<prompt> What is not given in fructose intolerance patient:GlucoseGalactoseFructoseMaltose  <response>: Ans. c FructoseRef: Harpers Biochemistry, 30 edn. pg. 205th Hereditary fructose intolerance HFI is an inborn error of fructose metabolism caused by a deficiency of the enzyme aldolase-B. In the deficiency of Aldolase B enzyme, if fructose is ingested, it will lead to an accumulation of fructose-1- phosphate. This accumulation has downstream effects on gluconeogenesis and regeneration of ATP. Symptoms of HFI include: Vomiting, hypoglycemia, jaundice, hemorrhage, hepatomegaly, hyperuricemia and potentially kidney failure. The key identifying feature of HFI: Appearance of symptoms with the introduction of fructose to the diet. Sucrose, sorbitol should also be restricted in diet. 