<prompt> Please answer with one of the option in the bracket. Write reasoning in between . Write answer in between .Q:A 6-month-old boy is referred to a geneticist after he is found to have persistent hypotonia and failure to thrive. He has also had episodes of what appears to be respiratory distress and has an enlarged heart on physical exam. There is a family history of childhood onset hypertrophic cardiomyopathy, so a biopsy is performed showing electron dense granules within the lysosomes. Genetic testing is performed showing a defect in glycogen processing. A deficiency in which of the following enzymes is most likely to be responsible for this patients symptoms?? A: Glucose-6-phosphatase, B: Lysosomal alpha 1,4-glucosidase, C: Debranching enzyme, D: Branching enzyme, E: Muscle phosphorylase,  <response>: This is a question about an infant with symptoms of hypotonia, failure to thrive, respiratory distress, and cardiomyopathy. The history and biopsy findings of lysosomal storage disease point towards a glycogen storage disease. The choices list different enzymes involved in glycogen metabolism. Based on the clinical presentation and biopsy findings, this infant most likely has Pompe disease, which is caused by a deficiency in the lysosomal enzyme acid alpha-glucosidase acid maltase. This enzyme breaks down glycogen in the lysosomes. A deficiency leads to glycogen accumulation and lysosomal dysfunction, which can cause the symptoms seen in this patient.B: Lysosomal alpha 1,4-glucosidase 