<prompt> Von Geirkes occurs due to deficiency of -Glucose-6-phosphataseLiver PhosphoryiaseMuscle phosphoryiaseDebranching enzyme  <response>: Ans. is a i.e., Glucose-6-phosphate 19-2o Glucose - 6- phosphatase is deficient in Von Gierkes disease.Type Enzyme deficiencyOrgan s affected1von Gierkes diseaseGlucose 6-phosphataseLiver, kidney11Pompes diseasea 1 - 4 Glucosidase acid maltaseAll organsIIICoris diseaseForbes diseaseDebranching enzymeMuscle, liverIVAndersens diseaseBranching enzymeLiver, myocardiumVMcArdles diseasePhosphorylaseMuscleVIHers diseasePhosphorylaseLiverVIITaruis diseasePhosphofructokinaseMuscle, RBCsVIII Phosphorylase kinaseLivero There is also on X-ltnked form of phosphorylase kinase deficiency. This is sole exception as all other glycogen storage diseases are inherited as autosomal recessive trait. 