<prompt> Hepatomegaly is an essential feature ofVon Gierkes diseaseNieman Pick diseaseHurler syndromeHepatic porphyria  <response>: Hepatomegaly is an essential feature of von Gierkes disease all glycogen storage diseases except type 2, 5, 7, Hurler Scheic syndrome all mucopolysaccharidosis and Nieman-Pick disease. But the hepatic involvement of hepatic porphyria is variable. Patients with chronic hepatic porphyria porphyria cutanea tarda, however may show liver enlargement dt fatty infiltration but frank sings of hepatomegaly and iron overload are rare. 