<prompt> Glucose 6-phosphatase deficiency occurs inGauchers diseaseVon Gierkes diseasePompes diseaseHurlers disease  <response>: Von Gierkes disease 269- U.S 3rdGLYCOGEN-STORAGE DISEASETypeNAMEENZYME-DEFECTI Von Gierkes disease type I glycogenosisGlucose-6 phosphataseIIPompes diseaseLysosomal a-1, 4 glucosidase acid maltaseIIICoris disease limit dextrinosis, Forbes diseaseAmylo a-1, 6- glucosidase debranching enzymeIVAndersons disease amylopectinosisGlucosyl 4-6 transferase branching enzymeVMe Ardles disease type V glycogenosisMuscle glycogen phosphorylaseVIHers diseaseLiver glycogen phosphorylaseVIITaruls diseasePhospho fructokinase SPHINGOMYELINSCEREBROSIDES1.Niemann-Pick disease - defect in enzyme sphingomyelinase1.Gauchers disease - due to b-glucosidase defect2.Fabers disease - defect in enzyme ceramidase2.Krabbes disease - due to b-galactosidase enzyme defect 