 - Stable disease: Patients receive low-dose oral dexamethasone once weekly for 6 months months 7-12 with anakinra SC once daily. Patients who maintain stable disease or responded will continue low-dose oral dexamethasone and anakinra SC once daily for 6 additional months months 13-18. Patients who develop disease progression at any time proceed to treatment with high dose dexamethasone. 