<prompt> Congenital Wilsons disease is characterized by:KF ring is present at birthMay present as acute hepatitisDecreased urinary copper excretionDecreased hepatic copper concentration  <response>: b. May present as acute hepatitisRef: Nelsons 20e p 1939-1940, Ghai 8e p 320-321Kayser-Fleischer rings are absent in young patients with hepatic Wilson disease up to 50 of the time but are present in 95 of patients with neurologic symptoms. 