<prompt> A child presents with hepatomegaly and hypoglycemia. There is no improvement in blood sugar even after administration of epinephrine. What is the likely diagnosis -Von girkes diseaseAndersons diseasePompes diseaseMc Ardles disease  <response>: Ans. is a i.e., Von Girkes disease o Amongst the given options only Von Girkes disease presents with hepatomegaly and hypoglycemia. A diagnosis of type I glycogen storage disease Von Girkes disease should be suspected whenever there is hepatomegaly with hypoglycemia that is unresponsive to glucagon or epinephrine. 