
moothrasanchiyude extrophy

extrophy-epispadias complexinte spectrathil nilanilkkunna oru janmasidhamaaya apaakathayaan bladder extrophy, athil ettavum pradhanamaayi vayarile mathilile oru thakaraariloode moothrasanchiyude puramthallal ulppedunnu. asthi pelvis, pelvik floor, jananendriyangalude asaadhaaranathakal ulppede palappozhum athinte avatharanam vyathyaasappettirikkunnu. moothraashaya extrophyilekku nayikkunna antharleenamaaya bhroonaghadana anjjaathamaanu, ennirunnaalum ithu bhaagikamaayi mesoderm vazhi clocal membron shakthippeduthunnathil paraajayappettathaan kaaranamenn karuthappedunnu.
extrophy ennaal pollayaya oru avayavathinte vipareethamaanu.
adayaalangalum lakshanangalum.
moothrasanchiyude extrophy classic aavirbhavam avatharippikkunnath
sthreekalkku palappozhum sthaanabhramsham sambhavichathum idungiyathumaaya yoniyude dwaaram, befeed klittoris, divergent labia enniva undaakunnu.
kaaranam.
kaaranam ithuvare vaidyashaasthraparamaayi sthaapichittillenkilum adisthaana mesoderm vazhi clocal membron shakthippeduthunnathil paraajayappettathaan bhaagikamaayi kaaranamenn karuthappedunnu.
roganirnayam.
25 garbhadhaaranangalekkurichula oru cheria munkaala padanatthil moothrasanchiyude extrophy prasavapoorva roganirnayavumaayi anchu gadakangal shakthamayi bandhappettirikkunnave kandethithi
bhooribhaagam garbhangalilum moothrasanchiyude extrophy roganirnayam munkaala praabalyathode nadathiyappol, moonnu kesukalil maathramaan prasavapoorva roganirnayam nadathiyathu.
maanejment.
rogathinte angeyattam apoorvatha eee rogikalil aavashyamaaya sankeernamaaya closher pariseelikkaanulla sasthrakriya avasarangale parimithappedutthunnu. ekkaaranathaal, sasthrakriya, nazhsing teamukalkk rogam paricharikkunnathil vipulamaaya parichayamulla uyarnna vooliyam kendrangalil moothrasanchikal adaykkumbol rogikalkku mikacha phalangal labikkum. americayileyum lokathileyum ettavum uyarnna vooliyam sentar merilaandile baltimorile johns hopkins aashupathriyaanu; kazhinja 50 varshathinide 1300 ladhikam extrophy rogikale avar kandittundu.
prasavikkumbol, thuranna moothrasanchiyil jalasechanam nadathukayum baahya paristhithiyumaayi kazhiyunnathra sanbarkkam thadayunnathinaayi oru noonn-adleyant philim sthaapikkukayum cheiyunnu. uchithamaaya extrophy support teaminoppam oru medical sentaril kutty janichillengil transfer undakaan saadhyathayund. kaimaattam cheyyappedumbozho allengil moothrasanchiyude extrophy paripalikkaan kazhiyunna oru medical sentaril janicha sisukkalkku, shasthrakriyaykk vidheyamaakunna kuttikk munbulla jeevithathinte aadya kurachu manikkoorukalil imaging nadannekkaam.
sariyaaya valippam, ilaasthikatha, churukkam ennivayulla moothraashayamulla rogikalil maathrame praadhamika (udanadi) adachupoottal soochippikkukayulloo, kaaranam aaa rogikalkku aadyakaala shasthrakriyaykk sesham mathiyaya sheshiyulla moothraashayamundaakaan saadhyathayund.
moothrasanchiyude paryapthatha undaayirunnittum samboornna virudhachihnangalaaya avasthakalil lingathinteyo vrishanathinteyo erattivayppum ganyamaaya ubhaykakshi hydronephrosis ulppedunnu.
sasthrakriya.
aadhunika therapy moothrasanchiyudeyum jananendriyathinteyum sasthrakriya punarnirmmaanamaan lakshyamidunnathu. eee vairudhyavumaayittaanu sthreekalum purushanmaarum janikkunnath. chikitsa samaanamaan.
purushanmaarude chikilsayil ivayaanu
extrophy (msre) aadhunika ghattathilulla attakuttappaniyil prarambha ghattam vayarile mathil adaykkuka ennathaanu, palappozhum pelvik austiyottami aavasyamaanu. ithu rogiye linga epispadias moothrathinte aniyanthrithathayum undaakkunnu. ekadesham 2-3 vayass praayamaakumbol, testostiron uthejanathinu sesham rogi epispaadiyakalude attakuttappanikalkk vidheyanaakunnu. avasaanamaayi, moothraashayathinte kazhuthu nannaakkal saadhaaranayaayi 4-5 vayass praayatthil sambhavikkunnu, ennirunnaalum ithu mathiyaya sheshiyulla moothraashayathe aasrayichirikkunnu, ettavum pradhanamaayi, kuttikk bhookhandamaakaan thaalpparyamundennathinte soochanayaanu. moothrasanchiyude chila punarnirmmanangalil, punarnirmmicha moothrasanchiyude vooliyam sheshi vardhippikkunnathinaayi valia kudalile oru bhagam cherthu moothrasanchiyude vardhanavu varuthunnu.
extrophy (sii. pii. aarr. iii) poornnamaaya praadhamika attakuttappaniyil, chelavukalum rogaavasthayum kuraykkunnathinulla shramathil moothrasanchiyude adaykkal oru epispadius attakuttappaniyumaayi samyojippikkunnu. ennirunnaalum, eee saankethikavidya, prathyekichu cheruppakkaaraaya rogikalil, lingathinteyum shaareerika koshangaludeyum ganyamaaya nashtatthilekku nayichu.
sthree chikilsayil inipparayunnava ulppedunnu
rund vyathyastha sareerangalaayi verthirikkappettirikku klittorisinte sasthrakriya punarnirmmaanam. moothraashayathinte pilarpp sariyaakkunnathinulla sasthrakriya punarnirmmaanam, moothraashayathinte kazhuthinteyum moothranaaliyudeyum ghadana punarnirvachikkuka. vaginoplasty munvashath sthaanabhramsham sambhavicha yoniye sariyaakkum. gudadvaaram ulppettittundengil athu nannaakkukayum cheiyunnu. prathyulppaadanasheshi nilanilkkukayum moothrasanchiyude extrophyumaayi janicha sthreekalkku saadhaaranayaayi pelvik florinte durbalamaaya peshikal kaaranam prolapse undaakukayum cheiyunnu.
pravachanam.
deerghakaala roganirnayam mechappeduthunnathinulla ettavum pradhanappetta maanadandam prarambha adachupoottalinte vijayamaan. oru rogikk onniladhikam adavukal aavashyamaanenkil oro adhika adavilum bhookhandangalude saadhyatha pettennu kurayunnu-rund adavukalil bhookhandangal illaathaakaanulla saadhyatha verum 17 sathamaanam maathramaan.
vijayakaramaya shasthrakriyayiloode polum aalukalkk deerghakaala sankeernathakal undakam. ettavum saadhaaranamaaya chilath ivayaanu
epidemiology.
10, 000-ll 1 muthal 50,000-ll 1 vare enna nirakkil sambhavikkunna, purushan sthriyum thammilulla anupatham 2.3-6:1 aanenkil, moothrasanchiyile extrophy thaarathamyena apoorvamaanu. moothrasanchiyude extrophy ulla vyakthikalkk, avarude kuttikalil, avarude prathyulppaadana sheshi nilanirthunnuvenkil, moothrasanchiyude extrophy undakanulla saadhyatha saadhaarana janasamkhyayekkaal ekadesham 500 madangu kooduthalaanu.

