<prompt> Refsums syndrome is associated with ?Retinitis pigmentosaXerophthalmiaChalcosisDiabetes retinopathy  <response>: Ans. is a i.e., Retinitis pigmentosa Associations of retinitis pigmentosa Ocular associations : These include myopia, primary open angle glaucoma, microphthalmos, conical cornea and posterior subcapsular cataract. Systemic associations : These are in the form of following syndromes :- i Laurence-Moon-Biedl syndrome : It is characterised by retinitis pigmentosa, obesity, hypogenitalism, polydactyly and mental deficiency. ii Cockaynes syndrome : It comprises retinitis pigmentosa, progressive infantile deafness, dwarfism, mental retardation, nystagmus and ataxia. iii Refsums syndrome : It is characterized by retinitis pigmentosa, peripheral neuropathy and cerebellar ataxia. iv Ushers syndrome : It includes retinitis pigmentosa and labyrinthine deafness. v Hallgrens syndrome : It comprises retinitis pigmentosa, vestibulo-cerebellar ataxia, congenital deafness and mental deficiency. 