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Fraser syndrome is a rare genetic disorder characterized by partial webbing of the fingers and/or toes (partial syndactyly), kidney (renal) abnormalities, genital malformations, and/or, in some cases, complete fusion of the eyelids (cryptophthalmos) that may be associated with malformation of the eyes, causing blindness. In infants with Fraser syndrome, renal malformations may include improper development (dysplasia), underdevelopment (hypoplasia), or absence of one or both kidneys (unilateral or bilateral renal agenesis). In affected males, one or both testes may fail to descend into the scrotum (cryptorchidism), the urinary opening (meatus) may be abnormally placed on the underside of the penis (hypospadias), and/or the penis may be abnormally small (micropenis). Affected females may have malformed fallopian tubes, an abnormally enlarged clitoris (clitoromegaly), and/or an abnormally shaped uterus (bicornate uterus). In addition, the folds of skin on either side of the vaginal opening (labia) may be abnormally fused. Infants and children with Fraser syndrome may also have additional abnormalities including malformations of the middle and outer ear that may result in hearing impairment. Fraser syndrome is inherited as an autosomal recessive genetic trait.
Fraser syndrome is characterized by multiple physical abnormalities. These may include eye defects with complete fusion of the eyelids (cryptophthalmos), malformed or missing kidneys (renal agenesis), partial fusion of the fingers and toes (syndactyly) and middle and outer ear deformities. The nose is usually broad with a flattened bridge and deep indentations on the side of each nostril. Other characteristics may include hair growth that extends from the forehead to the eyebrows, high or cleft palate, malformation of the eyelid ducts that convey tears, a displaced navel, malformed or missing larynx, widely spaced nipples, malformation of the pubic bones and mental deficiency.
Incomplete development of the genitals may be symptomatic of this syndrome. In males there may be an abnormal opening of the urethra on the underside of the penis, or failure of the testicles to descend into the scrotum (cryptorchidism). In females there may be a single or double uterus with horn-like extensions (bicornuate uterus), an enlarged clitoris (clitoromegaly), malformed fallopian tubes or a fusion of the vaginal opening (labia).
Fraser syndrome is an autosomal recessive genetic disorder. The mutant gene has been tracked to the long arm of chromosome 4 (4q21).
Chromosomes, which are present in the nucleus of human cells, carry the genetic information for each individual. Human body cells normally have 46 chromosomes. Pairs of human chromosomes are numbered from 1 through 22 and the sex chromosomes are designated X and Y. Males have one X and one Y chromosome and females have two X chromosomes. Each chromosome has a short arm designated "p" and a long arm designated "q". Chromosomes are further sub-divided into many bands that are numbered. For example, "chromosome 4q21" refers to band 21 on the long arm of chromosome 4. The numbered bands specify the location of the thousands of genes that are present on each chromosome.
Genetic diseases are determined by the combination of genes for a particular trait that are on the chromosomes received from the father and the mother.
Recessive genetic disorders occur when an individual inherits the same abnormal gene for the same trait from each parent. If an individual receives one normal gene and one gene for the disease, the person will be a carrier for the disease, but usually will not show symptoms. The risk for two carrier parents to both pass the defective gene and, therefore, have an affected child is 25% with each pregnancy. The risk to have a child who is a carrier like the parents is 50% with each pregnancy. The chance for a child to receive normal genes from both parents and be genetically normal for that particular trait is 25%. The risk is the same for males and females.
All individuals carry a few abnormal genes. Parents who are close relatives (consanguineous) have a higher chance than unrelated parents to both carry the same abnormal gene, which increases the risk to have children with a recessive genetic disorder.
Dominant genetic disorders occur when only a single copy of an abnormal gene is necessary for the appearance of the disease. The abnormal gene can be inherited from either parent, or can be the result of a new mutation (gene change) in the affected individual. The risk of passing the abnormal gene from affected parent to offspring is 50% for each pregnancy regardless of the sex of the resulting child.
Diagnosis depends on a good family history and physical examination. Confirmation is generall. easy and is performed by means of imaging devices.
Treatment of Fraser syndrome may include surgery to correct some of the malformations associated with this disorder. Other treatment is symptomatic and supportive. Genetic counseling may be of benefit for families of children with this disorder.
Information on current clinical trials is posted on the Internet at www.clinicaltrials.gov. All studies receiving U.S. government funding, and some supported by private industry, are posted on this government web site.
For information about clinical trials being conducted at the NIH Clinical Center in Bethesda, MD, contact the NIH Patient Recruitment Office:
Tollfree: (800) 411-1222
Email: [email protected]
For information about clinical trials sponsored by private sources, contact:
Stevens, C. In NORD Guide to Rare Disorders. Lippincott Williams & Wilkins. Philadelphia, PA. 2003:196.
Gorlin RJ, Cohen MMJr, Levin LS, eds. Syndromes of the Head and Neck. 3rd ed. Oxford University Press, London, UK; 1990
Jones KL, ed. Smith's Recognizable Patterns of Human Malformation. 5th ed. W. B. Saunders Co., Philadelphia, PA; 1997.
Okumus N, Onal EE, Turkyilmaz C, et al. Resuscitation failure in a newborn undiagnosed in the prenatal period. Reuscitation. 2005;65:221-23.
Wong LJ, Lin YH Suwannarat P, et al. Mitochondrial DNA mutations in a patient with sex reversal and clinical features consistent with Fraser syndrome. Clin Genet. 005;67:252-57.
Hambire SD, Bhavsar PP, Jayakar AV. Fraser-Cryptophthalmos syndrome with cardiovascular malformations: a rare association. Indian Pediatr. 2003;40:888-90.
Vrontou S, Petrou P, Meyer BI, et al. Fras1 deficiency results in cryptophthalmos, renal agenesis and blebbed phenotype in mice. Nat Genet. 2003;34:209-14.
McGregor L, Makela V, Darling SM, et al. Fraser syndrome and mouse blebbed phenotype caused by mutations in FRAS1/Fras1 encoding a putative extracellular matrix protein. Nat Genet. 2003;34:203-08.
Rousseau T, Laurent N, Thauvin-Robinet C, et al. Prenatal diagnosis and intrafamilial clinical heterogeneity of Fraser syndrome. Prenat Diagn. 2002;22:692-96.
Slavotinek AM, Tifft CJ. Fraser syndrome and cryptophthalmos: review of the diagnostic criteria and evidence for phenotypic modules in complex malformation syndromes. J Med Genet. 2002;39:623-33.
McKusick VA, ed. Online Mendelian Inheritance In Man (OMIM). The Johns Hopkins University. Fraser Syndrome. Entry Number;219000:Last Edit Date;5/4/2005.
Fraser syndrome. Multiple Congenital Anomaly/Mental Retardation (MCA/MR) Syndromes. National Library of Medicine. nd. 2pp.
The information in NORD's Rare Disease Database is for educational purposes only and is not intended to replace the advice of a physician or other qualified medical professional.
The content of the website and databases of the National Organization for Rare Disorders (NORD) is copyrighted and may not be reproduced, copied, downloaded or disseminated, in any way, for any commercial or public purpose, without prior written authorization and approval from NORD. Individuals may print one hard copy of an individual disease for personal use, provided that content is unmodified and includes NORD's copyright.
National Organization for Rare Disorders (NORD)
55 Kenosia Ave., Danbury CT 06810 • (203)744-0100


text: BAFTA Snubs: Helen Mirren, Tom Hardy, 'Spectre' 1:45 AM PST 1/8/2016 by Scott Roxborough FACEBOOK TWITTER EMAIL ME 'Spectre,' Courtesy of Metro-Goldwyn-Mayer Pictures/Columbia Pictures Daniel Craig in Spectre. There were also no noms for Johnny Depp, Michael Caine or the cast of '45 Years.' The British Film and Television Association unveiled the nominations for the 2016 BAFTA Awards on Friday morning, but some of Britain's and Hollywood's biggest stars and films didn't get any shots at the honors. Amid the crowd of familiar names and expected honorees — Eddie Redmayne and Michael Fassbender, Cate Blanchett and Brie Larson, Carol and The Martian in multiple categories — there were several notable snubs. The biggest surprise was the awards shut out for Spectre. The latest James Bond film was the number one British film of 2015, earning $139 million locally, but it failed to impress BAFTA voters. Spectre was snubbed in the big categories of best film, best British film and best director and didn't even get a mention in the technical categories of editing, sound, cinematography or visual effects. Nearly as striking were this year's BAFTA acting snubs. While the likes of Bryan Cranston, Idris Elba and Rooney Mara earned their first-ever BAFTA noms, several veteran British talents were left out. The British academy ignored Charlotte Rampling and Tom Courtenay for their critically acclaimed performances as a long-married couple in 45 Years (though the film did get one nomination in the best British film category). While she has won multiple BAFTAs, Helen Mirren's performance in Trumbo went unnoticed, as did Tom Hardy's turn as the title character in Mad Max: Fury Road, even though the film picked up seven BAFTA noms, all in technical categories. Others notable for their absence on the BAFTA nominations list were Johnny Depp, who was ignored for his turn as Boston gangster Whitey Bulger in Black Mass, a film shut out across the board on Friday; Jacob Tremblay, the 9-year-old sensation who turned in a star-making performance in Room; and Michael Caine for Paolo Sorrentino's Youth, a role that recently earned him a best actor honor at the European Film Awards. In the directing category, Danny Boyle was passed over by BAFTA for his helming of Steve Jobs. The film, however, picked up a best actor mention for Michael Fassbender, best supporting actress nom for Kate Winslet and an adapted screenplay nom for Aaron Sorkin. FACEBOOK TWITTER EMAIL ME Scott Roxborough firstname.lastname@example.com sroxborough

subset: commoncrawl


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The FIYA Flag Football Championship game was set Wednesday and Thursday with two well played Final Four games. First, Holy Trinity got off to a fast star against KIPP Academy of Opportunity, only to see KIPP battle back and make it a game in the second half. The Chargers held on though to advance. Then in a back and forth game between evenly matched teams, St. Anastasia and Century Academy fought hard for the their chance at the title. After exchanging leads throughout, St. Anastasia was able to make some big plays late to hang on for the victory and move on to the title game.
All four teams now advance to FIYA Championship Sunday December 1st at the Los Angeles Memorial Coliseum. Tickets are $10 and can be purchased at Gate 3960 on game day beginning at 9 AM. The 3rd Place game kicks-off at 9:45 AM with the championship to follow at 11:00 AM.


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This weekend was Boss' last soccer practice. How did that happen? I swear it went so fast. (remind me of that in years to come when I'm like oh another soccer game. ugh) Afterwards we went to a very kid friendly lunch at Red Robin. Gone are the days of leisurely Saturday brunches with poached eggs and mimosas by the beach and bring on the bottomless fries and grilled cheese.
It may be less glamorous, but it more joy filled that's for sure.
The day started out crazy rainy and cold and then bloomed into a lovely Spring-fever inducing day.
Then…and most importantly. This guy, our adorable non-sleeping Huckleberry is officially 9 months old.
He has now been out longer than he was in and boy howdy has it been a heck of a ride. He is sweeter than sugar and talking up a storm. He wields mama, dada, bob-bob and uga (again) with the power of Greyskull and knows how to melt hearts with a hey dada when he really wants something.
Too bad he doesn't like to sleep. Because I sure do. And I miss it ever so much.
What I wore: Me: Coach sunglasses via TJMaxx, Old Navy trench, AE Jeggings, Jessica Simpon boot socks (my soul dies a little every time I buy something with her stamp on it. Why must her shoes be so cute?) Gap fake wellies, Cynthia Rowley bag. Huckleberry: Osh Kosh Sweater, cassette tape screened onsie that TOTT made, too bad you can't see it. No idea on the jeans, and Children's place shoes. Boss: HIGH FASHION! Yeah. Adidas pants and shoes, no idea on the polo, and Children's Place sweatshirt.
linking to Stepping out Saturday


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Top 5 Hardscape Designs in the Granbury, TX Area
As you drive past Granbury's many attractive homes (both small and large), take note of the various ways in which homeowners use landscaping to achieve a unified and welcoming exterior.
Landscape design takes a home to another dimension through the artistic and skillful integration of softscape and hardscape elements. Softscape includes those elements that are living and mutable; such as shrubs, trees, flowers, and turf. Hardscape elements are solid and permanent, such as patios, pathways, fountains—actually, a multitude of elements are available, limited only by your imagination.
As you daydream about the design that will best suit your needs and aesthetic sensibilities, there are a couple things to keep in mind:
- Even if starting in one area, keep in mind the entire property.
- Have no more than one or two primary visual elements. More than that will subtract from, not add to, the overall effect.
- Be kind to the environment. If thinking of installing a fountain or waterfall, for instance, plan to capture the water and not let it go down a drainage pipe.
You're sure to find ideas in our Top 5 Hardscape Designs that demonstrate innovation, harmony, and artistry.
1. Bonick Landscaping
Photo: Houzz
Why we like it:
Bonick created a sensuous retreat in what previously had been a small backyard. You don't need acres to fulfill your landscaping dream. A saltwater pool, raised spa, and outdoor fireplace are enhanced by the indirect lighting that glows throughout the scene.
2. Artistic Stoneworks
Photo: Houzz
Why we like it:
There has long been the desire to bring the outdoors into our homes with plants, expansive windows, or natural materials. This patio takes the inside outdoors, with the living area fashioned from natural materials. Sit and reflect in front the fireplace while surrounded by the softscape elements of the design that provide you with as much privacy as you have inside your home.
3. Cuttin' It Right Lawn Care
Photo: Houzz
Why we like it:
What an enticing place to enjoy your hot tub! There you are, ensconced in the warm water in the quaint gazebo, surrounded by evergreens, plants, bushes, flowers—greens for all seasons. A special touch is the intricately cut stone path leading to the gazebo.
4. Fowlkes Norman and Associates, Inc.
Photo: Houzz
The pergola is a classic Graeco-Roman design accented with flower-filled Grecian planters on pedestals. The established trees are incorporated into the design as they hover above the pergola, providing additional shade. The contemporary table and chairs are a sharp, clean contrast to the classical setting. And the chairs will survive wet swim suits.
5. Fossil Creek Tree Farm and Nursery
Photo: Houzz
Why we like it:
This is a high-quality example of a landscape design that not only fits the home it's attached to but also fits with the surrounding land. The glistening and gracefully shaped pool is framed with the ruggedness of natural stone accents that are echoed in the custom-made stone bench.
That's it for our picks!
Have questions about lawn care? Visit our Granbury, TX lawn care page or share your thoughts in the comments below.


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Rolling out ..The All new Benz SL
The Real one of it's kind..One more attempt on creating a perspective view of the beautiful Roadster.
This is one more snap on the attempt to create Different perspective photos using the powerful options available from photoshop. My complete set on 3D manipulation can be seen here.


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Room Details
The Koa Lagoon 502 is a deluxe 1 bedroom/1 bath accommodation featuring a king bed, and a queen sofa sleeper. It also has a TV in the living room and bedroom. AMENITIES Washer/Dryer, Bathroom, Dishwasher, Microwave, Kitchen, Kitchenware, Tea/Coffee Maker, Dining area, HD Expanded Cable Channels, Alarm clock, Air Conditioning, Balcony, Telephone, Shower, Bath, Radio, CD Player, Ceiling fans, DVD Player, Refrigerator, Seating Area


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Re: Are individual jUnit test cases the same as a main method?
No, they are not the same thing. A main method in Java class in an entry point to application. While jUnit test case are for unit testing. The jUnit can report to you whether a test is pass or failed. You can for sure to use the main method to test. But you have to do alot of manual work.Website: Learn Java by Examples
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I was going through some computer files the other day and was surprised to find multiple folders from various iterations of the Fusion 47 website dating back to the late 1990s. As I started looking I realized that there was a bunch of content that I'd taken offline. There were stories, articles, photos…all kinds of stuff that may be useful, or at least entertaining to read. Of these items I found a section featuring a different climb each month. These are climbs I've done and generally considered classics, in one way or another.
I also dug up a page that had all of the information about the boulder I built in my backyard years ago. The boulder has since been torn down but all the pics and documentation remain.
But what I was really excited to find was a page about the history of the Norman Bouldering Competition from the first event in 1998 up through the last one in 2004. I am super excited to be re-launching the Norman Bouldering Competition (#7!) at our new gym, Climb UP! The event is Saturday, February 21, 2015. If you would like to register for this year's NBC you can go here.


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The Simpsons are currently in dire trouble with the Brazilian government for an episode in which they go to Rio and the children get taught how to do a lascivious dance called the Penetrada. This movie is set in Mexico, not Brazil, but the irresistible rhythm of the Penetrada throbs all the way through it nonetheless. It is the story of two cute guys from Mexico City, Tenoch and Julio, played by Diego Luna and Gael Garcia Bernal (from Amores Perros). Young, dumb and full of come, they take a road trip to a distant beach with a glamorous but troubled older woman, Luisa (Maribel Verdu), and get an education at her hands that is anything but sentimental.
From the first frames, it reveals itself as an outrageously, uproariously sexed-up piece of work, stylishly directed by Alfonso Cuaron from a script by his brother Carlos. The camera, in one of many unobtrusively long takes, noses into the bedroom of Tenoch who is shagging his girlfriend Ana with all-nude, slack-jawed, buttock-pounding fervour. Like the maladroit boy himself, the director does not believe in warming his audience up with narrative foreplay, and it's the same story when we cut to the family home of Julio's girlfriend, whose parents allow him into her bedroom to help her look for her passport, and she gleefully wrenches her tracksuit bottoms down.
The two girlfriends go off on a summer holiday trip to Italy, leaving our heroes with no outlet for their permanent hormonal uproar, other than to lie on the diving boards of a local swimming pool, their wrists a blur, wanking themselves into a frenzy of boredom and frustration. Like sex, masturbation is treated with an unapologetic frankness rarely found in our genteel anglophone cinema. The new object of the guys' fantasies: the beautiful, enigmatic Luisa, whom they've met at a grand society wedding (Tenoch's father is a dodgy politico). Before they know what's happening, she agrees to head off with them on a journey of discovery: a three-way love romp on wheels.
It looks like it's obsessed with sex - but actually this film is obsessed with death. The paradox is often carelessly invoked, but Cuaron's movie really does pull off the trick of mingling the ideas of sex and death, showing their blood relation. Every so often, he cuts out the soundtrack, emphatically, almost crudely, and has a voiceover point out some grim point of interest along the roadside: the corpse of an anonymous construction worker hit by a car because the pedestrian crossing was inconvenient for the building site; later, there's a roadside memorial for a horrific crash 10 years before.
While the three get high in the car and gigglingly discuss the merits of inserting a finger up the anus during intercourse, Cuaron's directorial gaze gets distracted by the sight of three sinister cops roughing someone up. The voiceover provides an extraordinary dose of severity, combining social analysis, political insight and an unflinching glimpse into the secret lives of these apparently ingenuous young boys. It is as if the American Pie DVD had a director's commentary by Susan Sontag or JK Galbraith.
All the time, the death theme continues underneath. After quite a bit of weed, Luisa tells her two companions about her first sexual experience; then she tells them the boy died, at the age of 17. Their age. Later on, Luisa, her face clouded with obscure melancholy, tries to teach a little girl to float in the sea "like a real dead body". And what is it that Julio wants to listen to on the car radio? Not rock'n'roll, not Latino music, not dance music. What he wants is Brian Eno's desperately sad By This River: "You and I/ Underneath the sky that's ever falling down, down, down/ Ever falling down." This happens to be the song played at the end of Nanni Moretti's anguished tale of family bereavement, The Son's Room.
Luna and Bernal give nicely spontaneous, natural performances, the kind that Cuaron has apparently been able to elicit just by placing the camera in front of them and letting them riff, while cinematographer Emmanuel Lubezki, who shot Ali and Sleepy Hollow, provides him with fluent, loose, daringly protracted steadicam shots. Lubezki and Cuaron find riveting images and cameos, perhaps genuine discoveries from their location work on the road: an old lady does a jigging little dance in the kitchen of her bar, and a placid village festival queen, dressed like a bride, smiles at passers-by while her neighbours solicit pious donations.
As Luisa, Verdu is sexy, tender and poignant. She provides the movie's ballast and maturity, a kind of mediating influence between the boys' puppyish vigour and the cold, pitiless detachment of Cuaron's voiceover - and she has the best line in the picture, exasperated with her quarrelling travel companions: "Play with babies and you end up washing diapers!" Her aplomb is shown most obviously when she finally invites them into her room for the much-anticipated threesome, and manoeuvres them into kissing each other. At this point, when I saw this film first at Venice, an elderly Italian in front of me sighed with eloquent resignation: "Andiamo." ("Here we go.")
After working on English-language movies such as A Little Princess and Great Expectations, Cuaron has made a triumphant return to his native Mexico City. This film is an exhilarating adventure in narrative, eroticism and social commentary.
• This article was amended on 30 September 2010. The original suggested that Tenoch and Julio's diving-board scene predated the wedding where they meet Luisa. This has been corrected.


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In the 1990s, the wreck of an unidentified U-Boat was discovered on the ocean floor off New Jersey in approximately 230 feet of water. It had suffered a massive explosion in the center of the pressure hull, and the conning tower was blown completely off the boat. The wreck was upright on the bottom. The divers who discovered it decided to try to identify it, a task they thought would take them a few days. However, this was not to be the case.
The first problem they had was that the aft section of the boat, which contained the Diesel motor room and the electric motor room, were not only reasonably intact but were sealed by debris at the forward end of the Diesel room. This was problematic because the electric motor room was where U-Boats stored spare parts, which were labelled with the boat's number using metal and laminate tags that would have survived the years of immersion.
During their searches of the accessible crew compartments, the divers turned up a knife with the name Horenberg carved into its handle. They took this knife to Germany and searched the archives of the U-Boat service. There, they found that there was only one man named Horenberg in the Kriegsmarine during the Second World War; he had been last posted to U-Boat U-869. However, the archives also showed that U-869 had met its end near Gibraltar, on the Atlantic side of the Straits, in early 1945.
The divers continued to work the wreck for six years, despite three fatalities. One diver was simply swept away by currents, his body not found for six months; it was never determined what had killed him. A father and son team were diving the wreck when the son became trapped; the father extricated him, but they were low on air and unable to find their reserve tanks. They surfaced, without decompressing. The father died on the boat, and the son died in a compression chamber in hospital.
Another artifact was found; the remnants of an aluminum engineering diagram. In the lower right corner, the symbols IX-C 40 and the word Bremen could be made out. The searchers deduced that the boat was a Type IX-C U-Boat, built in the Bremen yards in 1940. This narrowed it down to perhaps twenty or twenty-five boats out of the nearly 1,000 U-boats built in Germany during the war.
Finally, in a daring (some felt, foolish) maneuver, the team leader penetrated the aft electric motor room. He squeezed past the obstructions in the Diesel room (a fallen oil tank) by removing all but one tank of tri-mix (breathing gas), and holding that one loose in front of him. This gave him twenty minutes of air. The first attempt nearly ended in another death; he was trapped by a piece of steel, and his backup diver was forced to surface due to low gas levels; luckily, he freed himself and made it back to the surface. The second attempt went more smoothly, and he recovered a boxed spare part which was examined on the surface as he removed his gear.
On the box was a tag, reading U-869. The archives were incorrect. They had found the grave of the U-869, a Type IX-C, built in Bremen in 1940. During the final days of 1944, it sank off the coast of New Jersey while patrolling U.S. coastal waters for unprotected shipping.
Due to confusion about her final orders, however, the German Navy (and the Allied auditors after the war) all were convinced that U-869 had met her end near Gibraltar.
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PPV Programming and Sports Events
Whether you want to catch the latest hot movie now, or you're a fan of high-energy sports, pay-per-view (PPV) gives you more ways to get the entertainment you want.
Boxing, Sports and More
Have you heard the water cooler and social media chatter about that next big fight? It's easy to order the upcoming boxing match and other sporting events on PPV right through your Midco® remote and on-screen guide.
PPV Equipment Requirements
PPV viewing and ordering availability varies by your cable equipment type. You can view PPV if you use a Midco TiVo® DVR, standard Midco DVR, HD digital receiver or standard digital receiver. HD digital adapters, digital adapters and CableCARDS (even when used in conjunction with a TiVo or DVR) are not compatible with PPV.
Movies on Your Time
Hot, new releases, old favorites and everything in between – Midco has it, ON Demand.
Get the perfect movie for date night, family movie night, or a rainy day – and settle in with some popcorn. Feel like binge watching your favorite show? You can do that, too. Hundreds of hours of free movies and shows are at your fingertips.
Equipment Details: ON Demand viewing is available if you use a Midco TiVo, standard Midco DVR, HD digital receiver or digital receiver. ON Demand is not available for HD digital adapters, digital adapters and CableCARDs.


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Apr 15 2007
Cropping in Paint Shop Pro v7
I know that some of you still have and use older versions of Paint Shop Pro, like version 7. In fact, although I have version 10 on my computer, I still have version 7 loaded as well. Why? It is a smaller program and thus loads much much faster than newer versions and uses less computer resources. If I want to do a quick crop of an image, or some other simple task, I'll use version 7.
However, version 7 is not as easy to use on some tasks. One example is cropping. Newer versions have simpler ways of doing these tasks.
Today's Paint Shop Pro video tutorial will show you how to crop in version 7 and next weekend I'll try to post the same video using a newer version, so you can see the difference.
While you watch the video, take special note of the circled area as indicated in the screen shot below. Each common print size has a different ratio. By knowing, and using, these ratios, you can have your photos properly cropped before printing.
print size horizontal ratio vertical ratio -------------------------------------------------- 4 x 6 1.500 0.667 5 x 7 1.400 0.714 8 x 10 1.250 0.800
Click on the kitten and rabbit screen shot below to view the video. After the video finishes, it will return you to our main (Home) page. The video is about 1.8 MB in size and runs for 1:40.


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MESQUITE — On the way to proving themselves on a state-wide level, Whitehouse turned many heads with an impressive performance against John Tyler last week.
And with the postseason having arrived, the Wildcats drawn another tradition-rich program this week — Ennis.
Today, the Wildcats (9-1) and Lions (8-2) meet in a Class 4A Division II bi-district playoff at Mesquite Memorial Stadium. The matchup features up-and-coming Whitehouse against traditional power Ennis, an owner of three state titles since the turn of the century.
Whitehouse enters the matchup on the heels of a dramatic 45-38 loss to second-ranked John Tyler, a classic showdown for the District 16-4A title in front of more than 12,000 fans. Ennis also heads into the following a loss, but the Lions have dropped back-to-back games against Lancaster (51-14) and Waxahachie (16-0).
Whitehouse quarterback Patrick Mahomes earned Class 4A's Built Ford Tough Player of the Week honor with his performance against John Tyler, in which the junior completed 28 of 57 passes for 445 yards with five touchdowns (four passing, one rushing). The first-year starting quarterback now has 3,061 yards and 37 touchdowns on the season, plus has rushed for six scores.
Fellow junior Jake Parker moved into the team lead in receptions last week, having caught 55 passes for 770 yards and seven touchdowns this season. Senior Dylan Cantrell, a Texas Tech pledge, has 52 catches for a team-high 1,024 yards and 12 scores.
Unlike their state-championship teams, Ennis likes to run the football these days. Lions running back Terence Williams leads the way with 185 carries for 1,174 yards and 14 touchdowns, while Nick Gabriel is second on the team in rushing with 118 carries for 698 yards and 11 TDs.
Quarterback Brandon Adams has completed 67 of 151 passes for 974 yards and 13 touchdowns.
The winner will meet either Sulphur Springs (8-2) or Wylie East (7-3) in the area round. Whitehouse has built a rivalry with Sulphur Springs in recent seasons, and beat the Wildcats 38-33 earlier this year.
Whitehouse is in the playoffs for the seventh consecutive season. The Wildcats' best run during the span came 2006, when they advanced to the third round and finished 10-3.


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Here is a look at our picks this week for programming on myTV38. See our program guide for the complete schedule of what to watch!
Monday 5/12 – 5:00pm
The King of Queens
"Deacon Blues"
Doug bumps into Deacon with another woman while picking up takeout. Carrie says that it's still considered cheating even if they keep their clothes on.
Carrie: Doug, do I strike you as stupid and/or unaware?
Doug: Nope. You're sharp as a Ginsu, pretty girl.
Tuesday 5/13 – 6:00pm
Two and a Half Men
"Untainted by Filth"
Charlie and Alan go out after Charlie sets his wedding date. However, they both wake up perplexed in bed with the same woman.
Alan: Who would've guessed that of the two of us, I'd end up being the care-free bachelor?
Charlie: If by care-free you mean broke and homeless, then everyone could have guessed that.
Wednesday 5/14 – 7:00pm
The Big Bang Theory
"The 43 Peculiarity"
Howard and Raj are determined to figure out why Sheldon leaves the apartment every afternoon at 2:45. Meanwhile, Penny and Leonard must deal with jealousy in their relationship.
Leonard: It's not to go to the bathroom. He goes at 8:00 AM, with follow-ups at 1:45 and 7:10 on high-fiber Fridays.
Howard: It's sad that you know that.
Leonard: That's just the tip of the sadness iceberg.
Thursday 5/15 – 5:30pm
The King of Queens
"Steve Moscow"
Carrie and Doug hire Russian workers to fix some home repairs. However, they must resort to bribing them to make sure they come to work on time.
Carrie: Where are they?
Doug: Maybe they didn't feel like rushin'.
Carrie: Do you have to make a Russian joke every morning?
Doug: Yes, I do.
Friday 5/16 – 7:00pm
The Big Bang Theory
"The Santa Simulation"
The girls invite Raj out for ladies' night so they can help him find a woman. Meanwhile, Sheldon revisits old Christmas memories during Dungeons and Dragons.
Raj: I'm always attracted to women I can't have; I do it all the time. I did the same thing with the two of you.
Amy: The two of them? I don't understand.
Raj: Well, uh, there was a time when I had a thing for Penny, and I thought she was into me too because she got drunk and naked and climbed into bed with me, but apparently I misread those signals.
Amy: And you like Bernadette also?
Raj: Uh, that was before Penny. I make it a rule to only fall for one of my friends' girlfriends at a time. I'm very old-fashioned that way.


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Listings in Apple Pie Trail, General Store, Yoga Studio, Family Meals & Take Out, Specialty Food Shops and Farms in Glen Huron and Orangeville
Giffen's Country Market & Restaurant
Giffen's is currently offering a call-in dinner box Tuesday - Friday. For $70 customers can pick 5 large frozen meals (4-6 servings) from the menu. The restaurant is currently closed for takeout and delivery.
55 Station Street
Glen Huron, Ontario, South Georgian Bay L0M 1L0
Mylar & Loreta's Restaurant
Mylar & Loreta's Restaurant is a popular dining establishment for locals and tourists alike. It's convenient proximity to many year-round outdoor recreational activities, with a great reputation for serving fabulous home-cooked meals.
Grey County Rd 124 , ON
Orangeville, Ontario, South Georgian Bay N0C 1M0


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What is SMI-S? What is the EMC SMI-S Provider? What is ECOM?
What is SMI-S? What is the EMC SMI-S Provider?
The first step in understanding the functionality of ECOM and the EMC SMI-S Provider, is to first answer the question of what is SMI-S? Essentially it is an attempt at standardisation of storage management and it's related technologies to increase interoperability. This standardisation was created by The Storage Networking Industry Association (SNIA) who envisions "leading the storage industry in developing and promoting vendor-neutral architectures and standards" according to their mission statement. This is lead by the SNIA's Storage Management Initiative (SMI). The Storage Management Initiative Specification (SMI-S) is a standard that has been developed by the SNIA.
How many more acronyms are there?
A few more.. but I'll keep it short. These are more for reference than anything else.
- The SMI Architecture is based on Web-Based Enterprise Management (WBEM) from the Distributed Management Task Force (DMTF).
- The architecture is a client-server model that uses CIM-XML as the protocol. The client interface is the combination of the operations defined in CIM-XML and the model defined in SMI-S. The model is defined using the Common Information Model (CIM) and based on the CIM Schema. The EMC implementation of CIM is named ECIM.
- The CIM is an object oriented model based on the Unified Modeling Language (UML). Managed elements are represented as CIM Classes that include properties and methods to represent management data and functions.
What is ECOM?
The EMC Common Object Manager (ECOM) enables communications and common services for applications. ECOM supports the ECIM which is used to represent the wide variety of components found in data centers using the CIM schema. The CIM schema provides a common methodology for representing systems, networks, applications, and services as a set of object-oriented models that can be bound to real-world functionality. Management applications based on CIM can interact with resources such as data storage hardware from multiple vendors, without direct knowledge of the underlying systems.
CIM classes identify types of resources. A class can represent a broad category of resources or can be subclassed to represent a specific type. For example, the class CIM_NetworkPort represents a broad category of heterogeneous network communications hardware, while EMC_NetworkPort is a subclass that represents an EMC specific subset. While classes define types of things found in a managed IT environment, instances represent individual implementations of a class. A specific port at a specific network address is an example of an instance of class EMC_NetworkPort.
The ability to exchange information, retrieve data, execute commands, and discover available resources are also required to link the elements in a network. Before resources can be managed, they must first be discovered by management applications. The Service Location Protocol (SLP) defines a mechanism for locating services in a network. Applications looking for a service are called user agents (UA), and applications providing a service are called service agents (SA). In terms of SLP, ECOM acts as a service agent that advertises its address and capabilities. When a UA has found the ECOM-exposed services that it needs, it begins communicating directly with each ECOM instance via CIM-XML messages.
A successful SMI implementation
ECOM is vital to the successful implementation of SMI. In order to successfully implement SMI there are two requirements; A WBEM Server and a SMI Provider. A WBEM server is responsible for routing of requests and management of SMI Providers. An SMI Provider will use an Application Programming Interface (API) to communicate with devices and retrieve the information in CIM format. In this scenario the ECOM service and the EMC SMI-S Provider are paired together to successfully implement an SMI-compliant interface.
So what makes this the EMC SMI-S Provider as opposed to a generic SMI-S Provider? Due to the exceedingly large number of classes available in CIM and because of their broad nature, profiles were created. Profiles allow one to make use of CIM for specific domains. A profile defines the set of classes and properties that must be used to model the managed resource. The EMC SMI-S Provider is made up from the array providers. The profiles from these providers allow an SMI-S Client to retrieve information from, or make changes to specific storage systems.


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Sold Out.
Whether you're having dinner or you're relaxing and playing Kingdom Hearts, you'll be able to enjoy your favorite beverage while still showing love for you favorite game series with this two pack of Kingdom Hearts glasses! Featuring two different Sora and Mickey decals, these awesome glasses are sure to steal the hearts of Kingdom Hearts fans everywhere.


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Rehab Resources has been leading the way in pediatric rehabilitation in the Midwest for 25 years! We are a therapist owned and operated organization that is focused on achieving superior student outcomes through our core values of performance, compassion and agility.
Advantages of partnering with Rehab Resources for your school district include:
Contact us to learn more about a partnership with Rehab Resources for your school!


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As consumers, we often pay insurance premiums for years relying on the promise made by the insurer that they will pay claims for any loss covered by the policy. Bad faith allegations usually arise from claims wrongfully denied by the insurer.
Some examples of insurance bad faith include:
- Wrongfully denying coverage for claims that should be covered by the policy
- Misrepresenting policy provisions or important facts related to coverage
- Failing to attempt to come to a reasonable settlement when liability is clear
- Failure to provide a reasonable explanation when denying a claim
Not every claim denied or decision you disagree with will necessarily constitute bad faith. But, if you have been unfairly treated or have had a claim wrongfully denied or delayed, you may have a cause of action against your insurance company.
If this has happened to you, an Arizona Insurance Bad Faith Attorney with expertise in insurance bad faith can review your case to help you determine if you have a case against the insurer and provide guidance on how to proceed.
If you have had a claim wrongfully denied by an insurer, have been treated unfairly, or have been subjected to unreasonable delays in the processing of your claim, contact us at the Law Office of Douglas F. Dieker for a confidential assessment of your situation.


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The Secret to Doubling the Size of a Small Bathroom
And five other design tips you might have missed this month!
While bathrooms are typically the smallest rooms of any home, there's no reason for them to feel like it. We're firmly of the opinion that bathrooms should be a spa-like hideaway, with all the functionality that practicality demands of course, yet beautiful enough to transport you to a world of relaxation after a long day at work. And that just ain't going to happen in a poky claustrophobic space. Luckily for you, we're about to reveal the secret to doubling the size of a small bathroom. Keep reading to discover how to make a small bathroom look bigger, and five other design tips you might have missed this month.
Design Tip #1
Use mirrored design accents to make a small bathroom look bigger
How to make a small bathroom look bigger? Well, simply put, it all comes down to clever design. We all know that adding a mirror instantly brightens a space, making it feel infinitely larger. Why not then go one step further with mirrored design accents? That's what the design team behind the bathroom at Magnolia House did, complete with mirrored bathtub and shiny chrome hardware. When paired with the neutral white and greige color scheme, the space feels twice the size!
See more of Magnolia House HERE.
Design Tip #2
Treat lighting as more than just a practical necessity
Yes, lighting is a necessity, but that doesn't mean you can't use it as a design feature too. And I'm not simply talking about having a beautiful sculptural light piece on display. Think about lighting in terms of the mood you want to create in a space. Take this sauna-inspired bathroom for instance, which uses recessed lighting, candles and spotlights to create a cozy glow reminiscent of a relaxing spa. In the age of technology, smart lighting can also be used to create everything from a fun party environment to an intimate home theater.
Head HERE for other ways to make your bathroom feel like a luxury spa.
Design Tip #3
No garden? No problem, head to the rooftop instead
Given our affinity for all things green, our least favorite part of apartment living has to be that lack of outdoor space. Specifically, the lack of space for a herb and vegetable garden. But that's all about to change thanks to some creative 'blue-sky' thinking. Rooftop gardens might not be new, but they are novel, which is why we enlisted the team over at Rooftop Republic to share their tips and tricks for creating one of our very own. Note to self: sunlight is key!
Discover how to create your own rooftop garden HERE.
Design Tip #4
Wood panels are not just for walls and floors
If you're a long time reader of NONAGON.style, you'll know that we're partial to a wood panel here and there. Whether in the form of wood panel walls, or sleek wood flooring, we just can't get enough. We did think that we had all the wood panel bases covered, until we came across wood panel ceilings in the Benguela Cove home tour. A modern take on rustic country beams, the design detail is subtle yet effective, drawing the eye and elongating the rafters. It's safe to say, we're in love.
Check out more of the Benguela Cove home tour HERE.
Design Tip #5
Steel frame windows are the ultimate dividing hero for studio apartments
Open plan studio apartments are all well and good in theory, but practically speaking, they're perhaps less functional than one might think – especially when it houses more than one tenant. Luckily for us, Egue Y Seta revealed how to get all the benefits of open plan living (i.e. generous light and that sense of spaciousness), without actually having an open plan layout. For this, it turns out our old friends, steel framed windows, are the hero of the hour. Working as partitions, they do a good job in demarcating private spaces without compromising on the light and ventilation front. In our book, that makes them the perfect room divider.
Peek into Egue Y Seta's design in full HERE.
Design Tip #6
Don't be afraid to decorate with black
If white is the golden child of interior hues, black is undoubtedly the bad egg – the black sheep of the wall color family if you will. But if Sarah Ward has anything to do with it, that won't be the case for much longer. In a tour of the interior designer's Calgary home, we were struck by the dark-walled den which Sarah claims to be her favorite room of the house. And it's not hard to see why. The black walls create a cozy intimate feel, while simultaneously highlighting the bold vibrancy of her modern abstract artwork. Consider us official converts!
See more of Sarah Ward's home HERE.
For more design tips you're going to want to head on over to our 'Tips & Guides' page. Here you'll discover everything from how to create a functional mudroom to how to bring mindfulness into your home, and much more!


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David Webster's pottery is a privately owned pottery studio in Sayre, Pennslyvania. He came to me and asked if I could migrate his existing site from sites.google.com to his own domain, and build it so that he can easily manage the content himself.
This is a website that I built for my own wedding. The site's framework is built on Bootstrap. A custom RSVP and SMS system was developed for this site.
The Belles Springs Country Barn Restaurant was one of the first websites that I developed for a former employer. He needed a simple website that allowed dynamic control of his menu, times, and images for his gallery.
San-Du Auto Sales is a privately owned used car dealership in Wellsboro, PA. I was asked to develop a website for the owners that was easy to use, scalable, and user-friendly so that they could market for online sales and advertising.


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Thanks to our pals at TrendHunter, we've got a great BlackBerry TV (bbTV) review to toss your way. For the less-informed, bbTV (yes, lower case), is the world's first television broadcasting on a Blackberry. Overall, the service receives a favourable review (unlike our review of the bbTV logo). U.S. readers, just a heads up - the service is only available North of the border for now, and you know what that means - we can watch Newhart on our way home from the office before you can. So there.
"The episodes stream at 12-15 frames per second and the sound is very clear. Finally, it's a deal at $5 per month, which is pretty much free relative to the cost of a good data plan. "


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Working at Laerdal
We have set a clear vision, an ambitious goal and a roadmap to get us there. But we know that we cannot get there alone. Colleagues and collaboration are key. Find job opportunities here.
Interested candidates for any openings should send their Curriculum Vitae and Salary Requirements to firstname.lastname@example.com or confidential fax to 845-298-4557. For accommodations or assistance in applying or inquiring about any openings, please contact firstname.lastname@example.com.
This contractor and subcontractor shall abide by the requirements of 41 CFR §§ 60-1.4(a), 60-300.5(a) and 60-741.5(a). These regulations prohibit discrimination against qualified individuals based on their status as protected veterans or individuals with disabilities and prohibit discrimination against all individuals based on their race, color, religion, sex, or national origin. Moreover, these regulations require that covered prime contractors and subcontractors take affirmative action to employ and advance in employment individuals without regard to race, color, religion, sex, national origin, protected veteran status or disability.
Product Manager - B-Line Medical, A Laerdal Company - Washington D.C.
UX/UI Designer - B-Line Medical, A Laerdal Company - Washington D.C.
Technical Product Support Specialist - Based in Wappingers Falls, NY
Product Repair Specialist - Based in Wappingers Falls, NY
Customer Support Specialist - Based in Wappingers Falls, NY | Shifts vary 9-5, 10-6, 12p-8p


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Recurrent Stroke-Like Events Before Diagnosis of X-Linked Charcot—Marie—Tooth Disease
Awareness of pathognomonic findings may prevent unnecessary tests and treatments.
By Arayamparambil C. Anilkumar, MD
Initial Case Presentation
A white boy, age 11 years, was seen for a first occurrence of hemiparesis, ataxia, and dysarthria, which had been present for 3 days. He had a history of abdominal surgery a month earlier as treatment for a ruptured appendix. He was otherwise healthy and had no developmental delay. On admission, the patient had facial drooping, dysarthria, and ataxia. There were no signs of acute infection, signs of meningeal irritation, or vision problems. No hyporeflexia or sensory impairments were present.
His family history was negative for stroke, epilepsy, multiple sclerosis, and hemiplegic migraines. Multiple family members had symptoms of peripheral neuropathy, but none was formally diagnosed, including the patient's mother, maternal uncle, maternal grandmother, maternal great-grandfather, and a nephew of his maternal grandmother.
Diagnostic Testing
Along with routine hematological and biochemical tests, we obtained lumbar puncture and cerebrospinal fluid (CSF) analysis, brain MRI, brain magnetic resonance angiography (MRA), and an EEG. Analysis of CSF showed normal cell-count, protein, and glucose levels. There was no bacterial growth after CSF culture. Polymerase chain reaction (PCR) of the CSF was negative for common viral infections (eg, enterovirus, Epstein-Barr virus, or human herpes viruses). The EEG result was normal. Biochemical screening results were negative for mitochondrial and lysosomal disorders. Diffusion-weighted MRI (DWI) and apparent diffusion coefficient (ADC) sequences showed symmetric white matter signal alteration with restricted diffusion involving the bilateral centrum semiovale and the splenium of the corpus callosum (Figure 1). Brain MRA results were normal.
We treated the patient empirically with intravenous methylprednisone because of the brain MRI findings suggestive of demyelination. However, CSF analysis showed no evidence of demyelination (eg, presence of myelin basic protein or increased intrathecal immunoglobulins). Our patient's symptoms resolved after 1 day of hospitalization. A brain MRI taken 5 days later showed decreases in the amount of white matter signal abnormality. A repeat brain MRI taken 6 months later was normal, with complete resolution of the previously detected signal abnormalities. Clinical findings were resolved.
Case Presentation 3 Years Later
At age 14, our patient presented again after 1 day with acute dizziness followed by transient slurring of speech and left facial droop. He had a history of presumed viral gastroenteritis 4 weeks earlier.
Diagnostic Testing
Brain MRI findings were symmetric, restricted diffusion involving the bilateral centrum semiovale and splenium of the corpus callosum, similar to imaging findings at initial presentation (Figure 2). We treated the patient with methylpredisone, and again the symptoms resolved. At a follow-up outpatient clinic visit, genetic testing was ordered (because of the reported family history of neuropathy and diminished extremity reflexes), and results showed X-linked Charcot–Marie–Tooth (CMT) disease with 2 mutations in the gene for connexin: homozygous transversion of thymine for guanine at nucleotide position 467 resulting in a leucine for arginine substitution at codon 156. Annual follow-up visits were recommended.
Case Presentation 5 and 6 Years After Initial Presentation
At follow-up 2 years later and 5 years after his initial presentation, our patient had mild lower extremity weakness with foot drop and mild distal sensory loss.
At age 17, 6 years after the initial presentation, our patient presented with acute-onset facial weakness, right arm weakness, and dysarthria. A day earlier, he had intermittent slurring of speech, mild left facial weakness, and decreased sensation over the left side of his face. He had been apparently healthy since last 1 year ago, except for being diagnosed 3 weeks earlier with infectious mononucleosis.
He was dysarthric with decreased facial muscle movement on the left and mild wasting of the thenar muscles. There was mild weakness in his peroneal muscles, absent deep tendon reflexes in the lower extremities, and hyporeflexia in the upper extremities. He had decreased distal vibration sensation in all extremities. His gait was wide based, with noticeable foot drop, and he had difficulty with both heel and tandem walking.
Diagnostic Testing
We ordered a brain MRI that showed restricted diffusion in the bilateral periventricular white matter identical to the previous abnormal MRIs seen at age 11 and age 14. Results of routine blood chemistry and hematologic tests were normal. There was also restricted diffusion in the cerebellar peduncles that had not been seen previously (Figure 3).
We treated the patient with intravenous methylprednisone and his symptoms resolved completely in 24 hours.
As noted, this patient was diagnosed with CMT1X at age 14. CMT is a broad umbrella term for a variety of hereditary neuropathies.1 Usual onset is in early childhood, but diagnosis can be delayed until early adulthood. Distal motor and sensory neuropathy characterized by slowly progressing gait disturbances, pes cavus, and depressed tendon reflexes is characteristic.2 Patients occasionally present with central nervous system involvement.3-10 When peripheral neuropathy is not yet clinically manifested, recurrent encephalopathy with focal neurological deficits can make clinical diagnosis challenging.
Originally described as slowly progressive, predominantly peroneal muscular atrophy, several other types of CMT have been described since. The classic appearance of CMT includes distal muscle atrophy, with onset in lower extremities, champagne-bottle appearance of calves, high arched feet, equinovarus deformities, clawed hands, absent deep tendon reflexes, and absent sensations.
Electrodiagnostic studies identified the extent, type, and severity of these familial polyneuropathies, characterizing the taxonomy of CMT (ie, axonal vs demyelinating). Molecular genetic testing led to understanding both the natural history and the spectrum of CMT.
Various CMT classification schemes use the genotype (currently favored) or the pathology (ie, demyelinating neuropathies (CMT1), axonal (CMT2), and severe hereditary motor sensory neuropathy III, or Dejerine-Sottas disease (CMT3), which includes congenital hypomyelination syndromes and severe disability.) There are also overlaps with classification schemes used to create algorithms for genetic testing that are based on family history and inheritance (eg, autosomal-dominant, autosomal-recessive, and X-linked), Such algorithms are used to streamline diagnosis and reduce redundancy and cost associated with testing. Genes implicated in CMT I and II encode for peripheral myelin protein 22 (PMP22), myelin protein zero (MPZ), gap junction beta-1 protein (GJB1), and mitofusin-2(MFN2); in CMT3, mutations of early growth response factor 2 (EGR2) and periaxin (PRX) genes are found.
The most common form is CMT1, which is autosomal dominant and accounts for 75% to 80% of cases; X-linked CMT accounts for approximately 15% of all cases.
Testing for mutations in GJB1 detects 90% of CMT1X.
Mutations of GJB1, which encodes the protein connexin 32 (Cx32) that is expressed in Schwann cells and oligodendrocytes are the only known causes of CMT1X, a common cause of childhood-onset hereditary peripheral neuropathy.1 More than 400 mutations in GJB1 have been reported.1,2
This is a case of recurring acute encephalopathy syndrome with characteristic MRI abnormalities prior to the onset of classical manifestations and diagnosis of CMT1X.
Differential diagnosis of recurrent neurological deficits and encephalopathy includes cerebrovascular diseases (eg, strokes, vasculitis, hypertensive encephalopathy syndrome), metabolic disturbances, and inherited metabolic disorders. Most patients with CMT do not have any CNS abnormalities; clinically, CMT is a disease of the peripheral nervous system.
Patients with Charcot-Marie-Tooth disease occasionally have recurrent stroke-like events with abnormalities in brain imaging, often after infectious illnesses or metabolic stress.
Silent CNS involvement with abnormal brainstem-evoked responses and pyramidal tract signs have been described in CMT. The clinical episodes in the case described were occurred a few weeks after infectious and inflammatory illnesses. Acute-onset aphasia, dysarthria, hemiparesis, facial weakness, and ataxia are common manifestations4-8 that can last 3 to 4 days before almost complete resolution. Antecedent viral infections5 and other metabolic stressors (eg, hyperventilation7 and travel to high altitude9) have been previously reported.
Transient focal deficits and encephalopathy along with abnormal imaging results are a pathognomonic clinical presentation of CMT1X.6,11 However, as in our case, these findings can predate the diagnosis of CMT1X, especially if clinical findings of peripheral neuropathy are absent or there is no positive family history available.
Brain imaging findings during these events are also of considerable diagnostic importance. Restricted white-matter diffusion over the centrum semiovale, posterior corpus callosum, and sometimes cerebellar peduncles is noted with minimal findings in T2 and FLAIR imaging.3-8 Stroke-like events with diffusion abnormalities may be confused with cerebral ischemia.1,10 However, the diffusion abnormalities spare cortical U fibers, are bilateral and symmetrical, and are not restricted to specific cerebrovascular areas. Brain MRA is normal. The findings on brain MRI are reversible, although may persist for months. The extent, appearance, or resolution of imaging findings does not correlate well with clinical symptoms.
Diffusion-weighted MRI abnormalities are bilaterally symmetrical and not restricted to vascular territories.
The pathogenesis of brain MRI lesions is thought to result from intramyelin edema or discompaction of myelinated fibers secondary to abnormal gap junction protein. Characteristic, nonvascular territorial, bilaterally symmetric diffusion abnormalities on brain MRI associated with transient encephalopathy are pathognomonic of CMT1X. Patients with certain CNS phenotypes of CMT1X commonly present with this clinical picture.3
It is unknown whether acute treatment with steroids hastens symptom resolution. As the diffusion sequences became routine in brain MRI studies, these findings created diagnostic challenges for both neurologists and neuroradiologists.
Awareness of these unusual CNS manifestations and the imaging findings in CMT1X is important to avoid unnecessary investigations and treatment.
1. Kleopa KA. The role of gap junctions in Charcot-Marie-Tooth disease. J Neurosci. 2011;31(49):17753–17760.
2. Bird TD. Charcot-Marie-Tooth neuropathy X type 1. 2016. In: Adam MP, Ardinger HH, Pagon RA, et al., editors. GeneReviews [website]. Seattle (WA): University of Washington, Seattle; 1993-2018. https://www.ncbi.nlm.nih.gov/books/NBK1374/ Last accessed May 2, 2018.
3. Taylor R A, Simon EM, Marks HG, Scherer SS. The CNS phenotype of X-linked Charcot-Marie-Tooth disease: More than a peripheral problem. Neurology. 2003;61(11):1475-1478.
4. Fusco C, Frattini D, Pisani F, et al. Coexistent central and peripheral nervous system involvement in a Charcot-Marie-Tooth syndrome X-linked patient. J Child Neurol. 2010;25(6):759-763.
5. Schelhaas HJ, Van Engelen BG, Gabreëls-Festen AA, et al. Transient cerebral white matter lesions in a patient with connexin 32 missense mutation. Neurology. 2002;59(12):2007-2008.
6. Citton V, Burlina A, Baracchini C, et al. Apparent diffusion coefficient restriction in the white matter: going beyond acute brain territorial ischemia. Insights Imaging. 2012;3(2):155-164.
7. Srinivasan J, Leventer RJ, Kornberg AJ, Dahl HH, Ryan MM. Central nervous system signs in X-linked Charcot-Marie-Tooth disease after hyperventilation. Pediatr Neurol. 2008;38(4):293–295
8. Siskind C, Feely SM, Bernes S, Shy ME, Garbern JY. Persistent CNS dysfunction in a boy with CMT1X. J Neurol Sci. 2009;279(1-2):109-113.
9. Paulson HL, Garbern JY, Hoban TF, et al. Transient central nervous system white matter abnormality in X-linked Charcot-Marie-Tooth disease. Ann Neurol. 2002;52:429-434.
10. Basu A, Horvath R, Esisi B, Birchall D, Chinnery PF. Recurrent stroke-like episodes in X-linked Charcot-Marie-Tooth disease. Neurology. 2011;77(12):1205-1206.
11. Hanemann CO, Bergmann C, Senderek J, Zerres K, Sperfeld A. Transient, recurrent, white matter lesions in X-linked Charcot-Marie-Tooth disease with novel connexin 32 mutation. Arch Neurol. 2003;60:605-609.
Acknowledgements: The author thanks Oleg Bronov MD, Neuroradiologist for providing relevant neuroimaging studies.
Arayamparambil C. Anilkumar, MD
Associate Professor
Department of Child Health
Director, Division of Pediatric Neurology
University of Missouri School of Medicine
Columbia, MO


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By Gary Murphy
With 12 role premieres under his belt, baritone Rod Gilfry is flying high these days—both literally and figuratively—with a career that spans almost four decades. Even with that longevity, Rod is no old hat. The New York Times recently stated that Rod has become "the singer of choice for new [italics added] American operas."
After reprising his role as Mr. Potter in Jake Heggie's new opera adaptation of It's A Wonderful Life at San Francisco Opera in December, Rod returns to Los Angeles for yet another role premiere in the loser, an intense tour-de-force and daringly staged one-act opera from Pulitzer Prize-winning composer David Lang. Based on the novel by Austrian writer Thomas Bernhard, the loser tells the tale of a failed piano student who recounts a life lived in the shadows of his famous friend Glenn Gould. This painful meditation on dreams forsaken and hopes unrealized unfolds in an unusually intimate staging that incorporates multiple levels of the spectacular Theatre at Ace Hotel in Downtown L.A., February 22 and 23, 2019.
Rod sat down with the Opera League to talk about the West Coast premiere of the loser, an intimate work for baritone, piano and chamber ensemble, plus a few of his LA Opera memories.
BRAVO: David Lang's the loser seems an intriguing role choice for you. Is it really a 65-minute sung monologue performed on a platform built above the orchestra?
Rod Gilfry: That's exactly what it is. It is just me standing on a 4' x 4' platform that's perched 20 feet in the air with no chairs, no water and no place to sit. I'm simply standing there dressed in a tuxedo. It's both intense and challenging for me, no doubt. The material doesn't seem a likely candidate for an opera or a dramatic setting, but composer David Lang finds these odd vehicles and makes great theatre from them. Take anatomy theater for example. He turned human dissection into an opera. He saw something in Thomas Bernhard's novel, also entitled the loser, and thought it would make a good opera piece.
BRAVO: You play the character of the Narrator who is one of two piano students who were in school at the same time as Glenn Gould. Is that correct to say?
RG: Yes, there are three characters in the book—Glenn Gould, who has just died, and there is Wertheimer, who has just killed himself. The survivor of the trio is the Narrator who never reveals his name. It's interesting how the book is written in these massively long paragraphs, each one its own chapter. That's a style of Thomas Bernhard, it's one of his literary idiosyncrasies.
BRAVO: I would imagine the tension must be high for the audience as they watch you standing on a small raised platform above the stage.
RG: It's a fascinating piece, and many people have told me how captivated they are in the theatre. You have to understand something else about the way it is envisioned. The platform I stand on is built above the orchestra section of the house which is left empty—no one sits there. Everyone sits in the mezzanine section, and I am eye to eye with the audience while the bare mainstage sits behind me.
It's only in the last five minutes of my monologue that a light comes up onstage revealing a beautiful grand concert piano and a pianist lightly playing some sort of vague impression of a Bach piece. Maybe it's Bach, perhaps a bit of the "Goldberg Variations" which is mentioned several times throughout the piece. David has written it as a sort of very loose and lovely, somewhat mysterious interpretation of a Bach composition.
BRAVO: You just wrapped It's A Wonderful Life in San Francisco where you reprised the role of Mr. Potter that you originated at Houston Grand Opera. You seem to enjoy creating new roles and recently did so in Crossing here at LA Opera. Is it harder to create new roles versus finding your character in well-known roles?
RG: It's a totally different process. One of the things about doing a new role is that it's a completely blank slate. You can do what you want and figure out your own way through it, and then you're the original one that everyone else goes from and you're the point of departure.
Whereas if you do a familiar role, then you must honor tradition whilst somehow making it distinctively yours. Though I have to say there is not much latitude in any classical vocal music. By the time the composer has set the text, about 95% of your choices have been decided by the composer in terms of speed, rise and fall of the line, where you pause, the dynamic. All those elements are pre-determined by the composer so the leeway you have for interpreting is only about 5% as opposed to an actor where you can essentially be the composer.
BRAVO: You've performed at LA Opera many times from The Merry Widow to Nicholas and Alexandra, and, most notably, the title role in Billy Budd. When did you first appear onstage for LA Opera?
RG: The first role I did was in Otello, the 1986 inaugural production that began LA Opera. I played the role of the Herald, Araldo, who had a single line to sing in the opera. It's the opening of the third act, and I step out onstage and sing one line—"La vedetta del porto ha segnalato la veneta galea che a Cipro adduce gli ambasciatori." And Plácido Domingo as Otello sang back to me, "Bene sta." It was short but a great moment in my life.
I have a cabaret show where I talk about how I got started and mention LAO's inaugural season and how I had this fantastic role Araldo and had a beautiful aria. I'm setting up the scene for my audience, describing the whole story. My pianist plays the introduction, and I come back onstage steeling myself to sing this beautiful aria. The audience laughs, but I say that I sing that line to Plácido Domingo. Well, one night I was doing my show at the opera house in Barcelona where Plácido happened to be singing, so he came to my show. This time, when I got to my one line, Plácido stood up in the audience and loudly sang Otello's response: "Bene sta!" It was definitely the most affirming moment of my career!
BRAVO: I'm sure the Opera League has become a friend of yours over these many years. Is there one Opera League moment that stands out?
RG: Most certainly. The one thing I totally remember was in 2000 when I was performing Billy Budd, a role I had been singing all over the world. It was the last opera of Peter Hemmings' last season, and it always had been his dream to have Billy Budd in Los Angeles. It was the Opera League that stood up and guaranteed they would find enough funding to ensure the Billy Budd production. As it turned out, it was not only Peter's last production at LA Opera, it was also the last time I performed Billy. It was all so poignant.
BRAVO: Are you still teaching at the University of Southern California's Thornton School of Music?
RG: Yes, it's my 10th anniversary as a voice professor at USC. This semester I'm only teaching about five weeks! I am very lucky to be allowed to blend my performing career with my teaching career. I love working with students to help them discover their voices and coaching them with their roles, especially if it is a role I've sung. At this point in my life and my career, I find great passion in teaching, as I have so much to share. If there is one important lesson that I want to inspire in my students, it is the need to communicate, whether in the opera repertory or in art song, they must communicate from the stage with authenticity, proper diction and vocal color. I say to them, "If I can't understand your words, you are no longer telling me the story. You're just making pretty sounds." Clear communication and authenticity is key.
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|The Mothman Prophecies - RETROSPECTIVE
You might have heard about all the Mothman type sightings in Chicago lately, something like 30 in the last 3 years all over the city.
I'm as skeptical as they get on some things, but this mystery is close to my heart, I guess. Is this a shared psychosis? Do we really know that there aren't entities just beyond what we perceive? I thought I might go back to the movie again today, and I was really astonished at how good it was. It stars Richard Gere, Laura Linney, Deborah Messing, and Will Patton. Gere has that acting style that only Richard Gere can do, but his portrayal as an obsessed person was better than usual for him. Laura Linney was great at playing the voice of reason - even when there was none to be made. Messing had a small roll as Gere's wife - who dies right in the beginning after seeing a Mothman.
I've got to say the best acting in the movie was Patton as Gordon - who was being constantly visited and tormented. Talk about a character of neurosis - he pulled that one off big time.
The story stayed pretty close to the original reportings though 40 years later ... which kept it interesting and the musical score was bordering on very tense yet experimental. Mark Pellington directed it. He also did Arlington Road - top notch movie, Jerry Maguire and Almost Famous - along with a Pearl Jam movie and U23D. It seems he likes to mix it up a little bit. Maybe I'll even watch Jerry Maguire next - I never saw that stinker of a movie.
Definitely check out the movie - the myth, the legend. Positivity and love to all my peeps in Chicago - Rahm is one disaster too many!


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Hello Foodies,
Here is my winter wonder ladoo recipe, no sugar, no jaggery added. This is the season to
Here is my winter wonder ladoo recipe, no sugar, no jaggery added. This is the season to
The foundation of a healthful diet is whole grains, fruits, nuts, vegetables, and seeds. The fat contained in nuts and seeds is mostly monounsaturated fat, a form of fat now generally thought to be better for health than saturated fats. Dates are incredibly versatile and make a delicious dessert. They are sticky, which makes them useful binder in many recipes like, energy bars, smoothies, and cookies.
Why dates?
Dates are naturally sweet and are an obvious choice for sugar-free preparations. Dates are a healthy substitute for white sugar in dessert because of their sweet taste, nutrition, antioxidants.
Why Flax Seeds are good for winter?
Flax seeds are the richest source of plant-based omega-3 fatty acids. It is an excellent alternative to omega-3 fats in fish for people with a seafood allergy or people those are vegan or vegetarians and people who sensitive to gluten.
Why Sesame seeds?
Sesame seeds are one of the popular winter food and are used in many Indian recipes. It is an excellent source of zinc. Our body needs zinc for proper growth and development. Zinc plays a role in the manufacturing of new proteins and blood, and it helps to protect your body's immune system.
Why Poppy seeds?
In Indian cuisine, Poppy seeds are added for thickness, texture and to add the aroma to the recipes. It is a rich source of dietary fiber, which helps to prevent constipation. Also an excellent source of zinc which helps to boost bone health.
Why Almonds?
Almonds are the best source of vitamin E. They are low in carbs and high in fiber, healthy fats, magnesium, and protein. These nuts are the healthiest foods you can eat.
Why ghee?
Ghee is a staple of Indian cuisine and Ayurvedic medicine. Ghee contains vitamin E, the most powerful antioxidants. Ghee works an excellent fat burner besides providing lubrication to joints and keeps skin soft.
Preparation Time: 5 Minutes; Cooking Time: 10 Minutes.
Each Ladoo contains 100 calories.
YouTube Video :
- Flaxseeds ¼ Cup
- Sesame seeds ¼ Cup
- Poppy seeds ¼ Cup
- Almonds ¼ Cup
- Dates ½ Cup (75 g)(seedless)
- Ghee 2 Tsp
- Grind dates and keep aside.
- Dry roast flax seeds, sesame
- Grind dry roasted flaxseeds, sesame seeds, poppy seeds, and almonds to make a powder(save 1 Tbsp of Poppy seeds to roll ladoos).
- Heat ghee in a pan and add grounded dates and saute for a minute or 2.
- Now add grinded seeds and almond powder and saute and cook for 2-3 minutes.
- Turn off the flame and let the mixture cool.
- Take a handful portion of prepared mixture and roll to make a ladoos.
- Roll prepared ladoos into dry roasted poppy seeds.
- Tadaa, nutritious, crunchy and sweet winter wonder ladoos are ready. Enjoy!!!
My Take:
- To make vegan version: you can use coconut oil or vegan butter instead of ghee.
- Once ladoos prepared you can roll them into sesame seeds or crushed dry nuts instead of poppy seeds.
- If you need it sweeter, you can increase the quantity of dates according to your taste.
- You can add dry nuts of your choice.
Dietary Comments
- It makes 10 servings. And based on a 2000 calorie diet, per serving contains 100 calories, along with 9 g carbohydrates, 3 g dietary fiber, 6.94 g fats, and 3 g protein.
Health Benefits of Winter Ladoos:
- Dates, Poppy seeds, Sesame seeds, Flaxseeds are a great source of iron.
- Iron is one of mineral that forms part of the hemoglobin of red blood cells and helps carry oxygen to body's cells and being part of myoglobin that provides oxygen to the muscles in your body. When your iron stores are low, you can't get enough oxygen and form of anemia results, and you may feel tired.
- Omega-3 fatty acids - Flax seeds are the most abundant source of plant-based omega-3 fatty acids.
- Weight loss - flax seeds are full of healthy fats and fiber, it will help you to feel satisfied longer so you will eat fewer calories overall which may lead to weight loss.
- For vegan or vegetarians - flax seeds may also be an excellent alternative to omega-3 fats in fish for people with a seafood allergy or people those are vegan or vegetarians.
- Gluten sensitivity - Using flax is a great way to naturally replace gluten-containing grains. So, flax seeds are great for those who have Celiac disease or have a gluten-sensitivity.
- Digestion - Flax is very high in soluble and insoluble fiber which can also improve digestive health, and it is beneficial to eat flax to relieve constipation naturally.
- Flaxseeds are a good source of essential fats and b-vitamins which can help reduce dryness and flakiness skin and scalp.
- Sesame seeds have properties of fighting, preventing, and reversing illness and disease.
- Sesame is the best option for high protein in a vegetarian diet.
- The high content of zinc which helps to boost bone mineral density and bone health as a whole.
- Dates may promote and ease natural labor for pregnant women when consumed during the last few weeks of pregnancy.
- Dates contain several minerals like phosphorus, magnesium, calcium, and potassium and are beneficial for bone health.
Eat Healthy, Stay Healthy!!!


text: Said Tahseen was born in Damascus in 1904, and died in 1985. He learned art through self-teaching, and contributed to the establishment of the Arab Society of Fine Arts in Syria, where he was elected chairman. He worked as an art teacher and was awarded the National Syrian Garter. Tahseen participated in the majority of the constitutive exhibitions of the Fine Arts Association and the shows organised by the National Museum in Damascus. He is regarded as one of the pioneers of the art movement in Syria. His artworks depict historical characters and events in addition to scenes from Damascene life, focusing on social gatherings and traditional architecture. His works are influenced by impressionism and realism, but he also addressed existential issues including symbolic figures and colours.


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QNAP announced its first portable NAS and a Braswell version of one of its popular product lines.
Thecus is trialing a new version of its NAS OS.
Updated - Synology's DS216 delivers surprisingly high performance for a Marvell-powered NAS.
ASUSTOR's AS1002T and AS1004T are good values in two and four-bay NASes.
QNAP new TS-x53A NASes sport Intel Braswell CPUs.
Thecus' N7770-10G provides a good combination of capacity and performance in a 10GbE NAS.
Synology's latest two-bay NAS is powered by a dual-core Marvell CPU.
WD's My Cloud Mirror Gen 2 offers a good blend of performance, features and value for the typical SOHO user.
The QNAP TS-563 is a good value in a 10GbE capable NAS.
Updated - Our first look at the performance of NETGEAR's RAX80 and ASUS' RT-AX88U shows little benefit functioning as AC routers.
Updated: The first draft 11ax routers are almost here. Take a little time to know what you might be buying into.
Updated - 160 MHz channel bandwidth is an essential feature of 802.11ax. We take a look at whether it means trouble for your 11ac network.
Ever wonder what happens behind the scenes when Wi-Fi devices roam, or more likely don't? We'll show you why the "seamless" roaming Wi-Fi gear makers promise is still as elusive as a Yeti.


text:
The Board values the contributions of local building
officials and others who work together to ensure the safety of Mississippi's
buildings and spaces. Anyone with questions or concerns regarding architectural, interior design or landscape architectural requirements is invited to contact the Board
office by phone (601-856-6760) or email (firstname.lastname@example.com).
Building Permit and Construction Documents Requirements
Building Officials Guide to Architecture & Engineering
Building Officials Guide to Landscape Architecture Requirements
Construction Administration Notification Form
Institute for Business and Home Safety
International Code Council (ICC) (IBC)
Mississippi Insurance Department/State Fire Marshal
Mississippi Fire Prevention Code (applies in areas without a more stringent code such as IBC)
Construction Management Services


text:
NEW YORK -- Flyers goalie Michal Neuvirth was released from Pennsylvania Hospital Sunday afternoon and is at home resting after collapsing Saturday night.
All tests on Neuvirth came back "normal," according to Flyers general manager Ron Hextall, and it is believed Neuvirth was suffering after-effects from a severe upper respiratory infection he's been fighting for more than a week.
Neuvirth suddenly collapsed in his crease at the 13:24 mark of Saturday's opening period vs. New Jersey. He laid prone on the ice for several minutes as he was attended to by medical personnel from both the Flyers and Devils. Neuvirth eventually sat up and was stretchered off the ice.
Hextall said the Flyers' medical team will reevaluate Neuvirth on Monday, which is an off day for the Flyers before they visit New Jersey on Tuesday.
Neuvirth was replaced in net Saturday by Anthony Stolarz, who finished off the Flyers' 3-0 win. Ironically, Neuvirth gets credit for the shutout because the Flyers were leading 1-0 on a Brayden Schenn power-play goal at the time Neuvirth's episode began.
Backup Steve Mason was also ill and did not dress. Mason felt well enough to join the team in New York on Sunday, but he likely won't play against the Rangers (see injury update).
All signs point to Stolarz starting Sunday at Madison Square Garden.


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Female • 6 weeks
Puppy ID #658161
DOB September 4, 2020
Available October 30, 2020
Color Black & Rust
Mom's Weight 75 - 80 lbs
Dad's Weight 85 - 90 lbs
Registry AKC
1/4 steps complete
Bonded with Mom
Old Enough
Weighs Enough
The Doberman is a large, fearless dog that is well-known for its historically common job as a guard dog. Originating in Germany, the Doberman Pinscher is highly intelligent and loyal, and is well suited for police work, tracking, and competitive obedience. At home, these dogs are sweet, affectionate, and thrive on human companionship. Dobermans are usually excellent with children and other pets, and are consistently ranked among the AKC's most popular dog breeds. Read More
We do all of the 'ruff' work - screening and vetting breeders, performing health checks and coordinating travel so you can focus on what really matters: welcoming home your new furry family member! Learn more
PuppySpot will help find the right puppy for you. Search by breed or take our Breed Match Quiz to find the perfect furry friend.
Connect with your very own Puppy Concierge, who will help you find your new best friend!
A friendly Puppy Manager will help get your pup home safely! Take a peek at our pup-friendly travel options.
Congrats on your new furry family member! Don't forget to share your Wet Nose Moments on social media using #PuppySpot.
Loreen L.
Doberman Pinscher
Excellent people to work with. Our puppy camp to us happy and healthy and the breeder is so helpful.
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Doberman Pinscher
Even though this Covid 19 hit us hard the Puppy Spot still found a way to get us our puppy. Andrea in Hollywood, Fl made it happen. Would love our new puppy so much. He's such a a healthy and happy puppy.
joseph d.
Doberman Pinscher
puppyspot helped me find my new best friend and I am thankful for that and the service was great


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Here's why you should spend your tax refund on a new air conditioner
It's April. It's the time of year where baseball starts, the weather warms up, and taxes are due. Okay, that last item is less exciting than the others. However, if you're like most Americans, you're probably anticipating a tax refund; the average in Louisiana is $3,073. Exciting!
Many people use their refund to pay off debt, go on vacation, or buy boats / cars. However, in this blog post, we'll argue the reasons why you should re-invest your refund in your home's value by upgrading an old air conditioner.
If you're ready to make the switch from your old system to a new one, contact Southern Air for a free in-home estimate.
#1. Replacing your old air conditioner can benefit your home's value
If you're thinking at all about selling your home in the next decade, replacing that old air conditioner with a new one using your tax refund makes sense. A new air conditioner will increase your home's value, improve your curb appeal, and even be a deciding factor for many homebuyers.
Why is an air conditioner so impactful? When you're buying a home, there are a lot of upfront costs to consider, from closing costs to the downpayment itself. An older air conditioner on the verge of dying is a big turnoff for buyers, because they know they run the risk of having to replace the system themselves at a time when they're lowest on cash.
As the seller, you can just have Southern Air install a new air conditioner for the home and then up your home's value.
#2. You can feel the better comfort
There are a lot of luxury items you can spend your tax refund on. However, will any of them make you feel as comfortable as a new air conditioner will on the hottest, most humid nights of the summer?
Whether you're planning on selling your home or not, you and your family should still feel comfortable in your home. Consider using your refund to upgrade to a new Carrier air conditioner, installed by the Southern Air team.
#3. Cut down on miscellaneous costs
An older air conditioner is more likely to cost you miscellaneous money on two fronts:
- Higher energy bills: Even with seasonal maintenance, an older air conditioner just isn't as energy-efficient as a new system. This means you're paying more for summers to come.
- More frequent repairs: Older air conditioners are more likely to break down than new systems, which means you'll need AC repair more often. Over successive summers, these costs can really add up.
Call Southern Air for a free in-home estimate
Southern Air offers free in-home estimates on new air conditioners. If you're considering using this year's tax refund on a new air conditioner, give us a call at (318) 936-9677.


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| 8.6°C Belfast
Around 50 jobs are to go in Northern Ireland following the collapse of menswear retailer Austin Reed.
The company currently has a Viyella and Country Casuals store in Belfast city centre, and an Austin Reed outlet shop in Junction One outside Antrim.
Across the UK, Austin Reed will close 120 stores after administrators to the collapsed menswear retailer failed to find a buyer for the entire business, resulting in the loss of approximately 1,000 jobs.
Edinburgh Woollen Mill, headed by Philip Day, has acquired the 116-year-old chain's brand and five concessions, but did not want to take on the entire store estate.
Administrator AlixPartners said "no viable offers" for the rest of the business could be found.
Peter Saville of AlixPartners said: "We have explored all options to sell the business since our appointment and continued to trade the business with the support of the secured creditors in what is clearly an extremely challenging retail environment.
"Despite a significant number of interested parties coming forward during this period, it became clear as the process progressed that a viable solution which kept the business whole was not forthcoming. As a result we have made the difficult decision to cease trading the business and commence a wind-down of the estate."
The 120 stores will now be sold off to other retailers.
Austin Reed fell into administration in April and the news comes amid a torrid time for the high street, with the fate of department store chain BHS set to be revealed later this week.
A number of bidders were mooted to be interested in Austin Reed after its owner, the distressed retail specialist Alteri Investors, threw in the towel last month. They included Mike Ashley's Sports Direct, but a suitable offer did not materialise.
It was founded in 1900 as a tailoring firm and once counted Winston Churchill and Elizabeth Taylor as customers. But retail experts have bemoaned the firm's failure to adapt to a multi-channel environment.
Belfast Telegraph


text: A repeatable field allows an author to create lists of values of the same field type in an entry. Once this option is enabled for a field, multiple items can be added, removed and ordered in the repeated list. Make a field repeatable Supported fields Examples A list of names Perhaps you want a list of names of research paper contributors that exist outside of your organisation. Setting a text field to be repeatable allows you to enter multiple names. Opening hours To create a list of opening hours, you could set up an opening hours component containing days of the week and two fields for the from and to time. You could then set this component to be repeatable so your authors can easily enter a set of opening hours unique to your business. Feature item If you need to highlight an aspect of your product or service, you could create a feature component that could be made repeatable, allowing you to add multiple items.


text:
nursery Schools within 2 miles of PE25 2QT
We have found 1 match as a result of your search for nursery Schools within 2 miles (or 3.22Km ) of the centre of PE25 2QT. Please note that the distances shown below are "as the crow flies" from the entered postcode (PE25 2QT) and do not take into account road layouts or any obstructions or detours needed.
There is a Google Map at the bottom of this page showing the location of all the schools in the area surrounding PE25 2QT.
Approx 0 miles away : Skegness Neighbourhood Nursery
|Brunswick Drive
|Tel: 01754 766440
|Ofsted Report Page
|Street Map
|This is a nursery school
If you know of any of the details shown above that are incorrect (such as a change of Head Teacher) please contact us using the link at the bottom of this page. Thank you.
We have found a total of 1 nursery schools in and near PE25 2QT (including the entries listed above).
|Key to map below: -
|: Pre School
|: Nursery
|: Primary School
|: Secondary School
|: Colleges, 16 plus
|: Other types of schools
You can click on any of the markers shown on the map for more details and you can also drag the map around, zoom in or out, and change to a satellite view if you wish.


text:
Want to bring your group to Australia?
We craft fantastic tours to Australia for international groups.
Australian history, our natural wonders and landmarks, Aboriginal and Torres Strait Islander culture, performing arts and sporting events are just some of the many themes we cover.
Here are some ideas.
Check back soon for more info :)


text:
At its September 12th meeting, The Windham Town Council enacted a "Moratorium Ordinance on Development within the Highland Lake Watershed." The Moratorium will halt any new development in our watershed that has not received final approval for an initial period of 180 days, with extensions available as long as we do our part to implement best management practices. The Moratorium is in direct response to the serious concerns related to the deteriorating water quality in Highland Lake.
The Moratorium is the result of an intense three months of collaborative effort by Highland Lake Association, Highland Lake watershed residents and the towns of Windham and Falmouth in response to the alarming recurrence of a picocyanobacteria bloom for a fourth season in Highland Lake. The community has determined that a moratorium is necessary to provide the opportunity for the towns to review the town's current code of ordinances and zoning regulations to determine appropriate modifications or updates that will reduce the environmental impacts of development within the Highland Lake watershed.
Highland Lake residents responded enthusiastically to this announcement, and also expressed a commitment to renewed efforts within the watershed to implement best management practices that include: regular maintenance and upgrading of private roads, installing and improving buffers on shoreline properties, regular maintenance to septic systems, and when necessary to upgrade outdated systems. It should be noted that all these improvements and ongoing maintenance would be permitted under the Moratorium regulations.
In addition, a copy of the Moratorium is available below.
Highland Lake Association President Rosie Hartzler presented a list of action items that the HLA will focus on during the upcoming year. For more information, see the post "Action Items for 2017 – 18"


text:
Fish by Liam Francis Walsh (InfoSoup)
A boy and his dog head out onto the lake to fish one morning. Both boy and dog have their own fishing poles. They first catch the letter F. Then the letter I. The letter S is next. But beware the huge letter C that is circling the boat. When they hook a Q, it is thrown back into the water. Soon though they are caught in a whirlpool of letters, swept underwater among schools of them zigging and zagging. When the boy makes it back to the boat, he has the H under his arm, but loses it as the huge letter C reappears. Not to worry, his dog has saved the day with the H to complete FISH. But was that what they were trying to catch?
This wordless picture book depends on its wonderful illustrations to carry the story. And do they ever! Done with a limited color palette of pale blue and bright red, they shine on the page. Each character also shines with personality and energy. The ending of the book is very satisfying, especially since all readers will think that the goal was to catch FISH when actually it was to do something entirely different. It's a great twist that is filled with jolly cheer.
A standout wordless picture book that illustrates how letters form words in the most energetic and playful of ways. Appropriate for ages 2-4.
Reviewed from library copy.


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Borla Camaro Long Tube Headers - V8 SS
Borla exhausts feature patented, straight-through and multi-core technology to unleash hidden horsepower. Increased exhaust velocity adds power, driving excitement, fuel economy and the distinctive BORLA Sound of Power respected by motoring enthusiasts everywhere. Each system is built from premium austenitic stainless steel, superior to T-400 series knockoffs, to give you the absolute best in performance and durability. Ultra-smooth mandrel bends ensure maximum flow and power, and precision computer-controlled CNC manufacturing ensures an accurate fit. Best of all, BORLA stands behind every system with a Million-Mile Warranty. Just what you'd expect from the world's most experienced (and most winning) exhaust brand.
|Vehicle Fitment
2014 Chevy Camaro SS
2013 Chevy Camaro SS
2012 Chevy Camaro SS
2011 Chevy Camaro SS
2010 Chevy Camaro SS
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