<prompt> Metabolic abnormalities in which jaundice is seen are all of the following except?Von Gierke diseaseGalactosemiaTyrosinemiaHereditary fructose intolerance  <response>: a. Von Gierke diseaseRef: Nelson 20e p 716In Von Gierke disease, hepatic carbohydrate metabolism is affected, which is responsible for plasma glucose homeostasis. So, fasting hypoglycemia and hepatomegaly is seen. Despite, marked hepatomegaly, the liver transaminase levels are usually normal or only slightly elevated. Jaundice is usually not seen. 