
hypertallorism

hypertallorism mhanje done avayavanmadhil kinwa sharirik bhaganmadhil asamanyaritya vadhalele antar, jeey sahasa kakshanmadhil (dolhe) kinwa kakshiy hypertailorismadhil vadhiv antar darshavate. yaa sthiteet dolhyachya aateel kopyanmadhil antar tasech putalyanmadhil antar samanyapeksha jaast asate. hypertalorismcha aanee telecanthuscha gondhal houu naye, jyamadhye dolhyachya aateel kopyanmadhil antar vadhate parantu dolhyachya bahereel kopya aanee bahereel bahulyanmadhil antar badalat rahate.
edward syndrome (trisomy 18), 1q21.1 duplication syndrome, besal seela naves syndrome, digeorge syndrome aanee loyas-dietz syndrome yasah vividh syndromedhye hypertallorism heey eka lakshan aahe.
hypertallorism heey eppert syndrome, autism spectrum disorder, chraniophrontonasal dysplasia, dunan syndrome, neurofibromatosis, lapered syndrome, crousion syndrome, wolf-hirshorn syndrome, anderson-tovill syndrome, wardenberg syndrome aanee cree duu chatt syndromedhye dekhil disun yete, tasech piebaldism, pramukh aateel trutiyansh bhuvaya, vegvegalya rangache iris, spondyloephisal dysplasia, mucopolysaccharide chayapachay vikar (morkeo syndrome aanee hurler syndrome), bahirepana aanee hypothyroidism disun yete. hypertallorism aanee attension deficit hyperactivity disorder yanchyat kahee sambandh aadhalale aahet.
bhrunshastra.
hypertallorism hii janmajat vikaranchya vijatiy gatashi sambandhit eka sharirik sthitee asalyane, asey manale jaate qee hypertalorismchi antarnihit yantrana dekhil vijatiy aahe. siddhantanmadhye sphenoidchya khalchya pankhanche khoop lavkar ausification, ethmoid sinuschya vadhatya rundimule aurbita darmyanchi vadhaleli jaaga, vikasadarmyan kshetra dosh, anunasik capsule tayar karnyat ayashasvi hone, samanya madhya kakshiy sthalantarat apayash yene aanee kapal besachya nirmitimadhye adthala aanane yancha samavesh hoto, jeey eppert aanee crazone sarkhya syndromedhye disu shakate.
upchar.
hypertallorism durust karnyasathi chraniophacial shastrakriya sahasa paach teey aath varshanchya darmyan kelee jaate. hii saundarya-kendrit prakriya mulachya shaley suruvatichya varshatil manosamajik pailoonvar laksh kendrit karate. paach varshe kinwa tyahoon adhik vayachya durustiche aanakhi eka kaaran mhanje datanchya kalya maxilamadhye puresha pramanat qamee hoiparyant shastrakriyes vilamb jhaala pahije, jyamule tyanche nuksan rokhata yete. tasech, vayachya pachvya varshapurvich kapalavaril hadey patal aanee najuk asatat, jyamule shastrakriya sudharane katheen houu shakate. yavyatirikt, balpanat kakshiy shastrakriya madhyabhagachya vadhis pratibandh karoo shakate.
hypertalorism upcharansathi done mukhya operative paryay aaheth boxes austiyotami aanee chehnyavaril dvidaleey vibhajan (jyala madhyasth faciotomy asehi mhanatat).
boxes austiyotami.
aurbital hypertalorismcha haah upchar pratham paul tacierne keela hota. kavaticha sampoorn hadancha bhag kavatipasoon aanee chehnyachya sabhovatalachya hadanpasoon vegala karananya vividh asthisandhivatanni shastrakriya suru hote. austiyotomipaiki eka mhanje kakshanmadhil haad kadhoon takane. tyanantar kakshanna ekatra kele jaate aanee ekmekankade aanale jaate. kaaran yamule anekada kakshanmadhye jastichi tvacha tayar hote aanee tvacheche madhyareshetil chhedan varanvar aavashyak asate. heey bhuvaya aanee dolhyanchya kopyanchaa andaj lavte aanee adhik anandadayi swaroop pradan karate.
chehnyavaril dvidaleey vibhajan.
manak prakriya (boxes austiyotomi) jacks vanne dair myulendware sudharit kelee gelee aanee parinami chehnyachya dvidal vibhajanacha (kinwa madhyam faciotomy) vikas jhaala.
chehnyachya dvidaleey vibhajanat pratham agrabhagache haad suprorbital rimpasoon vibhajit karane samavisht asate. mug monoblock austiyotomicha vapar karoon kavatichya talapasoon kaksha aanee madhyabhag sodale jaatat. mug hadancha trikoni aakaracha tukada madhyabhagachya madhyareshetun kadhala jaato. yaa trikoni bhagacha paya kakshechya varr aahe aanee shikhar varchya chhedan datanchya darmyan aahe. haah bhag kadhoon taklyanantar madhyabhagache done bhag ekmekankade firavane shakya aahe, parinami kakshanmadhil antar qamee hote. yacha parinam vhee-aakarachya maxilachi patali vadhavanyat aanee tyamule tee rund honyat dekhil hoto.
hypertallorism haah anekada epertsarkhya lakshananshi sambandhit asalyane, hypertallorism haah anekada midface displasiachya sanyogane disun yeto. jarr asey asel tarr chehnyavaril dvidaleey vibhajan heey vichalit karananya austiogenesishi jodale jaau shakate. madhyabhagachya vichalit karananya austiogenesischa uddesh mhanje kakshiy kathapasoon dolhyaparyantche sambandh samanya karane aanee zygoma, naak aanee maxilachi sthitee dekhil samanya karane.
mauu uutinchi punarrachana.
kakshiy hypertalorism sudharananmadhye sweekarya saundarya parinam tayar karnyasathi, mauu-uutinchi punarrachana vicharat ghene dekhil mahatvache aahe. yaa sandarbhat, anunasik vikrutee sudharane hii adhik katheen prakriyanpaiki eka aahe. nakachi chaukat tayar karnyasathi aanee udaharanarth kapalavarchya flaps sthanik firanyasathi haad aanee upasthi kalam aavashyak asoo shakatat kinwa naak jhakanyasathi pragat flapscha vapar keela jaau shakato.
shastrakriyemule honari guntagunt.
jawaljawal pratyek prakarchya shastrakriyepramanech, hypertalorism donhi upcharanmadhil mukhya guntaguntinmadhye jaast raktastrav, sansargacha dhoka aanee see. ess. eff. galatee aanee dural fistula yancha samavesh hoto. perioperative pratijaivike deuun aanee konatehi ashru olakhoon aanee bund karoon sansarg aanee galatee rokhali jaau shakate. lakshaniy raktastravacha dhoka kaljipurvak kelelya tantradvare rokhala jaau shakato aanee raktastravanchi bharpai rakt sankramanadvare kelee jaate. hypotensive anaesthesia deunahi raktastrav qamee keela jaau shakato. andhatvasah dolhyanchya mothya jakhama kvachitach disatat. kakshiy halchalinnantar dolhyanchya snayunchya asantulanamule drushtitil vyatyay yeu shakatat. tossis aanee diplopia heey shastrakriyenantar dekhil houu shakatat, parantu heey sahasa swatah sudharate. shastrakriyenantar durust karane hii eka atishay katheen samasya aahe canthal drift, jee canthal kandara jodanya shakya titkya kaljipurvak jatan karoon sarvottam prakare vyavasthapit kelee jaau shakate. yaa prakriyanmadhye vistar asoonahi, hypertalorism operative sudharananmadhye mrutyu kvachitach disun yeto.