<prompt> Which disorder of carbohydrate metabolism typically has cardiac involvement?Glycogen Storage Disease Type I Von Gierke diseaseGlycogen Storage Disease Type II Pompe diseaseHereditary fructose intoleranceGalactosemia  <response>: Pompe disease: coarse facies hepatomegaly, hypotonia progressive cardiomegaly and cardiac dysfunction ECG- sho PR, large QRS complexes. 