<prompt> Congenital hepatic fibrosis is predominantly associated with which cystic disease of kidney?Autosomal dominant polycystic kidney disease ADPKDAutosomal recessive polycystic kidney disease ARPKDMedullary sponge kidneyNephronophthisis  <response>: In Autosomal recessive polycystic kidney disease ARPKD, patients who survive infancy may develop a peculiar hepatic injury characterized by:- Bland peripoal fibrosis Proliferation of well differentiated biliary ductules, now termed as congenital hepatic fibrosis. 