<prompt> Hypoglycemia, hepatomegaly, growth retardation, muscle weakness and accumulation of limit dextrins is caused by which glycogen storage disease?Coris diseaseVon Gierkes diseaseAnderson diseasePompes disease  <response>: a. Coris diseaseRef: Nelsons 20e p 715-725, Ghai 8e p 655-657Important Glycogen Storage Diseases:TypeNameEnzyme deficientCharacteristicsType IVon Gierkes diseaseGlucose-6-phosphataseLiver and renal tubule cells loaded with glycogen. Hypo-glycemia, lactic acidemia, ketosis, hyperlipidemia.Type IIPompes diseaseLysosomal a-1 - 4 and 1 - 6-glucosidaseacid maltaseFatal, accumulation of glycogen in lysosomes, heart failure; muscle involvement seenType IIILimit dextrinosis, or Coris diseaseDebranching enzymeAccumulation of a characteristic branched polysaccharide resembling Limit dextrinType IVAmylopectinosis, Andersens diseaseBranching enzymeAccumulation of a polysaccharide having few branch points. Death due to cardiac or liver failure in 1st year of life.Type VMcArdles diseaseMuscle phosphorylaseDiminished exercise tolerance; Little or no lactate in blood after exercise; exercise-induced myoglobinuria secondary to rhabdomyolysis seenType VIHers diseaseLiver phosphorylaseQHigh glycogen content in liver, tendency towards hypoglycemia; Ketosis seen;Type VIITaruis diseasePhosphofructokinase in muscle and erythrocytesAs for type V hemolytic anemia. 