<prompt> Juenes syndrome is inherited as: RepeatARADXRXD  <response>: Ans: A AR Ref: Robbins Pathologic Basis of Disease, 8th edition.Explanation:Refer to explanation in 2011 Pediatrics Question Jeune syndrome Familial asphyxiating thoracic dystrophyAutosomal recessive disorderClassic manifestations in infancy includeDw arfism with short ribsShort limbsCharacteristic radiographic changes in ribs and pelvisSmall chestsRespiratory insufficiencyLung hypoplasia Due to a restricted thoracic cage Major cause of death in infancy.Renal and pancreatic insufficiency in those w ho survive newborn periodOther Clinical FeaturesRespiratory distressChest deformity of varying degreeShort-limbed dwarfismFailure to thriveGastroenteritisRecurrent rectal prolapseDiarrheaCongestive cardiac failurePuffy face, andAnkle swelling 