<prompt> Giucose-6-phosphatase is absent or deficient in:Von Gierkes diseasePompes diseaseCoris diseaseMcArdles disease  <response>: Ans. A. Von Gierkes diseaseGlycogen Storage Diseases GSDs are caused due to deficiency of certain enzymes:TypeName of the diseaseEnzyme deficientClinical FeaturesType IVon Gierkes diseaseGlucose-6-PhosphataseHypoglycemia, Ketosis, Hyperuricemia, HepatomegalyType IIPompes diseaseLysosomal a-1,4 1,6 glucosidaseAccumulation of glycogen in lysosomes, heart failureType IIICoris diseaseDebranching enzymeAccumulation of branched polysaccharideType IVAndersens diseaseBranching enzymeHypoglycemia, Hepatic failure, Liver Cirrhosis, AscitesType VMe. Ardles diseaseMuscle phosphorylaseMuscle cramps on exercise, Pain in muscle, weakness and stiffness of muscle.Type VIHers diseaseLiver phosphorylaseHypoglycemia, High glycogen content in liver.Type VIITaruis diseasePhosphofructokinase in RBC MuscleAs in type VType VIIIHepatic phosphorylase kinase deficiencyLiver phosphorylase kinaseAs in Type VI 