 They included pleomorphic adenoma, myoepithelioma, myxoid neurofibroma, neurothekeoma (nerve sheath myxoma), chondroid choristoma, extraskeletal myxoid chondrosarcoma, focal oral mucinosis, and an ossifying fibromyxoid tumor of soft parts.Exceedingly rare, this tumor develops in a wide age range, although often in young patients without a sex predilection.The vast majority develop within the anterior dorsal tongue, with palate and base of tongue rarely affected.