
harris platelet syndrome

paarambaryamaayi labhikkuna ettavum saadhaaranamaaya bheeman platelet disorderaanu harris platelet syndrome (echps).
avatharanam.
indian upabhookhandathinte vadakkukizhakkan bhaagathe aarogyamulla rakthadaathaakkalil rakthasraavam illaatha lakshanagal, bheeman platelettukalulla (sharashari platelet vooliyam 10 efl) mithamayathum kadinavumaaya thrombocytopenia (platelettukal apoorvvamaayi 50 × 109/lii), mye 9 mutation illaatha saadhaarana platelet aggregation padanangal ennivayil echu. pii. ezz. thiricharinju.
echu. pii. ezz. rachayithaakkalulla rakthadaathaakkalil sthithivivarakkanakusaricha uyarnna emm. pii. vii, aarr. dii. dablyu, kuranja platelet kaundu, platelet biomass enniva kandethi.
roganirnayam.
nilavil rogiyude vamseeyatha nirnnayikkukayum athupole thanne thrombocytopeniac kaaranamakunna avasthakal vilayiruthukayum, paarambaryamaayi labhicha bheeman platelet desorders (aii. jii. pii. dii) mattu janmana undaakunna thrombocytopeniakalum ozhivaakkukayum cheythaanu echu. pii. ezz roganirnayam nadathunnathu. nirbhagyavashaal aii. jii. pii. dii ulla chila rogikale corticosteroidukal, immunoglobulin infusionukal, splenectomy enniva upayogichu anuchithamayi chikilsikkunnu.
vyaapanam.
indian upabhookhandathile chila bhaagangalile janasamkhyayude moonnilonnu baadikkunnathinaal harris platelet syndrome thirichariyunnathu valare pradhaanamaan.
padavali.
2002ll eee syndrome "lakshanarahithamaya constitutional macro thrombocytopenia" (acmt) ennu vilikkapettu.
2005-ll, acmt janmana amegacariocytic thrombocytopeny (camt) thammilulla ashayakkuzhappam ozhivakkaan eee kyaamt entittiye harris platelet syndrome ennu vilichirunnu.