<prompt> Alagille syndrome isBile duct paucityIHBR dilationPBCPSC  <response>: Alagille syndrome is an autosomal dominant genetic disorder affecting liver,hea,kidney,etc.Liver biopsy in Alagille syndrome shows too few bile ductsbile duct paucity or in some cases,the complete absence of bile ductsbiliary atresia.Bile duct paucity results in reduced absorption of fat vitaminsA,D,E,K which may lead to ricketsa failure to thrive in children. 