<prompt> In which syndrome is sensorineural hearing loss associated with abnormality of thyroxin synthesis?AlportPendredKlippel-FeilUsher  <response>: In Pendred syndrome child is born deaf. Thyroid enlargement appear in adolescence and becomes nodular in adulthood.Alports syndrome: Progressive glomerulonephritis.Klippel-Feil syndrome: Congenital spinal deformities.Usher syndrome: Retinitis pigmentosa. 