<prompt> A girl at 16 years of age presents with primary amenorrhea. On examination breast development is normal , axillary and pubic hair are present. Vaginal examination reveals an absent vaginal opening. Ultrasound suggests normal ovaries with absent uterus. Most probable diagnosis is?Androgen insensitivity syndromeMRKH Mayer Rokitansky Kuster Hauser SyndromeTurners syndromePure gonadal dysgenesis  <response>: MRKH Androgen insensitivity syndrome Genotype XX XY Gonad Ovaries Testes Breast development Normal Normal Pubic and axillary hair Normal Absent insensitivity to testosterone Vagina Shallow and blind Shallow and blind Uterus Absent Absent Vulva Normal Normal Sr Androgen levels 20-80 ngdl 200-800 ngdl TURNERS IS XO - Near normal female phenotype and streak ovaries. This is the most common type of gonadal dysgenesis. 