<prompt> True hermaphroditism karyotype45 X0 STREAKED GONADS46 XX OVO TESTIS47 XY947 XX  <response>: True hermaphrodite or ovotesticular disorder of sexual differentiation OVO-DSD is one of the rarest variety of all inter sex anomalies. In about 90 of cases, patients have 46 XX karyotype. Rarely, 46 XY46 XX mosaicism may occur REF : SHAW TEXT BOOK OF GYNECOLOGY 