<prompt> fanconi bickel syndrome is due to mutation of ?glut 1glut 2glut 4naiodine channels  <response>: FANCONI--BICKEL SYNDROME Hepatic glycogenesis with renal fanconi syndrome. Rare AR disorder. ;deficiency of GLUT 2 in .hepatocytes , pancreatic beta cells, intestinal Proximal renal tubular dysfunction. Presents in 1st year of life as FTT , rickets , hepatomegaly , renomegaly. ref : guyton and hall 