yuu. kyu. see. see. 2

ubquinol-cytochrome see reductage complexes assembly factor 2 ack protein haye jise manushyon mein mein jeane dwara encode kiya jaataa haye. mitochondrial nucleod mein sthit, yeh protein ack jatil III assembly kaarak haye, joe protein protein key saath cytochrome bee biogenesis mein bhoomika nibhaata haye. yeh insulin sraav aur mitochondrial aeye. tii. pee. utpaadan aur oxygen kii khapat koo niyantrit kartaa haye. ekmatra darj mamle mein, mein jeane mein ack utparivartan jatil III kii kamee kaa kaaran banaa, jisaki visheshta antargarbhashayi vikas mandata, navjat lactic acidosis aur gurde kii tubeler shithilata haye.
sanrachana.
संरचना। jeane gunasutra 6 kii pee bhuja parr 21.31 sthiti mein sthit haye aur 14,990 aadhar jode mein faila huaa haye. jeane 126 amino acid seey banaa 14.9 kilo dee. aeye. protein paida kartaa haye. iss protein kaa anya gyaat proteins key saath koee samroop kshetra naheen haye. yeh mitochondrial nucleod seey judaa huaa haye, joe sambhavatah paridhiya kshetra mein sthit haye. iss protein kaa vitaran pattern mitochondrial nucleod key anya ghatakon key samaan haye, jaise aim. tii. aiss. bee. aur pee. aich. bee. 1/pee. aich. bee. 2.
kaary.
yeh jeane ack nuclead protein koo kootbaddh kartaa haye joe mitochondrial aantarik jhilli mein sthaaniyakrit hotaa haye aur mitochondrial matricks mein upa-sthaaniyakrit hotaa haye. encoded protein anumeya roop seey agnyashay kii beeta koshikaon mein insulin sraav koo niyantrit kartaa haye, sakaratmak roop seey mitochondrial aeye. tii. pee. utpaadan aur oxygen kii khapat koo niyantrit kartaa haye, aur mitochondrial shwasan shrinkhala gatividhi key modulan key madhyam seey kankal kii maanspeshiyon key vibhedan mein shamil hotaa haye. yeh protein complexes III key sanyojan key liye aavashyak haye. iss protein kii abhivyakti cumm aim. tii. dee. aine. aeye. vaali koshikaon mein cumm hoe jaati haye.
naidaanik mahatva.
ekmatra darj mamle mein, mein jeane key intron 2 mein ack samroopata utparivartan ack vibhajan vyavadhaan kaa kaaran banaa; rogi koo paramanu prakaar 7 jatil III kii kamee key lakshnon key saath prastut kiya gayaa, jisamen navjat lactic acidosis, renal tubulopathy aur gambhir antargarbhashayi vikas mandata shamil hain. atirikt naidaanik visheshtaon mein chehare kii vikriti, vilambit manoprerak vikas, swaleenta kii visheshataaen, aakramak vyavhaar aur halki samvedi shravan haani shamil hain. isake alawa, rogi mein yuu. kyu. see. see. 1 kaa star cumm hoe gayaa thaa.
antahkriyaaen.
yeh protein protein key saath antahkriya kartaa haye.

