<prompt> True about incontinenta pigmenti include the following exceptX-linked dominantPrimary skin abnormalityAvascularity of peripheral retinaOcular involvement is seen in almost 100 cases and is typically unilateral  <response>: Ocular involvement occurs in 20-35 of cases. Involvement is assynzetrical. The two pathognomic changes are -Retinal pigmentary changes with mottled diffuse hypopigmentation.Abnormal peripheral retinal vessels with areas of non perfusion a vascularity. 