<prompt> Enzyme defective in Maple syrup urine disease is:TyrosinasePhenylalanine hydroxylaseBranched chain alpha ketoacid dehydrogenaseHomogentisate oxidase  <response>: Enzyme deficiencies and conditionsTyrosinase is deficient in albinismPhenylalanine hydroxylase is deficient in phenylketonuriaMaple syrup urine disease is due to a defect in the enzyme branched chain alpha-keto acid dehydrogenaseHomogentisate oxidase is deficient in alkaptonuria 