<prompt> Joube syndrome is associated with?Autosomal dominant polycystic kidney diseasesMedullary cystic kidney diseaseNephronophthisisAutosomal recessive polycystic kidney diseases  <response>: Joube syndrome Defined by multiple neurologic findings, including hypoplasia of the cerebellar vermis. Autosomal recessive disorder It include Nephronothisis as a component Most common presenting feature in the newborn period is an Abnormal breathing pattern Radiologic Finding- Molar tooth sign 