<prompt> All the following Lipidoses are inherited as Autosomal Recessive ExceptFabryKrabbeGaucherTaysachs  <response>: FABRY DISEASE This disease is an X-linked inborn error of glycosphingolipid metabolism caused by the absent or markedly deficient activity of a-galactosidase A a-gal A.Reference: Nelson Textbook of Paediatrics; 20th edition; Chapter 86; Defects in Metabolism of Lipids 