<prompt> A 7-year old boy presents with a right-sided hemangioma and left-sided focal seizures. The most likely diagnosis is;NeurofibromatosisIncontinetia pigmentiHypermelanosis of ItoSturge-Weber disease  <response>: Ans. d. Sturge-Weber syndrome Ref: Bailey 26e p599; Nelson 19e p2051A 7-year old boy presents with a right-sided hemangioma and left-sided focal seizures. The most likely diagnosis is Sturge-Weber syndrome.Sturge-Weber syndromeEncephalotrigemmal syndromeUsually sporadic, characterized by:Large unilateral cutaneous angiomaQ port-wine stainAngiomas in brain involving ipsilateral cerebral hemisphere and meninges Focal seizuresQ typically occurs opposite to the side of lesionQAdrenal pheochromocytomaCerebral angiomas lead to cortical atrophyQAngiomas are visible radiologically as Tram-track or rail track calcification mainly in occipital regionQ 