<prompt> Wilms tumor is associated with all the following except :AniridiaBeckwith syndromePolycystic kidneyHemi hypertrohy  <response>: Warn s tamer :Wilms tumor, also known as nephroblastoma, is the most common malignant tumor of kidney in children. Etiology.Most of the tumor are sporadic.1- 2 may have family history.Familial predisposition to wilms tumor is inherited in an autosornal dominant manner.Mutation of the following genes are seen in wilms tumor.Wilms tumor gene WT 1 on chromosome 11.CTNNB I gene encoding the protooncogene beta - ca ten in.p53.Wilms tumor is associated with three distinct syndromes.WAGR syndromeBeck with Wiedemnn syndromeDenys - Drash syndromeWilms tumorAniridiaGenital abnormalitiesMental RetardationEnlargement of body organsHemihypertrophyRenal medullary cystsAdrenal cytomegaly : abnormal large cells in adrenal cortexGonadal dysgenesis Male pseudo - hermaphroditeNephropathy leading to Renal failure 