<prompt> True about incontinenta pigmenti includes the following except:X-linked dominantPrimary skin abnormalityAvascularity of peripheral retinaOcular involvement is seen in almost 100 cases and is typically unilateral  <response>: INCONTINENTIA PIGMENTI X-linked dominant neurocutaneous syndrome with cutaneous, neurologic, ophthalmologic, and dental manifestations. Skin features occur in 4 stages Stage 1 vesicular Stage 2 verrucous Stage 3 hyperpigmented Stage 4 atrophichypopigmented Ophthalmologic findings Ophthalmologic findings occur in 20-35 of patients, and asymmetric involvement is common. Retinal vaso-occlusive events with resultant ischemia is primary mechanism in ocular pathology Treatment: Family counselling may prevent occurrence of new cases Skin lesions subside in adulthood spontaneously 