<prompt> A girl has primary amenorrhea with normal ovaries, absent internal genitalia but normal external genitalia. Most probable diagnosis?Mayer-Rokitansky-Kuster-Hausers- syndromeTurners syndromeNoonansAndrogen insensitivity syndrome  <response>: Mayer Rokitansky Kuster Hausers syndrome : karyotype is 46,XX Normal secondary sexual charecteristics Functional ovaries Normal hormonal profile Associated with skeletal and renal anomalies Management involves creation of a functional vagina for coital purposes and can become biological mother by surrogacy. SHAWS TEXTBOOK OF GYNAECOLOGY,Pg no:286,15th edition 