<prompt> A 6-month-old child presented with multiple episodes of seizures for past 2.5 months. The child was admitted to the ward. He had frequent episodes of hypoglycemia which precipitated the seizures. OE, Hepatosplenomegaly Sho stature Thin extremities Doll like facies Lab findings revealed hyperuricemia, lactic acidosis, hyperlipidemias Which enzyme deficiency is responsible for this disorder?Glucose-6-phosphataseAcid maltasePhosphofructokinaseDebranching enzyme  <response>: This is a case of type I GSD Von-gierke disease Autosomal recessive Deficiency of Glucose-6-phosphatase in liver Presents:- Fasting hypoglycemia Lactic acidosis Hypoglycemic seizures Hepatosplenomegaly Lab findings: - Lactic acidosis Increased uric acid levels Hyperlipidemia 