<prompt> Earliest presentation of Friedrichs ataxia is?AtaxiaSeizuresOptic atrophyStuttering  <response>: Answer is A Ataxia: In most patients ataxia of gait and stance is the first manifestation of the disease.- Clinical Neurology by Goetz 2d742 Friedreichs ataxia presents with progressive staggering gait, frequent falling and titubation- Harrison Note: The first pathological changes in Friendreichs Ataxia are thought to occur is dorsal root ganglia with loss of large sensory neurons. 