<prompt> Sandhoffs disease is dt absence of which enzyme?Beta-hexosaminidaseBeta-glucuronibaseAryl sulphataseAlpha galactosidase  <response>: It is a lipid storage disease.Due to deficiency of hexaminidase.Leads to accumulation of globoside Table;14.4Ref: DM Vasudevan, 7th edition, page no: 193 