<prompt> Menkes syndrome is a disorder ofCopper transpoIron TranspoSodium transpoPotassium Transpo  <response>: Menkes kinky hair syndromeEtiologyFeaturesPrognosisX-linked metabolic disturbance of copper metabolismMutation in copper-transpoing ATP7A geneMental retardationHypocupremiaDecreased circulating ceruloplasminChildren with this disease often die within 5 years because of dissecting aneurysms or cardiac ruptureRef: Harrisons 18e p604 