<prompt> 12-year-old boy with a history of deafness and recurrent hematuria present with CKD. Family history revealed death of his maternal uncle due to same disease. Kidney biopsy was performed and showed a normal light microscopy. What is the probable diagnosis?Alports syndromeGood pasture syndromeThin basement membrane diseasePSGN  <response>: Ans. A Alports syndromeRef: Harrisons Principle of Internal Medicine 20th Ed; Page No-2284DeafnessHematuria and Family history with CKD: Suggestive Alport syndrome.Deafness and CKD is not a feature of thin absent membrane disease.Normal light microscopy rules out PSGN and Goodpasture syndrome. 