<prompt> Cells cultured from patients with this disorder exhibit low activity for the nucleotide excision repair process. This autosomal recessive genetic disease includes marked sensitivity to sunlight Ultra voilet light with subsequent formation of multiple skin cancers and premature death, the disorder isAcute intermittent porphyriaAlkaptonuriaXeroderma pigmentosaAtaxia - Telangiectasa  <response>: This patient has -Defect in nucleotide excision repair Increased sensitivity to sunlight photosensitivityIncreased susceptibility to skin cancerPremature deathAll suggests the diagnosis of Xeroderma pigmentosa. 