<prompt> Hallervorden-Spatz diseaseIs an iron storage disorder in brainMost commonly occurs in adultsRelentlessly non progressive diseaseInherited as Autosomal dominant  <response>: Its a rare disorder characterized by progressive extrapyramidal dysfunction and dementiaA form of familial inherited recessively-linked to chromosome 20 brain degeneration characterized by iron deposition in the brainA mutation in the pantothenate kinase gene has been describedMRI shows eye-of-the-tiger signThe disease is relentlessly progressive and the affected individuals typically die in 2nd or 3rd decaderef:Harrison 18th e p2251 