<prompt> Cells cultured from patients with this disorder exhibit low activity for the nucleotide excision repair process. This autosomal recessive genetic disease includes marked sensitivity to sunlight Ultra voilet light with subsequent formation of multiple skin cancers and premature death, the disorder is:Acute intermittent PorphyriaAlkaptonuriaXeroderma PigmentosaAtaxia - Telangiectasa  <response>: C i.e. Xeroderma pigmentosa Xeroderma pigmentosa is an autosomal recessive genodermal disease in which DNA repair is defective dt defective NER nucleotide excision repair pathwayQ. This results in marked hypersensitivity to ultraviolet sun light, photosensitivity, dry pigmented skin, increased risk of skin malignancy and premature deathQ. 