
aine. dee. aff. aeye. 4

aine. dee. aff. aeye. 4, mitochondrial complexes seey judaa ack protein haye joe manushyon mein aine. dee. aff. aeye. 4 jeane dwara kootbaddh kiya jaataa haye. aine. dee. aff. aeye. 4 protein koo pahali baar naadh dehydrogenase (ubquinone) kaa ack upghatak bataaya gayaa thaa, joe mitochondrial aantarik jhilli mein sthit haye aur electron parivahan shrinkhala key paanch parisaron mein seey sabse badaa haye. haalaanki, haal key shodh ney endufa4 koo cytochrome "see" oxidase key upa-ikai key roop mein varnit kiya haye. endufa4 jeane mein utparivartan lii syndrome seey judey hotey hain.
sanrachana.
endufa4 jeane gunasutra 7 kii pee bhuja parr 21.3 kii sthiti mein 8,234 aadhar jode kii kull lambai key saath sthit haye. aine. dee. yuu. aff. aeye. 4 jeane 81 emino acid seey banaa 9.4 key. dee. aeye. protein paida kartaa haye.
aine. dee. yuu. aff. aeye. 4 koo paaramparik roop seey enzyme naadh dehydrogenase (ubquinone) (complexes i) key upa-ikai key roop mein paribhaashit kiya gayaa haye, joe shwasan parisaron mein sabse badaa haye. 
haal key shodh seey pataa chalaa haye kii aine. dee. yuu. aff. aeye. 4 hataane parr jatil aaee kaa koee gadbadi naheen hoti haye, jisase iss parisar mein isaki bhoomika parr sawal uthate hain. yeh pradarshit kiya gayaa haye kii endufa4 jatil IV kaary aur javic utpatti mein ack bhoomika nibhaata haye, halanki, kuchh lekhakon kaa sujhaav haye kii endufa4 jeane kaa naam badal diyaa jaae aur jatil i aur jatil IV donon kii sanrachana kaa punarmulyankan kiya jaae.
naidaanik mahatva.
endufa4 jeane mein utparivartan key parinamswarup lii syndrome hoe sakata haye, ack gambhir tantrika sambandhi vikaar joe aamtaur parr jeevan key pahale varsh mein utpann hotaa haye. jatil IV kaa vyavadhaan, jise cytochrome see oxidase yaa cox bhee kahaa jaataa haye, leh syndrome kaa sabse aam kaaran haye. yeh dekhate hue kii aine. dee. yuu. aff. aeye. 4 koo haal hii mein jatil aaee key bajaay jatil IV key upa-ikai key roop mein pahachaana gayaa haye, pahale seey aspashteekrit cox kii kamee vaale rogiyon koo aine. dee. yuu. aff. aeye. 4 utparivartan key liye aanuvanshik roop seey pareekshan kiya jaa sakata haye.
antahkriyaaen.
aine. dee. yuu. aff. aeye. 4 mein kaee protein-protein antahkriyaaen hain, jinamen ubquitin protein jaise ubquitin see aur yuu. bee. ell. 4aeye, saath hii kull3 aur park7 shamil hain.

