<prompt> Amino acid metabolism is implicated in which disease?Maple syrup urine diseaseReyes syndromeVon Gierkes diseaseMcArdles diseases  <response>: OPTION 1: Maple syrup urine disease - It is inborn error of metabolism of branched chain amino acids Von Gierkes disease and McArdles diseases are glycogen storage diseases. Reyes syndrome is an acute self - limiting metabolic insult resulting in generalized mitochondrial dysfunction due to inhibition of fatty acid oxidation. 