down and obstructing the vulval cleft was seen on left side ( fig . unilateral vulval elephantiasis fnac ( fine needle aspiration cytology ) done outside 2 months before showed hypocellular smear with lymphocytes on a proteinecious background . biopsy showed lesion composing of interlacing band of fibroblasts and collagen and perivascular collection of lymphocytes and mononuclear cells were present ( fig . the stroma showed myxoid changes and foreign body granulomas were present and features suggestive of superficial chronic inflammation . biopsy report showing lymphatic infiltration and proliferation of fibrous tissue patient was started with antibiotics and daily dressing was done till the infection was subsided and the patient was planned for reconstructive surgery ( excise the swelling and reconstruction of external genital ) but the patient refused surgery due to personal reason . lymphatic filariasis external genitelia are very rare and it has been reported as sporadic case reports even though it was first described in 1673 ( 5 ) . largest study on these cases was from india in 1980 where they have described 25 case reports ( 4 ) . elephantiasis of vulva roughly affects not more than 1 - 2% of total case of filarial elephantiasis ( 6 ) . causes include filariasis , lymphogranuloma venerum , donovanosis and tuberculosis , it can also occur fallowing radical hysterectomy , pelvic lymphadenectomy and radiation . the main differential diagnosis include fibro epithelial polyp , fungal infection , granuloma inguinale , carcinoma and irradiation ( 7 ) . aim of the management is to reduce the swelling , restore the normal shape and sexual function and to prevent inflammatory episodes . diethylcarbamazine ( dec ) in three divided doses of 6 mg / kg / day for 12 days kills adults and microfilaria . good skin care and prompt treatment of the bacterial infections is very important in management . surgical management includes excision of skin and subcutaneous tissue of involved part and closing the defect with adjacent normal skin . if the defect is very large split thickness skin graft or bilateral super medial thigh flaps can be used . excision therapy for vulval elephantiasis is quiet satisfactory ( 8) . this case is presented because of its rarity and it recurrence after initial reconstructive surgery . neither the micro filarial is seen in peripheral smear nor the filarial worm demonstrated in the tissue section .
genital elephantiasis is caused by a variety of infective and non infective causes leading to blockage of lymphatic . 
 we are presenting a rare case of recurrent unilateral vulval elephantiasis which has recurred after initial reconstructive surgery . a 38 year old female presented with vulval swelling and on examination 
 there was gross unilateral vulval enlargement . 
 fnac ( fine needle aspiration cytology ) and biopsy were contributory for diagnosis . 
 patient was started with antibiotics and daily dressing was done till the infection was subsided and the patient was planned for reconstructive surgery .