<prompt> Bernard Soulier syndrome is due to defect inGP IBIXGP IIBIIIaFibrinogenvWF  <response>: Bernard-Soulier syndrome BSS, is a rare autosomal recessive bleeding disorder that causes a deficiency of glycoprotein IbGpIb, the receptor for von Willebrand factor Causes Mutations in GP1BA, GP1BB and GP9 Diagnostic method Flow cytometry analysis Treatment Platelet transfusion 