<prompt> Refsums disease is due to deficiency of which of the following enzyme?Malonate dehydrogenaseThiophoraseSuccinate thiokinasePhytanic alpha oxidase  <response>: Phytanic alpha oxidase Refsum disease is caused by a deficiency of phytanic acid α -hydroxylase α -oxidase which is required for a-oxidation of methylated fatty acids, phytanic acid. 