
janmana undaakunna disarithropoitic anaemiya tharam IV

konjenittal diserithropoitic anaemiya type IV (cda IV) cda II-nte saadhaarana roopaghadana savisheshathakalode vivarichittundu, pakshe oru negatteevu acidified-serem parisodhanayaanu.
avatharanam.
cda type IV-nte savisheshatha neriyathum mithavumaaya pleehayaanu. haemoglobin valare kuravaanu, rogikal rakthappakarchaye aasrayikkunnu. emm. sii. vii saadhaaranamo neriyatho aaya uyarnnathaan. erythropoisis normoblastic allengil mithamaayatho mithamaayatho aaya megaloblastic aanu. nonspeciphic erythroblast dysplasia undu.
janithakashasthram.
janithaka disarithropoitic anaemiya type IV ennathu vandhyathaykk kaaranamakunna phalapradamallaatha erythropoisis, haemolysis ennivayaal savisheshamaaya oru autosomal aadhipathya paarambarya chuvanna rakthaanukkalude thakaraaraan. asthimajjayil rakthachamkramanamulla erythroblaastukalum erythroblaastukalum vividha roopaghadanayile asaadhaaranathakal kaanikkunnu. sidan 4 baadhicha vyakthikalkkum garbhapindatthile haemoglobinte alavu vardhichittundu.
chikitsa.
pathivayi rakthappakarchayum cheleshan therapy ulppedunnathaanu chikitsa. asthi majja maattivaykkal, jeane therapy enniva saadhyamaaya rogashaanthikalil ulppedunnu.