<prompt> Plasma tyrosine level in Richner-Hanhart syndrome is:1-2 mgdL2-3 mgdL4-5 mgdL8-10 mgdL  <response>: Ans. C. 4-5 mgdLTyrosinemia Type II is due to the lack of hepatic transaminase. It is also called Richner -Hanhart syndrome. During this Plasma tyrosine level is elevated 4 to 5 mgdl. Clinical features include mental retardation, skin lesions, infants may exhibit self-mutilation and disturbances in fine co-ordination. 