<prompt> True statement about Puetz Jegher syndrome isAutosomal recessive inheritenceIleum is the most common siteCaused by gain of function mutation of STK 11Increased risk of sex cord tumors  <response>: Puetz Jegher syndromeAutosomal dominant inheritence.Jejunum is the most common site.Caused by loss of function of STK 11.Increased risk of sex cord tumours, small intestinal, pancreatic, breast, lung and ovarian cancer. 