<prompt> All are lysosomal disorders, exceptGauchers diseaseTay Sachs diseaseNeimann Pick diseaseVon Geirkes disease  <response>: Enzyme deficiencies of :Gauchers disease - Beta-glucosidaseNiemann-Pick disease - SphingomyelinaseTay-Sachs disease - Hexosaminidase AGlycogen storage disease, Type l von Gierke;s diseaseEnzyme-deficient-Glucose-6-phosphataseChromosome location-17Salient features-Hepatomegaly, cirrhosis, hypoglycemia, ketosis, hyperuricemiaRef: D M Vasudevan 7th edition Page no: 144, 430 