<prompt> A child presents with hepatomegaly and hypoglycemia. There is no improvement in blood sugar even after administration of epinephrine. What is the likely diagnosisVon girkes diseaseAndersons diseasePompes diseaseMc Ardles disease  <response>: Amongst the given options only Von Gierkes disease presents with hepatomegaly and hypoglycemia.A diagnosis of type I glycogen storage disease Von Gierkes disease should be suspected whenever there is hepatomegaly with hypoglycemia that is unresponsive to glucagon or epinephrine. 