<prompt> Which one of the following diseases is an autosomal dominant disorderHemochromatosisPhenylketonuriaMaturity onset diabetes of the youngGlucose-6 phosphate dehydrogenase deficiency  <response>: Maturity-onset diabetes of the young MODY is a heterogeneous single gene disorder characterized by non-insulin-dependent diabetes, an early onset and autosomal dominant inheritance.Approximately 15-20 of families fitting MODY criteria do not have mutations in any of the known genes Ref Robbins 9e pg 155 