<prompt> Which disorder of carbohydrate metabolism disorder typically has cardiac involvement?Glycogen Storage Disease Type II PompeGalactosemiaGlycogen Storage Disease Type I Von-GierkeHereditary fructose intolerance  <response>: Classic infantile form of Pompe disease presents with Cardiomyopathy and conduction disorders Muscular hypotonia floppy baby Macroglossia Organomegaly Cardiomyopathy- hyperophic type, severe thickening of the septum and free walls of the left and right hea. Glycogen storage involves cardiac myocytes, special cells of the conduction system A-V node and His-bundle cells, representing the histological background of classical ECG abnormalities in Pompe disease: pre-excitation patterns sho PR, delta waves, AV blocks and bundle branch abnormalities. 