<prompt> Which enzyme deficiency causes tyrosinemia type 1?Fumaryl acetoacetate hydrolaseTyrosine transaminaseHGA oxidaseTyrosinase  <response>: Fumarylacetoacetate is then hydrolyzed to fumarate and acetoacetate by a hydrolase step 6, Fig.17.2. This results in the production of a glucogenic product fumarate and a ketone body acetoacetate. Hence phenylalanine and tyrosine are paly glucogenic and paly ketogenic. Impoant Specialized Products from TyrosineRef: DM Vasudevan - Textbook of Biochemistry, 6th edition, page no: 204 