<prompt> Branching enzyme deficiency is seen inAndersen diseaseMcArdles syndromeCori diseaseVon Gierke disease  <response>: Type Name Enzyme Deficiency Clinical Features IV Amylopectinosis, Andersen disease Branching enzyme Hepatosplenomegaly Accumulation of polysaccharide with few branch points Death from hea or liver failure before age 5 Reference: Harper; 30th edition; Table: 18-2; Page no: 179 