<prompt> An infant has hepatosplenomegaly, hypoglycemia, hyperlipidemia, acidosis and normal structured glycogen deposition in liver. What is the diagnosis?Hers diseaseVon Gierkes diseaseCoris diseaseAndersons disease  <response>: b. Von Gierkes diseaseRef: Nelsons 20e p 715-725, Ghai 8e p 655-657Hepatorenomegaly, hypoglycemia, hyperlipidemia, acidosis and normal structured glycogen deposition in liver is suggestive of Von Gierkes disease; Normal structured glycogen excludes options c. Coris and d. Andersons disease. 