<prompt> An 8-year-old mentally retarded child presents with left side flank pain. On ultrasound hyperecoice lesion is seen in right kidney and multiple lesions in the liver. CT scan of abdomen shows -50 to -60 HU density of the lesions in kidney and liver. The most probable diagnosis is:Familial angiolipomatosisADPKDVHLTuberous sclerosis  <response>: Refer: Nelsonss textbook of pediatrics, 19th edition, pg no: 2049-2052Tuberous sclerosis Bournevilles disease EpiloaAutosomal dominant inheritance.Mutations in TSC-1 gene at 9q - encodes Tuberln.Mutations inTSC-2 gene at 16 p - encodes Hamartin. 