<prompt> Glanzmans thromboasthenia is characterized by defective -Gp IIBIIIAGp IBIXGp IBIIIAGpIIBIX  <response>: Ans is a Gp IIBIIIA Glanzmans thrombastheniao It is an autosomal recessive disorder due to deficiencydysfunction of glycoprotein Ilb-IIla Gp IlbIIIa. Thus there is defective platelet aggregation.o Platelet aggregation is normal to ristocetinln constant to Bernard soulier syndrome but no aggregation occurs in response to standard agonists collagen, A DP, thrombin.o Other differentiating features include normal platelet count and morphologyo BT is prolonged. vWF is normal.o The disease manifests at birth with increased bleeding from umbilical cord stump. 