<prompt> Defective fumarylacetoacetate hydrolase enzyme is associated withType 1 TyrosinemiaType 2 TyrosinemiaType 3 TyrosinemiaType 4 Tyrosinemia  <response>: Defective fumarylacetoacetate hydrolase enzyme is associated with type I tyrosinemia tyrosinosis. it is the most common type of tyrosinemia. Therapy employs a diet low in tyrosine and phenylalanine and nitisinone NTBC. Reference: Harpers illustrated biochemistry 30th edition 